Raras
Buscar doenças, sintomas, genes...
Artéria pulmonar proveniente da aorta
ORPHA:99050CID-10 · Q25.7CID-11 · LA8B.1DOENÇA RARA

Artéria pulmonar proveniente da aorta (PACA) é uma malformação cardíaca caracterizada pela origem anômala de um ramo das artérias pulmonares da aorta ascendente e origem normal da outra artéria pulmonar da via de saída do ventrículo direito, apresentando desconforto respiratório, insuficiência cardíaca congestiva e retardo de crescimento nos primeiros dias/meses de vida.

Mantido por Agente Raras·Colaborar como especialista →

Introdução

O que você precisa saber de cara

📋

Artéria pulmonar proveniente da aorta (PACA) é uma malformação cardíaca caracterizada pela origem anômala de um ramo das artérias pulmonares da aorta ascendente e origem normal da outra artéria pulmonar da via de saída do ventrículo direito, apresentando desconforto respiratório, insuficiência cardíaca congestiva e retardo de crescimento nos primeiros dias/meses de vida.

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Casos conhecidos
200
pacientes catalogados
Início
Infancy
+ neonatal
🏥
SUS: Cobertura mínimaScore: 15%
CID-10: Q25.7
🇧🇷Dados SUS / DATASUS
PROCEDIMENTOS SIGTAP (5)
0202010503
Cariótipo — bandas G, Q ou Rgenetic_test
0202010600
Pesquisa de microdeleções/microduplicações por FISHlab_test
0202010694
Sequenciamento completo do exoma (WES)rehabilitation
0202010260
Dosagem de alfa-fetoproteína
0301070040
Atendimento em reabilitação — doenças raras
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

❤️
Coração
15 sintomas
🫁
Pulmão
4 sintomas
📏
Crescimento
1 sintomas

+ 6 sintomas em outras categorias

Características mais comuns

90%prev.
Origem anômala da artéria pulmonar direita da aorta ascendente
Muito frequente (99-80%)
90%prev.
Morfologia anormal do sistema cardiovascular
Muito frequente (99-80%)
55%prev.
Insuficiência cardíaca congestiva
Frequente (79-30%)
55%prev.
Dispneia de esforço
Frequente (79-30%)
55%prev.
Shunt da esquerda para a direita
Frequente (79-30%)
55%prev.
Obstrução da via de saída do ventrículo esquerdo
Frequente (79-30%)
26sintomas
Muito frequente (2)
Frequente (9)
Ocasional (9)
Muito raro (6)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 26 características clínicas mais associadas, ordenadas por frequência.

Origem anômala da artéria pulmonar direita da aorta ascendenteAnomalous origin of right pulmonary artery from ascending aorta
Muito frequente (99-80%)90%
Morfologia anormal do sistema cardiovascularAbnormal cardiovascular system morphology
Muito frequente (99-80%)90%
Insuficiência cardíaca congestivaCongestive heart failure
Frequente (79-30%)55%
Dispneia de esforçoExertional dyspnea
Frequente (79-30%)55%
Shunt da esquerda para a direitaLeft-to-right shunt
Frequente (79-30%)55%

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Últimos 10 anos200publicações
Pico2025125 papers
Linha do tempo
2026Hoje · 2026📈 2025Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Artéria pulmonar proveniente da aorta

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

Nenhum ensaio clínico registrado para esta condição.

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Publicações mais relevantes

Timeline de publicações
0 papers (10 anos)
#1

Inferior wall ST-elevation myocardial infarction in a patient with a single coronary artery from the right coronary cusp trifurcating into the left anterior descending, left circumflex, and right coronary arteries: a rare coronary anomaly, case report.

European heart journal. Case reports2026 Mar

Abnormal origin of a coronary artery is a rare congenital condition that can significantly affect clinical outcomes especially when associated with acute coronary syndromes. Among these, the presence of a single coronary artery trifurcating from the right coronary cusp into all major coronary branches is exceptionally rare and poorly represented in the literature. A 35-year-old man presented with an inferior ST-elevation myocardial infarction. Emergency angiography revealed a single coronary artery arising from the right coronary cusp. The culprit was the right coronary artery. It was effectively treated with intravascular-guided percutaneous coronary intervention, and the remaining coronaries demonstrated normal flow, as shown in subsequent imaging. The patient recovered uneventfully, rehabilitated without complications. He was discharged on guideline directed medical therapy. Although the anomalous coronary anatomy was not the direct cause of infarction, it introduced significant procedural challenges that could have delayed or compromised revascularization. Our case highlights the importance of recognizing and anticipating coronary anomalies in acute settings. Multimodality imaging and anatomical classification systems help provide timely diagnosis, procedural planning, and risk assessment from a long-term perspective.

#2

Case report of mitral valve replacement in a single coronary artery patient: devil is hidden in the details.

European heart journal. Case reports2026 Jan

Single coronary artery (SCA) is a rare congenital anomaly that may have serious clinical consequences in different clinical settings despite often being asymptomatic. We report a case of a 75-year-old patient with a SCA originating from the right sinus of Valsalva presenting for pre-operative assessment for mitral valve (MV) stenosis. The patient developed cardiogenic shock post MV replacement surgery on grounds of iatrogenic occlusion of the ectopic left main coronary artery which was treated with a percutaneous revascularization procedure. SCA represents a major anatomical variant that can significantly impact clinical outcomes, particularly during cardiac surgery. An abnormal coronary anatomy poses technical challenges, due to potential inadvertent injury or compression of the anomalous artery relative to the extent of the myocardium at risk.

#3

A case report of J wave syndrome with abnormal potentials in both right and left ventricles and reversed J wave in lead V1.

European heart journal. Case reports2026 Feb

Abnormal epicardial potentials in J wave syndrome predominantly involve the right ventricular outflow tract (RVOT), while left ventricular (LV) involvement remains less characterized and associates with increased ventricular fibrillation (VF) risk. We report a case demonstrating an inverted J wave in lead V1, suggesting LV posterior wall substrate rather than typical RVOT involvement. A 19-year-old man with resuscitated VF received a subcutaneous implantable cardioverter-defibrillator (S-ICD). Despite cilostazol and quinidine therapy, he experienced five appropriate shocks within 6 months. Twelve-lead electrocardiography showed inferior J waves and a negative deflection in V1, suggesting an inverted J wave. Epicardial mapping showed fractionated potentials in both RVOT and LV posterior wall. Pilsicainide administration augmented RVOT potentials while attenuating those in the LV posterior wall. Spontaneous VF was triggered by premature ventricular contractions (PVCs) originating from the LV posterior wall, where prepotentials preceded QRS onset by 50 ms. Radiofrequency applications eliminated the PVCs, followed by anatomical ablation of RVOT fractionated regions. Subsequently, VF was never induced by program stimulation of up to triple extra stimuli. In the post-operative electrocardiogram, inverted J waves in the V1 lead disappeared. At 8 months post-ablation, the patient remained free from VF recurrence without antiarrhythmic medications, and no S-ICD therapies occurred. This case demonstrates complex electrophysiological manifestations of J wave syndrome, with the inverted J wave in V1 potentially reflecting LV posterior wall substrate. Although the overlapping ablation procedure limited definitive attribution, these findings contribute to understanding the heterogeneous substrates in J wave syndrome.

#4

Isolated left ventricular apical hypoplasia: a case report.

European heart journal. Case reports2026 Jan

Isolated left ventricular apical hypoplasia is a rare and lesser-known form of cardiomyopathy characterized by specific findings on cardiac imaging. It is thought to be congenital in origin, with clinical features that can range from being asymptomatic to presenting with heart failure and arrhythmias. A 43-year-old woman presented with chest pain and had previously undergone evaluation at another facility, including a 2D echocardiogram and computed tomography (CT) coronary angiography. These tests revealed a dilated left atrium and ventricle and reduced left ventricular function alongside a Type I left anterior descending artery. A cardiac magnetic resonance image (MRI) and review of the CT scan confirmed a diagnosis of isolated left ventricular apical hypoplasia. Guideline-directed medical therapy was initiated due to the initial presentation of left ventricular dysfunction. Left ventricular apical hypoplasia is characterized by (i) a truncated, spherical, and impaired left ventricle (LV) with bulging of the interventricular septum towards the right ventricle (RV), (ii) fatty material in the apical region of the LV, (iii) abnormalities in the papillary muscles and trabecular structures, and (iv) elongation of the RV wrapping around the underdeveloped LV. Limited data is available on this condition, with only a few reported cases. Currently, no definitive guidelines exist, and management is tailored to the patient's specific presentation, including treating heart failure and any arrhythmias that may arise. While the aetiology of this condition remains poorly understood, it is crucial to recognize it to prevent misdiagnosis and to encourage further research into its management.

#5

Fusiform dilatation of the ascending aorta and outpouching of the left A2 anterior cerebral artery segment in COL4A1 -related disorder.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology2026 Jan 10

COL4A1 encodes the alpha-1 chain of type IV collagen, which plays a crucial role in vascular basement membranes. The clinical manifestations of COL4A1-related disorders are yet to be fully defined. There is increasing evidence that COL4A1 may play crucial roles across the vascular system. We studied a 71-year-old man with a novel splice acceptor variant, COL4A1 [NM_001845.6] c.1466-1G > C. Clinical, radiological (including comprehensive imaging of the brain as well as chest and abdomen), and genetic assessments were performed. His medical history included fusiform dilatation (4.2 cm) of the ascending thoracic aorta, hearing loss, adrenal and pulmonary nodules, mild splenomegaly, and gallstones. Imaging showed fusiform dilatation (4.2 cm) of the ascending thoracic aorta and concomitant outpouching of the left A2 anterior cerebral artery in the patient in the setting of the heterozygous likely pathogenic splice site variant, COL4A1 c.1466-1G > C. Consistent with a diagnosis of COL4A1-related disorder, multiple cystic bilateral renal lesions were noticed on abdominal imaging. Magnetic resonance imaging of the brain also showed findings consistent with cerebral vasculopathy with scattered bilateral punctate T2/FLAIR hyperintensities within the supratentorial and pontine white matter. Our observations support the growing body of evidence suggesting crucial roles for COL4A1 in vascular homeostasis including medium sized vessel cerebral vasculopathy and aortopathy.

Publicações recentes

Ver todas no PubMed

📚 EuropePMCmostrando 200

2026

Inferior wall ST-elevation myocardial infarction in a patient with a single coronary artery from the right coronary cusp trifurcating into the left anterior descending, left circumflex, and right coronary arteries: a rare coronary anomaly, case report.

European heart journal. Case reports
2026

VF Arrest at Rest in a Teenager With Anomalous Origin of Coronaries and DSG2 Variant.

JACC. Case reports
2026

Coronary artery anomalies in common arterial trunk: proposal of a new anatomical classification.

Interdisciplinary cardiovascular and thoracic surgery
2026

The Association of Pulmonary Artery to Aorta Diameter Ratio With Postoperative Outcomes Following Left Ventricular Assist Device Implantation.

Journal of cardiothoracic and vascular anesthesia
2026

Direct venous-to-arterial communication as a novel mechanism for ectopic embolism following esophageal variceal embolization: A case report.

Experimental and therapeutic medicine
2026

Nonatherosclerotic Subclavian Steal Syndrome Due to Brachiocephalic Trunk Kinking in an Elderly Woman: A Case Report.

The American journal of case reports
2026

Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.

Cureus
2026

Pressure gradient vs. flow relationships in patients with symptomatic valvular aortic stenosis - PREFLOW.

Clinical research in cardiology : official journal of the German Cardiac Society
2025

The Effect of Aspirin Administration on Fetal Cardiovascular Function Between 18 to 24 Weeks of Gestation: A New Perspective on ASA Indication in Obstetrics.

Journal of reproduction &amp; infertility
2026

Comprehensive immunohistochemical and molecular characterization of paratesticular clear cell papillary cystadenomas: A multi-institutional study of 14 cases.

Annals of diagnostic pathology
2026

Unrepaired Truncus Arteriosus Type 1 With Eisenmenger Syndrome and Recurrent Embolic Strokes: An Adult Case Report.

The American journal of case reports
2026

Screening for Pulmonary Hypertension in Interstitial Lung Disease: Preliminary Results from the PHINDER Study.

Advances in therapy
2025

[Prosthetic repair of the ascending aorta in patients with normal and variant anatomy of the brachiocephalic trunk].

Angiologiia i sosudistaia khirurgiia = Angiology and vascular surgery
2026

Coronary Conundrum: Anomalous Pan-Coronary Origin from the Right Sinus with a "Type X" Dual LAD.

Methodist DeBakey cardiovascular journal
2026

Ectopic adrenal nodular hyperplasia mimicking right upper polar renal cell carcinoma: a case report and literature review.

Frontiers in oncology
2026

Case report of mitral valve replacement in a single coronary artery patient: devil is hidden in the details.

European heart journal. Case reports
2026

Prominent venous intravasation in hysterosalpingo-contrast sonography (HyCoSy): A case report.

Medicine
2026

Clinical management of aortic valve regurgitation after left ventricular assist device implantation: prediction, assessment, and treatment strategies.

Frontiers in cardiovascular medicine
2026

Outcomes of surgical repair of congenital vascular rings in children.

Journal of cardiothoracic surgery
2025

Patterns of Circle of Willis Variants among Patients Undergoing 3 Tesla Magnetic Resonance Angiography at a Tertiary Care Hospital: An Observational Study.

JNMA; journal of the Nepal Medical Association
2026

The utility of continuous high-enhanced-contrast electrocardiography-gated cardiac computed tomography method evaluating accurate minimal ductal diameter and ductus arteriosus morphology in a dog with patent ductus arteriosus.

Journal of veterinary cardiology : the official journal of the European Society of Veterinary Cardiology
2026

Endocardial Ito-slow Overexpression and Fibrotic Remodeling Underlying Pause-Dependent Early Repolarization in Humans.

JACC. Clinical electrophysiology
2026

Congenital Temporomandibular Joint Ankylosis: Investigating Potential Genetic Etiologies with Whole Exome Sequencing.

Journal of clinical medicine
2026

Embryologic and Developmental Origins of Gastroschisis: A Scoping Review of Historical and Contemporary Theories.

Children (Basel, Switzerland)
2026

Double trouble: a rare case of quadricuspid aortic valve and anomalous right coronary artery.

The international journal of cardiovascular imaging
2025

Right aortic arch with cervical origin of left subclavian artery: Unusual arch anomaly associated with tetralogy of Fallot.

Annals of pediatric cardiology
2026

Combination of Unroofing and Relocation to Treat Anomalous Origin of the Right Coronary Artery.

JACC. Case reports
2026

[Coronary embolism from atrial myxoma: a rare cause of myocardial infarction? Case report and literature review].

Giornale italiano di cardiologia (2006)
2026

Diagnostic Challenges of Anomalous Left Coronary Artery from the Right Pulmonary Artery.

CASE (Philadelphia, Pa.)
2026

End-to-End Resection for Neonatal Aortic Coarctation with Severe Left Ventricular Dysfunction and Large Ventricular Septal Defect: A Case Report in a 23-Day-Old Infant.

International medical case reports journal
2025

Anomalous aortic origin of the coronary arteries: a presentation of three cases and review of the literature.

Cardiovascular journal of Africa
2026

Activity-related skeletal changes at the olecranon tip in three individuals from the Iron Age cemetery in Hallstatt, Austria.

International journal of paleopathology
2026

A case report of J wave syndrome with abnormal potentials in both right and left ventricles and reversed J wave in lead V1.

European heart journal. Case reports
2026

Management of a Pulmonary Sequestration With a Large Aberrant Artery Using a Hybrid Approach: Thoracic Endovascular Aortic Repair Followed by Video-Assisted Thoracoscopic Lobectomy.

Case reports in surgery
2025

Shunt configuration's role in shaping hemodynamics of reverse Potts shunt in pediatric pulmonary arterial hypertension.

Frontiers in bioengineering and biotechnology
2026

Artery of percheron infarction and a very rare finding of ping pong gaze: A case report.

Radiology case reports
2026

Anatomical reduction for focal fasciculations in peroneus brevis spondylolisthesis: a case report suggesting a mechanism of peripherally derived tremor.

BMC musculoskeletal disorders
2026

Intralobar pulmonary sequestration coexisting with pulmonary cryptococcosis: A case report and literature review.

Experimental and therapeutic medicine
2026

Electrocardiographic Characteristics of Escape Rhythm During Complete Atrioventricular Block After Transcatheter Aortic Valve Replacement.

Reviews in cardiovascular medicine
2026

Inferior polar renal artery arising just above the aortic bifurcation: case report and brief literature review.

Folia morphologica
2026

A rare case of ectopic origin of the left anterior descending artery from the right coronary sinus misdiagnosed as a chronic total occlusion lesion.

The Journal of international medical research
2026

Aberrant right posterior hepatic artery originating from the gastroduodenal artery with a concomitant replaced left hepatic artery: a rare clinical variant.

Surgical and radiologic anatomy : SRA
2025

Transcutaneous Closure of Persistent Ductus Arteriosus: Complication Rates and Long-term Follow-up, a Single-Centre Retrospective Study.

CJC pediatric and congenital heart disease
2025

Case Report: Postmenopausal hyperandrogenism misled by adrenal incidentaloma: a rare case of androgen-secreting ovarian adult granulosa cell tumor and clinical implications.

Frontiers in oncology
2025

Removing an Embolized Peripheral Intravenous Catheter from the Left Caudal Lung Lobe of a Dog via Intercostal Thoracotomy.

Veterinary sciences
2026

Comparing perspectives from experts and individuals with lived experience in the Global North versus the Global South: ICF core sets for deafblindness.

Population health metrics
2026

Computed Tomography Angiography-Assisted Ovarian Vein Sampling for Diagnosing an Androgen-Producing Leydig Cell Tumor: A Case Report.

Case reports in endocrinology
2026

A case report and literature review of neuropsychiatric lupus presenting with coma as the initial symptom.

Medicine
2026

Tetrahymena JanusA gene encodes a polo kinase whose loss triggers a dorsal/ventral intracellular homeosis.

Current biology : CB
2026

Transcatheter Management of Atypical Scimitar Syndromes With Dual Venous Drainage.

JACC. Case reports
2025

MET exon 14 skipping gene-positive lung adenocarcinoma associated with atypical adenomatous hyperplasia in lungs and metachronous lung adenocarcinoma.

Klinicka onkologie : casopis Ceske a Slovenske onkologicke spolecnosti
2026

Evaluation of arterial and venous variations in thorax computed tomography examinations.

Journal of anatomy
2026

Right Aortic Arch With Bilateral Ductus Arteriosus, Aberrant Left Subclavian Artery, Interrupted Left Carotid Artery.

Echocardiography (Mount Kisco, N.Y.)
2025

High-Origin Radial Artery: Frequency and Morphology in Midwestern Cadaveric Specimens.

Cureus
2026

Isolated left ventricular apical hypoplasia: a case report.

European heart journal. Case reports
2026

A Novel Multiparametric Model Integrating Aortoseptal Angle to Predict the Origin of Outflow Tract Ventricular Arrhythmias.

Journal of arrhythmia
2026

Novel PKP2 compound heterozygous mutations causing neonatal early-onset arrhythmogenic cardiomyopathy: insights into the synergistic pathogenicity of biallelic inactivation.

Functional &amp; integrative genomics
2026

Pseudo-Left Ventricular Summit Premature Ventricular Contraction in a Patient With Abnormal Intraventricular Conduction.

JACC. Case reports
2025

Reimplantation of the Anomalous Origin of the Right Coronary Artery: A Case Report.

Cureus
2026

Volumetric non-invasive cardiac mapping for accessible global arrhythmia characterization.

Communications medicine
2026

Evaluation of aortic arch branching pattern variations with computed tomography angiography images.

Surgical and radiologic anatomy : SRA
2026

Percutaneous coronary intervention for acute myocardial infarction in a patient with an anomalous origin of the right coronary artery from the ascending aorta: a case report.

Journal of medical case reports
2026

Fusiform dilatation of the ascending aorta and outpouching of the left A2 anterior cerebral artery segment in COL4A1 -related disorder.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2026

Anomalous Origin of the Left Pulmonary Artery from Aorta.

Radiology. Cardiothoracic imaging
2026

Endovascular embolization for primary racemose hemangioma of the bronchial artery supplied by multiple systemic arteries: A rare case report.

Medicine
2026

Advanced primary fallopian tube cancer was found during chemotherapy for multiple myeloma: a case report and literature.

BMC women's health
2026

Detection of white matter microstructural changes in patients with systemic lupus erythematosus based on multiple diffusion models and related diffusion metrics.

Neural regeneration research
2026

Preoperative embolization of a pulmonary carcinoid tumor with unusual arterial supply: a case report.

Journal of cardiothoracic surgery
2026

Bilateral lung transplantation with simultaneous aortic replacement using donor aorta in a patient with pulmonary arterial hypertension and patent ductus arteriosus.

Journal of cardiothoracic surgery
2025

Bilateral Accessory Clavicular Heads of Sternocleidomastoid Stenosing Supraclavicular Fossa in Human: Case Report.

Prague medical report
2026

The Cardiovascular Anatomy of the Green Iguana (Iguana iguana): Heart Structure, Major Vessels, and Coelomic Circulation.

Anatomia, histologia, embryologia
2025

A case report of primary hyperparathyroidism due to a giant substernal parathyroid adenoma managed using a neck incision approach.

Medicine
2025

Prognostic value of left atrial stiffness index in adults with repaired coarctation of aorta.

European heart journal. Cardiovascular Imaging
2026

A disrupted compartment boundary underlies abnormal cardiac patterning and congenital heart defects.

Nature cardiovascular research
2025

Aberrant origins of the subclavian artery from pulmonary arteries: a case series and literature review.

Cardiology in the young
2025

Diagnosis of EBV and HCMV infections in pediatric heart transplant recipients.

BMC pediatrics
2025

Modeling based insights into mechanical dysfunction in esophageal motility disorders.

PLoS computational biology
2025

Hemodynamic Impact of the Aberrant Subclavian Artery: A CFD Investigation.

Journal of personalized medicine
2025

Bronchial Arteriovenous Malformation Detection Prior to Catheter Ablation for Paroxysmal Atrial Flutter and Fibrillation: A Case Report.

The American journal of case reports
2026

[MINOCA revealing an anomalous origin of right coronary artery and a pheochromocytoma : A case report with literature review].

Annales de cardiologie et d'angeiologie
2025

Integrated Cardio-Cerebral Assessment Predicts Adverse Outcomes in Aortic Stenosis: A Preliminary Study.

Echocardiography (Mount Kisco, N.Y.)
2026

Application of 3D printing in the evaluation of a clinically significant congenital uterine anomaly.

Ginekologia polska
2026

Computed Tomography-Guided Biopsy of a Ureteral Urothelial Carcinoma Mimicking a Submucosal Bladder Tumor at the Ureterovesical Junction.

IJU case reports
2025

Anatomical patterns and collateral pathways in congenital aplasia, atresia, and hypoplasia of iliac and lower extremity veins: a retrospective cohort study.

Surgical and radiologic anatomy : SRA
2025

Anomalous Aortic Origin of the Right Coronary Artery Between the Right and Left Coronary Sinuses: A Case Report.

Cureus
2026

[Anomalous origin of the left anterior descending artery from the right coronary artery: A case report].

Revista medica del Instituto Mexicano del Seguro Social
2025

Internal jugular vein anomaly in a young patient with facial hemangioma: a case report.

Journal of medical case reports
2025

Myocardial fibrosis and its relationship with ventricular arrhythmias and reduced ventricular systolic function in young and veteran endurance athletes.

European journal of preventive cardiology
2026

Salmonella Aortitis-Induced Aortocaval Fistula Masquerading as Tricuspid Disease.

JACC. Case reports
2025

[Prognostic analysis of imaging features of coronary artery anomalous origin from the opposite sinus in middle-aged and elderly patients].

Zhonghua xin xue guan bing za zhi
2025

Acute Kidney Failure and Myocarditis Triggered by Magic Mushroom Toxicity in a Patient With Prior Cocaine Exposure.

Cureus
2025

Case Report: A case of intrahepatic papillary neoplasm of the bile duct with invasive carcinoma in a young patient and review of the literature.

Frontiers in oncology
2025

Beyond the Pulmonary Veins: The Influence of Pulsed Field Ablation on the Superior Vena Cava.

Journal of arrhythmia
2025

Fever of Unknown Origin and Penetrating Aortic Ulcer Successfully Treated with Thoracic Endovascular Aortic Repair-A Case Report.

Diagnostics (Basel, Switzerland)
2025

Intrapulmonary Aorta to Coronary Artery Graft and Prosthetic Mitral Valve Replacement for Late-Diagnosed Anomalous Left Coronary Artery from the Pulmonary Artery.

World journal for pediatric &amp; congenital heart surgery
2025

Pulmonary arterial diameter remains dilated despite a reduction of pulmonary arterial pressure post lung transplantation: a retrospective study.

Quantitative imaging in medicine and surgery
2025

Child with progressive limb weakness caused by a neuroenteric cyst in the cervical segment: A case report.

Medicine
2025

Anomalous right coronary artery stemming from left coronary sinus and malignant interarterial course in a middle-aged woman: a case report and review of diagnostic and surgical management.

International journal of emergency medicine
2025

Origin of the Right Vertebral Artery Examined with CTA.

Prilozi (Makedonska akademija na naukite i umetnostite. Oddelenie za medicinski nauki)
2026

Complex Fetal Anomalies: Kluth Type Xc2 Variant Tracheoesophageal Fistula, Srikanth Group III Bronchopulmonary Foregut Malformation, Mirror-Image Dextrocardia with L-Looped Ventricles, Anomalous Coronary Origin from the Pulmonary Artery, and Cardiac-Type Total Anomalous Pulmonary Venous Connection.

Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology Society
2025

Coexistence of Atrial Flutter and Slow Ventricular Tachycardia: A Rare Cause of Reversible Cardiomyopathy.

JACC. Case reports
2025

A Case Report of HIV-Associated Pituitary Lymphoma and Review of the Literature.

Clinical case reports
2025

Macrophages in ventricular remodeling and heart failure: orchestrators of inflammation and repair.

Frontiers in immunology
2026

Pre-foraminal vertebral artery variation in the United States: A multi-institutional cadaveric study.

Annals of anatomy = Anatomischer Anzeiger : official organ of the Anatomische Gesellschaft
2025

HPV-Related Pelvic Squamous Cell Carcinoma of Unknown Primary: Two Case Studies.

Cancer reports (Hoboken, N.J.)
2025

A Delayed Diagnosis of an Oral Foreign Body Due to Post-traumatic Neglect: A Case Report and Literature Review.

Cureus
2025

Transcatheter Aortic Valve Implantation with Anomalous Left Main Origin From Right Coronary Cusp: A Case Report.

The American journal of case reports
2025

Congenital descending aorta to pulmonary vein fistula: an unusual cause of left ventricular dilation in a 21-year-old female.

Journal of cardiothoracic surgery
2025

Anatomical Variations of the Brachial Artery: A Systematic Review and Meta-Analysis.

FASEB journal : official publication of the Federation of American Societies for Experimental Biology
2025

Epigenetic Drugs Splitomicin, Suberohydroxamic Acid, CPTH6, BVT-948, and PBIT Moderate Fibro-Fatty Development in Arrhythmogenic Cardiomyopathy.

Biomolecules
2025

The Blood Supply of the Stomach: Anatomical and Surgical Considerations.

Diagnostics (Basel, Switzerland)
2025

Congenital absence of the right coronary artery in a patient with corrected congenital heart disease.

BMJ case reports
2026

Arcuate Foramen of the Atlas Vertebra and its Correlation with Clinical Implications in the Craniocervical Region: A Systematic Review and Meta-analysis.

World neurosurgery
2025

Establishment of immortalized ovarian stromal cell lines using Sendai virus vectors: a platform for studying tumor-stroma interactions and carcinogenesis.

Human cell
2025

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Proboscis lateralis with trans-ethmoidal meningocele and congenital nostril hypoplasia: a case report and literature review.

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Assessment of cardiac function by speckle tracking echocardiography in children with osteogenesis imperfecta.

Pediatric research
2025

[Anomalous Origin of the Right Coronary Artery from the Left Sinus of Valsalva Treated with Modified Unroofing Procedure].

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Anatomical Variation in the Formation of the Median Nerve With Triple and Quadruple Roots of Origin: A Cadaveric Case Report.

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Right lower lobectomy for lung cancer with anterior truncal basal pulmonary artery: A case report.

SAGE open medical case reports
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Digestion is unaffected by surgical elimination of the right-to-left cardiac shunt in American alligators (Alligator mississippiensis).

The Journal of experimental biology
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Myocardial Ischemia Secondary to Anomalous Origin of Left Anterior Descending Coronary Artery: A Case Report and Literature Review.

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Inhaled iloprost and 2D phase-contrast cardiac MRI in pulmonary vascular reversibility: an adolescent case of anomalous right pulmonary artery from the ascending aorta.

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Unusual Venous-Origin Intraparenchymal Hematoma in the Context of a Post-traumatic Carotid-Cavernous Fistula.

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Anatomical considerations in fixation of sternal fractures and nonunions.

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A case of panophthalmitis with orbital infection of polymicrobial origin.

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Malignant Anomalous Aortic Origin of the Left Main Coronary Artery Managed by Ostial Reimplantation: A Case Report.

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A Case of Follicular Dendritic Cell Sarcoma of the Palatine Tonsil That Developed as a Radiation-Induced Sarcoma.

Case reports in otolaryngology
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Pulmonary Vascular Features on CT Chest Differentially Associate with Adverse Outcomes in Smokers in COPDGene.

Annals of the American Thoracic Society
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Acute rupture of primary hepatic angiosarcoma with Kasabach-Merritt syndrome: a rare case report and literature review.

World journal of surgical oncology
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Extra-anatomical ascending-to-descending aortic bypass in an adult patient with aortic coarctation.

Multimedia manual of cardiothoracic surgery : MMCTS
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Rare congenital coronary artery anomalies diagnosed by coronary CT angiography: A 4-case series.

Radiology case reports
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The Silent Stranglehold: Multimodal Imaging in Postoperative Pulmonary Artery Stenosis.

Echocardiography (Mount Kisco, N.Y.)
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Untreated incomplete ALCAPA in an adult resulting in mitral regurgitation and reduced left ventricular ejection fraction: case report.

European heart journal. Case reports
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Y-Incision Aortic Annular Enlargement in Patients With Anomalous Left Circumflex Artery.

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Weight-based flow rate triphasic contrast injection protocol for pediatric cardiac computed tomography.

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The diagnostic efficacy of unenhanced CT for detecting acute central pulmonary embolism.

BMC cardiovascular disorders
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Anomalous origin of right coronary artery with interarterial and intramural course associated with bicuspid aortic valve and dilation of ascending aorta.

BMJ case reports
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Anomalous Systemic Arterial Supply to the Left Basal Segment With Arterial Dissection of the Feeding Artery: A Case Report and Literature Review.

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The American journal of case reports
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Annals of pediatric cardiology
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Physiological reports
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The Indian journal of radiology &amp; imaging
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Ultrasound in medicine &amp; biology
2026

Surgical Results for Anomalous Aortic Origin of Coronary Artery - Is Right Side Prompt Surgery Necessary?

Circulation journal : official journal of the Japanese Circulation Society
2025

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BMJ case reports
2025

Unusual Revelation of an Anomalous Right Coronary Artery: Non-ST Segment Elevation Myocardial Infarction (NSTEMI) in the Context of Drug Abuse.

Cureus
2025

STEMI From Left Main Compression by Pulmonary Artery Aneurysm Diagnosed With IVUS.

JACC. Case reports
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Surgical and radiologic anatomy : SRA
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Noninvasive Anatomical and Functional Imaging for Hemodynamic Relevance in Right Coronary Artery Anomalies.

JAMA cardiology
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European heart journal. Cardiovascular Imaging
2025

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ESC heart failure
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Frontiers in endocrinology
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Cabergoline-induced prolactinoma treatment and subsequent estrogen-driven vascular smooth muscle tumorigenesis in a middle-aged female: A case report.

International journal of surgery case reports
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A Rare Case of Femur Metastasis from Brain Meningioma.

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Infundibular origin of a duplicated anterior communicating artery mimicking an aneurysm.

Surgical and radiologic anatomy : SRA
2024

Case Report: Rare Bilateral Double Profunda Femoris Artery Variation: Clinical Implications and Considerations.

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Surgical and radiologic anatomy : SRA
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Severe Diffuse Takayasu Arteritis Manifestation in Childhood.

JACC. Case reports
2025

Progressive gray matter reduction in schizophrenia patients with persistent auditory hallucinations by causal structural covariance network analysis.

Psychological medicine
2025

[When rarity duplicates: myocardial non-compaction and single coronary artery, an association not to be underestimated].

Giornale italiano di cardiologia (2006)
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An Adult-Onset Case of Porokeratotic Eccrine Ostial and Dermal Duct Nevus (PEODDN) in a Previously Healthy 28-Year-Old Indian Male: A Case Report.

Cureus
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Kommerell's Diverticulum Masquerading in a Right Aortic Arch: A Vascular Surprise.

Methodist DeBakey cardiovascular journal
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Case Report: Anomalous origin of the left main coronary artery arising from the left ventricular outflow tract.

Frontiers in cardiovascular medicine
2025

Percutaneous Closure of Aortic-Pulmonary Artery Fistula in Cardiogenic Shock: The Modified Tootsie Roll Technique.

JACC. Case reports

Associações

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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Inferior wall ST-elevation myocardial infarction in a patient with a single coronary artery from the right coronary cusp trifurcating into the left anterior descending, left circumflex, and right coronary arteries: a rare coronary anomaly, case report.
    European heart journal. Case reports· 2026· PMID 41877722mais citado
  2. Case report of mitral valve replacement in a single coronary artery patient: devil is hidden in the details.
    European heart journal. Case reports· 2026· PMID 41798909mais citado
  3. A case report of J wave syndrome with abnormal potentials in both right and left ventricles and reversed J wave in lead V1.
    European heart journal. Case reports· 2026· PMID 41704830mais citado
  4. Isolated left ventricular apical hypoplasia: a case report.
    European heart journal. Case reports· 2026· PMID 41536733mais citado
  5. Fusiform dilatation of the ascending aorta and outpouching of the left A2 anterior cerebral artery segment in COL4A1 -related disorder.
    Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology· 2026· PMID 41514066mais citado
  6. Valve-sparing aortic root replacement after neonatal arterial switch operation.
    J Card Surg· 2021· PMID 33638201recente
  7. Single Coronary Artery Arising from the Right Sinus of Valsalva and the Role of Coronary Computed Tomography Angiography.
    S D Med· 2018· PMID 29991101recente
  8. [Assessment of congenital vascular rings with MDCT on children].
    Zhonghua Yi Xue Za Zhi· 2015· PMID 26815190recente
  9. Innovative hybrid procedure for dissection thoracic aorta in a patient with a previous bentall operation.
    Indian Heart J· 2008· PMID 19212026recente
  10. The 'aortic rim' recount: embolization of interatrial septal occluder into the main pulmonary artery bifurcation after atrial septal defect closure.
    Interact Cardiovasc Thorac Surg· 2007· PMID 17669873recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:99050(Orphanet)
  2. MONDO:0020391(MONDO)
  3. GARD:4586(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q55789325(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Artéria pulmonar proveniente da aorta
Compêndio · Raras BR

Artéria pulmonar proveniente da aorta

ORPHA:99050 · MONDO:0020391
Prevalência
Unknown
Casos
200 casos conhecidos
CID-10
Q25.7 · Outras malformações congênitas da artéria pulmonar
CID-11
Início
Infancy, Neonatal
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C5680322
Wikidata
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