Scott-Taor syndrome is a benign bone dysplasia with less than 50 cases reported. The latter is an autosomal dominant disease characterized mainly by patellar a/hypoplasia and bilateral malunion ossification of the ischiopubic junction, a wide gap between the first and second toes. The diagnosis is clinical and radiographical. Here, we present a 17-year-old female patient with this rare syndrome. Considering this diagnosis is crucial for a better understanding of the pathology and to effectively contextualize the patient's clinical findings.