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Pituicitoma
ORPHA:251623CID-10 · D44.3CID-11 · 2A00.0YDOENÇA RARA

É um tumor raríssimo, classificado como Grau I pela OMS (Organização Mundial da Saúde), o que significa que é de baixo risco. Ele é bem delimitado e de crescimento lento, surgindo da neuro-hipófise ou do infundíbulo (partes do cérebro) e é mais comum em adultos. Ele se caracteriza pela presença de células gliais (células de suporte do sistema nervoso) tumorais, que são alongadas e em forma de fuso. Essas células formam padrões em redemoinho ou agrupamentos de feixes entrelaçados. Os sinais e sintomas incluem problemas de visão, dor de cabeça, ausência de menstruação e diminuição do desejo sexual.

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Introdução

O que você precisa saber de cara

📋

É um tumor raríssimo, classificado como Grau I pela OMS (Organização Mundial da Saúde), o que significa que é de baixo risco. Ele é bem delimitado e de crescimento lento, surgindo da neuro-hipófise ou do infundíbulo (partes do cérebro) e é mais comum em adultos. Ele se caracteriza pela presença de células gliais (células de suporte do sistema nervoso) tumorais, que são alongadas e em forma de fuso. Essas células formam padrões em redemoinho ou agrupamentos de feixes entrelaçados. Os sinais e sintomas incluem problemas de visão, dor de cabeça, ausência de menstruação e diminuição do desejo sexual.

Publicações científicas
220 artigos
Último publicado: 2026 Jan

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
<1 / 1 000 000
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Casos conhecidos
171
pacientes catalogados
Início
Adult
🏥
SUS: Sem cobertura SUSScore: 0%
CID-10: D44.3
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

📏
Crescimento
8 sintomas
👁️
Olhos
1 sintomas

+ 11 sintomas em outras categorias

Características mais comuns

100%prev.
Neoplasia da hipófise posterior
100%prev.
Pituicitoma
90%prev.
Morfologia anormal da glândula pituitária
Muito frequente (99-80%)
55%prev.
Cefaleia
Frequente (79-30%)
55%prev.
Defeito do campo visual
Frequente (79-30%)
17%prev.
Anormalidade do nível circulante de adrenocorticotropina
Ocasional (29-5%)
20sintomas
Muito frequente (3)
Frequente (2)
Ocasional (13)
Muito raro (2)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 20 características clínicas mais associadas, ordenadas por frequência.

Neoplasia da hipófise posteriorNeoplasm of the posterior pituitary
Muito frequente100%
PituicitomaPituicytoma
Muito frequente100%
Morfologia anormal da glândula pituitáriaAbnormality of the pituitary gland
Muito frequente (99-80%)90%
CefaleiaHeadache
Frequente (79-30%)55%
Defeito do campo visualVisual field defect
Frequente (79-30%)55%

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2025
Total histórico220PubMed
Últimos 10 anos136publicações
Pico202121 papers
Linha do tempo
2025Hoje · 2026📈 2021Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Pituicitoma

🗺️

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Ensaios clínicos abertos e novidades científicas recentes

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Publicações mais relevantes

Timeline de publicações
138 papers (10 anos)
#1

Acromegaly in an elderly male with hepatic malignancy: a case report of a diagnostic dilemma.

Annals of medicine and surgery (2012)2026 Jan

Acromegaly is usually caused by a growth hormone (GH)-secreting pituitary adenoma; nonpituitary causes are rare, especially in elderly patients. Paraneoplastic insulin-like growth factor-1 (IGF-1) excess from hepatic malignancy is quite uncommon, and its coexistence with a pituitary infundibular lesion presents a diagnostic challenge. A 78-year-old diabetic man presented with coarse facial features, macroglossia, and increased interdental spacing. IGF-1 was elevated (218.6 ng/mL) with normal GH, ACTH, and prolactin. The 8 AM serum cortisol was high (36.27 μg/dL), suggesting ACTH-independent hypercortisolism. MRI brain revealed an enhancing pituitary infundibular lesion (pituicytoma vs granular cell tumor). CECT A + P exhibited a large hepatic mass with pulmonary metastases, elevated tumor markers (CEA, CA 19-9, AFP), and normal adrenal glands. Findings favored paraneoplastic IGF-1 excess and hypercortisolism from hepatic malignancy, with the pituitary lesion likely incidental. The family declined further workup, and the patient was lost to follow-up. Hepatic malignancy can rarely produce IGF-1 or cortisol-like substances, leading to acromegaly-like features and hypercortisolism independent of pituitary GH or ACTH secretion. The coexistence of paraneoplastic IGF-1 excess, ACTH-independent hypercortisolism, and an incidental pituitary lesion has not been previously reported. This case highlights the need to consider nonpituitary causes of acromegaly, especially in elderly patients with atypical biochemical or imaging findings. Non-pituitary causes of acromegaly should be considered in elderly patients with atypical biochemical profiles, as hepatic malignancy can rarely produce paraneoplastic IGF-1 excess even in the presence of incidental pituitary lesions.

#2

Posterior transpetrosal approach to a suprasellar retroinfundibular pituicytoma: A case report and comprehensive literature review.

Brain &amp; spine2025

Pituicytomas are rare benign glial neoplasms (WHO grade I) located in the sellar or suprasellar regions, arising from the neurohypophysis and infundibular area. They typically present with symptoms due to the slow growth of the tumor, including hormonal changes, visual impairment, and headaches. This case report evaluates the effectiveness of the posterior transpetrosal approach for the resection of a retroinfundibular suprasellar pituicytoma, focusing on preserving pituitary function and minimizing surgical risks. We present a 59-year-old female with a pituicytoma diagnosed by MRI and digital subtraction angiography (DSA). Preoperative embolization was performed to reduce the tumor's vascularity. The patient underwent a left posterior transpetrosal approach for tumor resection, with key surgical steps focusing on preserving the pituitary stalk, optic chiasm, and perforating vessels. The posterior transpetrosal approach provided excellent exposure, enabling near-total resection of the tumor. The patient had no new neurological deficits postoperatively, and follow-up MRI at 6 months showed no tumor recurrence. This case demonstrates the safety and efficacy of the posterior transpetrosal approach for pituicytoma resection. The approach allowed for optimal visualization and preservation of critical structures, particularly the pituitary stalk, leading to a favorable clinical outcome. Our findings, supported by a literature review, suggest that this technique is a valuable option for tumors in retroinfundibular and suprasellar locations.

#3

Posterior pituitary tumors and other rare entities involving the pituitary gland.

Brain pathology (Zurich, Switzerland)2025 Jan

Non-neuroendocrine tumors account for around 10% of all primary neoplasms of the sella. If meningiomas, craniopharyngiomas, and germ cell tumors are excluded, the remaining lesions include a broad spectrum of uncommon, benign, and aggressive, often diagnostically challenging lesions. This review aims to summarize the essential clinicopathological features of tumors of the posterior pituitary gland, infundibulum spectrum expressing thyroid transcription factor 1, and primary sellar atypical rhabdoid teratoid tumor, and provide the criteria for their diagnosis and management.

#4

Transnasal endoscopic removal of a pituicytoma: a case report.

Frontiers in oncology2025

Pituicytoma is an exceedingly rare tumor of the pituitary gland, classified as WHO grade 1. Its presentation varies widely, often mimicking other pituitary or sellar region tumors. This report discusses a unique case of pituicytoma in a young female presenting with a combination of visual disturbances, infertility, and endocrine dysfunction, emphasizing the role of multidisciplinary management and minimally invasive surgical techniques.

#5

Distinctive Characteristics of Rare Sellar Lesions Mimicking Pituitary Adenomas: A Collection of Unusual Neoplasms.

Cancers2025 Aug 04

Background/Objectives: Pituitary tumors account for over 90% of all sellar region masses. However, a spectrum of rare neoplastic, inflammatory, infectious, and vascular lesions-benign and malignant-can arise in the intra- and parasellar compartments and clinically and radiologically mimic PitNETs. We report a cohort of 47 such rare and cystic midline intracranial lesions, emphasizing their distinctive morphological, clinical, and imaging features and the personalized treatment strategies applied. Methods: In this retrospective single-center study, we reviewed all patients treated for suspected PitNETs via transsphenoidal approach between 2015 and 2024. Of 529 surgical cases, we excluded confirmed PitNETs, meningiomas, and classical intradural craniopharyngiomas. Collected data encompassed patient demographics, tumor characteristics, presenting symptoms, extent of resection or medical therapy, endocrine outcomes, and follow-up information. Results: Among all 529 patients who underwent surgical treatment for sellar lesions from 2015 to 2024, 47 cases (8.9%) were identified as rare or cystic masses. Forty-six underwent transsphenoidal resection; one patient with hypophysitis received corticosteroid therapy alone. Presenting symptoms included headache (n = 16), dizziness (n = 5), oculomotor disturbances (n = 2), and visual impairment (n = 17). Endocrine dysfunction was found in 30 patients, 27 of whom required hydrocortisone replacement. Histopathological diagnoses were led by colloid cysts (n = 14) and Rathke's cleft cysts (n = 11). The remaining 22 cases comprised plasmacytoma, germinoma, lymphoma, pituicytoma, inverted papilloma, metastatic carcinoma, chordoma, nasopharyngeal carcinoma, chloroma, and other rare entities. Preoperative imaging diagnosis proved incorrect in 38% (18/47) of cases, with several lesions initially misidentified as PitNETs. Conclusions: Nearly 9% of presumed PitNETs were rare, often benign or inflammatory lesions requiring distinct management. Most could be safely resected and demonstrated excellent long-term outcomes. Yet, despite advanced imaging techniques, accurate preoperative differentiation remains challenging, with over one-third misdiagnosed. Clinical red flags-such as early hormone deficits, rapid progression or atypical imaging findings-should prompt early interdisciplinary evaluation and, when indicated, image-guided biopsy to avoid unnecessary surgery and ensure tailored therapy.

Publicações recentes

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📚 EuropePMC125 artigos no totalmostrando 134

2026

Acromegaly in an elderly male with hepatic malignancy: a case report of a diagnostic dilemma.

Annals of medicine and surgery (2012)
2025

Transnasal endoscopic removal of a pituicytoma: a case report.

Frontiers in oncology
2025

Distinctive Characteristics of Rare Sellar Lesions Mimicking Pituitary Adenomas: A Collection of Unusual Neoplasms.

Cancers
2025

Histopathological Types, Clinical Presentation, Imaging Studies, Treatment Strategies, and Prognosis of Posterior Pituitary Tumors: An Updated Review.

Journal of clinical medicine
2025

Hypopituitarism in non-neuroendocrine pituitary tumors: a systematic review.

Reviews in endocrine &amp; metabolic disorders
2025

Three cases of pituicytoma with a review of the literature and insight into a rare variant of ependymal pituicytoma.

Clinical neuropathology
2025

A Rare Case of Pituicytoma During Pregnancy.

JCEM case reports
2025

Posterior transpetrosal approach to a suprasellar retroinfundibular pituicytoma: A case report and comprehensive literature review.

Brain &amp; spine
2025

Clinical, surgical, and endocrine outcome following treatment of posterior pituitary tumors: a retrospective cohort study.

Pituitary
2025

TTF1-positive posterior pituitary tumors: a single-center experience of 10 years.

Endocrine
2025

Oncocytic pituicytoma in a patient with Cushing's disease: a case report and narrative literature review.

Frontiers in endocrinology
2024

A Steerable Microcatheter Effectively Worked in Tumor Embolization.

Journal of neuroendovascular therapy
2024

[Pituicitoma in a patient with neurofibromatosis type 1].

Medicina
2024

Sustained Response to Brigatinib in an Aggressive Relapsing Atypical Pituicytoma With ELM4-ALK Fusion.

JCO precision oncology
2024

TTF-1 immunohistochemistry in primary CNS tumors: A systematic review.

Clinical neuropathology
2024

Pituitary spindle cell oncocytoma: Two cases report and literature review.

International journal of surgery case reports
2025

Posterior pituitary tumors and other rare entities involving the pituitary gland.

Brain pathology (Zurich, Switzerland)
2024

Intraventricular pituicytoma: illustrative case.

Journal of neurosurgery. Case lessons
2024

Pituitary Apoplexy: Description of Medical and Surgical Treatment and Clinical, Visual, and Endocrinological Outcomes During the SARS-CoV-2 Pandemic and Over Three Years.

Cureus
2024

Pituitary neuroendocrine tumors and granular cell pituicytomas at autopsy: Incidence, cell types, locations, and histogenesis in 150 pituitary glands.

American journal of clinical pathology
2024

[18F]FET PET/MRI: An Accurate Technique for Detection of Small Functional Pituitary Tumors.

Journal of nuclear medicine : official publication, Society of Nuclear Medicine
2023

An institutional experience in applying quality improvement measures to pituitary surgery: clinical and resource implications.

Neurosurgical focus
2023

Collision sellar lesion: coexistence of growth hormone-secreting pituitary neuroendocrine tumor and pituicytoma.

Polish archives of internal medicine
2023

Supra-sellar granular cell tumor: Report of a case with literature review.

International journal of surgery case reports
2023

Pituicytoma: A rare tumor of the sella. A case report and review of literature for diagnosis and management.

Surgical neurology international
2023

Synchronous Posterior and Anterior Pituitary Tumors: A Case Report of a Hypothetic Paracrine Relationship.

Asian journal of neurosurgery
2023

A rare case of pituicytoma-related hyperprolactinemia due to mass effect on infundibular stalk-Case report.

International journal of surgery case reports
2023

Granular cell tumor of the neurohypophysis presenting as a third ventricle mass.

Neuropathology : official journal of the Japanese Society of Neuropathology
2023

Epigenetic Alteration of H3K27me3 as a Possible Oncogenic Mechanism of Central Neurocytoma.

Laboratory investigation; a journal of technical methods and pathology
2023

Primary papillary epithelial tumor of the sella and posterior pituitary tumor show similar (epi)genetic features and constitute a single neuro-oncological entity.

Neuro-oncology
2023

Surgical approach to the treatment of pituicytoma. Report of five cases and a literature review.

World neurosurgery: X
2023

Pituitary tumours: molecular and genetic aspects.

The Journal of endocrinology
2023

Co-existence of pituicytoma and corticotroph adenoma in a patient with Cushing's disease.

Pathology
2023

Pituicytoma: A case report.

Asian journal of surgery
2022

Pituicytoma: A rare case report of sellar and suprasellar tumor.

International journal of surgery case reports
2023

Pituicytoma with pleomorphism: A case report with cytological findings.

Diagnostic cytopathology
2022

Pituicytoma Associated with Suspected Cushing's Disease: Two Case Reports and a Literature Review.

Journal of clinical medicine
2022

Multiple tumorous lesions of the pituitary gland.

Hormones (Athens, Greece)
2022

The Diagnostic Impact of Epigenomics in Pituicyte-derived Tumors: Report of an Unusual Sellar Lesion with Extensive Hemorrhage and Necrotic Debris.

Endocrine pathology
2022

[Pituicytoma: a clinicopathological analysis of five cases].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2022

Recommendation to improve the WHO classification of posterior pituitary tumors as a unique entity: evidence from a large case series.

Endocrine connections
2022

[Pituicytoma: a clinicopathological analysis of twenty-one cases].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2023

Surgical management of pituicytomas: a single-center case series.

Acta neurologica Belgica
2022

Overview of the 2022 WHO Classification of Pituitary Tumors.

Endocrine pathology
2022

Histopathology of Pituitary Lesions.

Otolaryngologic clinics of North America
2021

Pituicytoma in a Young Male and Review of Literature.

Neurology India
2022

Outcome of endoscopic transcortical intraventricular biopsy of isolated thickened pituitary stalk lesions in children.

Journal of neurosurgery. Pediatrics
2021

Pituicytoma: Four cases with unusual imaging features and a literature review.

Neuro endocrinology letters
2021

TTF1-positive Papillary Epithelial Tumor of Pituitary: An Epithelial Variant of Pituicytoma?: Retraction.

Applied immunohistochemistry &amp; molecular morphology : AIMM
2021

A Rare Case of Pituicytoma Presenting Cystic Formation.

Brain tumor research and treatment
2021

Genetic and epigenetic characterization of posterior pituitary tumors.

Acta neuropathologica
2021

Primary Tumors of the Pituitary Gland: Radiologic-Pathologic Correlation.

Radiographics : a review publication of the Radiological Society of North America, Inc
2021

Incidental Intra-Infundibular Pituicytoma.

Acta endocrinologica (Bucharest, Romania : 2005)
2021

Two challenging cases of pituicytoma.

Hormones (Athens, Greece)
2021

Clinical features, radiological profiles, pathological features and surgical outcomes of pituicytomas: a report of 11 cases and a pooled analysis of individual patient data.

Military Medical Research
2022

Skull Base Tumors: Neuropathology and Clinical Implications.

Neurosurgery
2021

Co-occurrence of Pituitary Neuroendocrine Tumors (PitNETs) and Tumors of the Neurohypophysis.

Endocrine pathology
2021

Treatment and prognostic factors of pituicytoma: a single-center experience and comprehensive literature review.

Pituitary
2021

Pituicytoma: Report of three cases and a systematic literature review.

Clinical neurology and neurosurgery
2021

[The 2017 WHO classification of pituitary tumors].

Der Pathologe
2021

Posterior pituitary tumours: patient outcomes and determinants of disease recurrence or persistence.

Endocrine connections
2021

Neuropathology of Pituitary Adenomas and Sellar Lesions.

Neurosurgery
2021

Genomics and Epigenomics of Pituitary Tumors: What Do Pathologists Need to Know?

Endocrine pathology
2021

Pituicytoma: Case report of a rare suprasellar tumor.

Indian journal of pathology &amp; microbiology
2021

Clinical-Pathological, Immunohistochemical, and Genetic Characterization of a Series of Posterior Pituitary Tumors.

Journal of neuropathology and experimental neurology
2021

Management of sellar and parasellar tumors becoming symptomatic during pregnancy: a practical algorithm based on multi-center experience and systematic literature review.

Pituitary
2020

Infectious Complications of Expanded Endoscopic Transsphenoidal Surgery: A Retrospective Cohort Analysis of 100 Cases.

Journal of neurological surgery. Part B, Skull base
2021

Limited utility of 5-ALA optical fluorescence in endoscopic endonasal skull base surgery: a multicenter retrospective study.

Journal of neurosurgery
2020

Epithelioid Pituicytoma: Expanding the Morphologic Spectrum of a Rare Neoplasm.

Journal of neuropathology and experimental neurology
2021

Primary Tumors of the Posterior Pituitary Gland: A Systematic Review of the Literature in Light of the New 2017 World Health Organization Classification of Pituitary Tumors.

World neurosurgery
2020

Adenohypophyseal hyperfunction syndromes and posterior pituitary tumors: prevalence, clinical characteristics, and pathophysiological mechanisms.

Endocrine
2020

Pituicytoma associated with Cushing's disease: a case report and literature review.

Journal of surgical case reports
2020

Clinical features and endoscopic findings of granular cell tumor of the sellar region: A case report and review of the literature.

Surgical neurology international
2020

A rare case report of pituicytoma with biphasic pattern and admixed with scattered Herring bodies.

World journal of surgical oncology
2020

Acellular dermal matrix as an alternative to autologous fascia lata for skull base repair following extended endoscopic endonasal approaches.

Acta neurochirurgica
2020

A recurrent case of pituicytoma 16 years later.

Annals of the Royal College of Surgeons of England
2020

Concurrent Pituicytoma, Meningioma, and Cavernomas After Cranial Irradiation for Childhood Acute Lymphoblastic Leukemia.

World neurosurgery
2020

Intraoperative cytology of pituicytomas.

Diagnostic cytopathology
2020

Pituicytoma Associated with Acromegaly and Cushing Disease.

World neurosurgery
2020

TTF1-positive Papillary Epithelial Tumor of Pituitary: An Epithelial Variant of Pituicytoma?

Applied immunohistochemistry &amp; molecular morphology : AIMM
2019

The coexistence of infundibular pituicytoma and Cushing's disease due to pituitary adenoma: A case report.

Endocrine regulations
2020

Tumors of the Neurohypophysis: One Unit's Experience and Literature Review.

World neurosurgery
2019

A rare case of pituicytoma presenting with severe Cushing disease: A case report and review of literature.

Medicine
2019

Hypothalamic Endocrine Tumors: An Update.

Journal of clinical medicine
2019

Surgical resection of granular cell tumor of the sellar region: three indications.

Pituitary
2019

Panniculitis Under Successful Targeted Inhibition of the MAPK/ERK Signaling Pathway in a Patient With BRAF V600E-mutated Spindle Cell Oncocytoma of the Pituitary Gland.

Anticancer research
2019

Rare Thyroid Transcription Factor 1-Positive Tumors of the Sellar Region: Barrow Neurological Institute Retrospective Case Series.

World neurosurgery
2019

Histologic, immunohistochemical, and molecular features of pituicytomas and atypical pituicytomas.

Acta neuropathologica communications
2019

Primary tumors of the posterior pituitary: A systematic review.

Reviews in endocrine &amp; metabolic disorders
2019

Application of indocyanine green fluorescence endoscopic system in transsphenoidal surgery for pituitary tumors.

Acta neurochirurgica
2019

Endoscopic Endonasal Approach Combined with a Simultaneous Transcranial Approach for Giant Pituitary Tumors.

World neurosurgery
2019

Posterior pituitary tumours: the spectrum of a unique entity. A clinical and histological study of a large case series.

Endocrine
2018

Is spindle cell oncocytoma a true entity or a variant of pituicytoma? A case report with review of literature.

Neurology India
2018

Epithelioid pituicytoma: An unusual case report.

Surgical neurology international
2018

Combined Endoscopic Endonasal and Video-microscopic Transcranial Approach with Preoperative Embolization for a Posterior Pituitary Tumor.

World neurosurgery
2018

Management of pituicytomas: a multicenter series of eight cases.

Pituitary
2019

Clinical features, diagnosis and therapy of pituicytoma: an update.

Journal of endocrinological investigation
2018

An exceptional presentation of pituicytoma apoplexy: A case report.

Oncology letters
2018

Correlations between clinical hormone change and pathological features of pituicytoma.

British journal of neurosurgery
2020

Non-adenomatous pituitary tumours mimicking functioning pituitary adenomas.

British journal of neurosurgery
2018

Histopathologic Findings in Canine Pituitary Glands.

Veterinary pathology
2018

Low-Grade Glioma of the Neurohypophysis: Clinical Characteristics and Surgical Outcomes.

World neurosurgery
2018

Welcoming the new WHO classification of pituitary tumors 2017: revolution in TTF-1-positive posterior pituitary tumors.

Brain tumor pathology
2018

Freiburg Neuropathology Case Conference : Tumor Located in the Anterior Portion of the Third Ventricle.

Clinical neuroradiology
2017

Sporadic Hemangioblastoma Arising from the Infundibulum.

Journal of radiology case reports
2018

What's new in pituitary pathology?

Histopathology
2017

Pituicytoma with Significant Tumor Vascularity Mimicking Pituitary Macroadenoma.

Brain tumor research and treatment
2018

First Depiction of Flow Voids to Differentiate Pituicytomas from Giant Adenomas.

World neurosurgery
2017

Extent of surgical resection and tumor size predicts prognosis in granular cell tumor of the sellar region.

Acta neurochirurgica
2017

[Pituicytoma: report of a case].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2017

The 2017 World Health Organization classification of tumors of the pituitary gland: a summary.

Acta neuropathologica
2017

Pituicytoma: Review of commonalities and distinguishing features among TTF-1 positive tumors of the central nervous system.

Annals of diagnostic pathology
2017

Overview of the 2017 WHO Classification of Pituitary Tumors.

Endocrine pathology
2017

Recurrent Pituicytoma with Pseudoaneurysm: Report of a Challenging Case.

World neurosurgery
2017

Pituicytoma-An outlook on possible targeted therapies.

CNS neuroscience &amp; therapeutics
2018

WHO 2016 classification: changes and advancements in the diagnosis of miscellaneous primary CNS tumours.

Neuropathology and applied neurobiology
2016

Pituicytoma: A report of three cases and literature review.

Oncology letters
2016

Histological features of pituitary adenomas and sellar region masses.

Current opinion in endocrinology, diabetes, and obesity
2017

Immunoprofiling of glial tumours of the neurohypophysis suggests a common pituicytic origin of neoplastic cells.

Pituitary
2016

Coexisting pituicytoma and pituitary adenoma: a second coincidence?

Human pathology
2016

Coexisting pituicytoma and pituitary adenoma; a second coincidence?-reply.

Human pathology
2016

Proceedings of the 2015 National Toxicology Program Satellite Symposium.

Toxicologic pathology
2016

Pituicytoma Coexisting With Corticotroph Hyperplasia: Literature Review With One Case Report.

Medicine
2016

The clinicopathological features of pituicytoma and the differential diagnosis of sellar glioma.

Neuropathology : official journal of the Japanese Society of Neuropathology
2015

Pituicytoma and Cushing's Disease in a 7-Year-Old Girl: A Mere Coincidence?

Pediatrics
2016

Synchronous pituitary adenoma and pituicytoma.

Human pathology
2015

A spontaneously occurring malignant pituicytoma in a male sprague dawley rat.

Journal of toxicologic pathology
2015

[Pituicytoma: a study of 3 cases with literature review].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2015

Prolactin-producing pituitary adenoma with atypical spindle cell morphology: a case report.

World journal of surgical oncology
2015

The Expanding Spectrum of Disease Treated by the Transnasal, Transsphenoidal Microscopic and Endoscopic Anterior Skull Base Approach: A Single-Center Experience 2008-2015.

World neurosurgery
2015

Suprasellar chordoid neoplasm with expression of thyroid transcription factor 1: evidence that chordoid glioma of the third ventricle and pituicytoma may form part of a spectrum of lineage-related tumors of the basal forebrain.

Human pathology
2015

TTF-1-positive oncocytic sellar tumor with follicle formation/ependymal differentiation: non-adenomatous tumor capable of two different interpretations as a pituicytoma or a spindle cell oncocytoma.

Brain tumor pathology
2015

Second-stage transsphenoidal approach (TSA) for highly vascular pituicytomas in children.

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
2015

Intrasellar pilocytic astrocytomas: clinical, imaging, pathological, and surgical findings.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia

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Doenças relacionadas

Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico

Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Acromegaly in an elderly male with hepatic malignancy: a case report of a diagnostic dilemma.
    Annals of medicine and surgery (2012)· 2026· PMID 41497147mais citado
  2. Posterior transpetrosal approach to a suprasellar retroinfundibular pituicytoma: A case report and comprehensive literature review.
    Brain &amp; spine· 2025· PMID 40206592mais citado
  3. Posterior pituitary tumors and other rare entities involving the pituitary gland.
    Brain pathology (Zurich, Switzerland)· 2025· PMID 39350562mais citado
  4. Transnasal endoscopic removal of a pituicytoma: a case report.
    Frontiers in oncology· 2025· PMID 41256330mais citado
  5. Distinctive Characteristics of Rare Sellar Lesions Mimicking Pituitary Adenomas: A Collection of Unusual Neoplasms.
    Cancers· 2025· PMID 40805263mais citado
  6. Histopathological Types, Clinical Presentation, Imaging Studies, Treatment Strategies, and Prognosis of Posterior Pituitary Tumors: An Updated Review.
    J Clin Med· 2025· PMID 40648926recente
  7. Hypopituitarism in non-neuroendocrine pituitary tumors: a systematic review.
    Rev Endocr Metab Disord· 2025· PMID 40360862recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:251623(Orphanet)
  2. MONDO:0006372(MONDO)
  3. GARD:20711(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q7199535(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Pituicitoma
Compêndio · Raras BR

Pituicitoma

ORPHA:251623 · MONDO:0006372
Prevalência
<1 / 1 000 000
Casos
171 casos conhecidos
Herança
Not applicable
CID-10
D44.3 · Neoplasia de comportamento incerto ou desconhecido da glândula hipófise (pituitária)
CID-11
Início
Adult
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C2986550
EuropePMC
Wikidata
Papers 10a
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