Pequeno tumor de células redondas com diferenciação neural originado de tecidos moles ou ossos.
Introdução
O que você precisa saber de cara
Pequeno tumor de células redondas com diferenciação neural originado de tecidos moles ou ossos.
Tem tratamento?
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Entender a doença
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 20 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 37 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Genes associados
1 gene identificado com associação a esta condição. Padrão de herança: Not applicable.
Sequence-specific transcriptional activator (PubMed:24100448, PubMed:26316623, PubMed:28255014). Recognizes the DNA sequence 5'-C[CA]GGAAGT-3'
Nucleus
Ewing sarcoma
A highly malignant, metastatic, primitive small round cell tumor of bone and soft tissue that affects children and adolescents. It belongs to the Ewing sarcoma family of tumors, a group of morphologically heterogeneous neoplasms that share the same cytogenetic features. They are considered neural tumors derived from cells of the neural crest. Ewing sarcoma represents the less differentiated form of the tumors.
Medicamentos e terapias
Mecanismo: DNA topoisomerase II inhibitor
Mecanismo: DNA topoisomerase II alpha inhibitor
Mecanismo: Tubulin inhibitor
Mecanismo: DNA topoisomerase II alpha inhibitor
Mecanismo: Tubulin inhibitor
Mecanismo: DNA topoisomerase II inhibitor
Variantes genéticas (ClinVar)
108 variantes patogênicas registradas no ClinVar.
Vias biológicas (Reactome)
1 via biológica associada aos genes desta condição.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Tumor neuroectodérmico primitivo periférico
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Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.
Pesquisa ativa
Ensaios clínicos abertos e novidades científicas recentes
Ensaios em destaque
🟢 Recrutando agora
4 pesquisas recrutando participantes. Converse com seu médico sobre a possibilidade de participar.
Outros ensaios clínicos
209 ensaios clínicos encontrados, 14 ativos.
Publicações mais relevantes
Neoadjuvant chemotherapy-enabled tumor conversion and surgical resection in pediatric primary pulmonary Ewing sarcoma: a case report.
Ewing sarcoma (EWS) is a highly aggressive malignant tumor that primarily affects the skeletal system in children and adolescents. Primary pulmonary Ewing sarcoma (PPEWS) is extremely rare, particularly in children, with very few cases reported in the literature. This report describes a 10-year-old girl who was admitted with an intermittent cough lasting over 7 months. Chest computed tomography (CT) revealed a mass in the right lower lung lobe. Bronchoscopic biopsy demonstrated a highly malignant undifferentiated small round cell tumor, with immunohistochemistry confirming EWS (positive for CD99, NKX2.2, and FLI-1). After 8 cycles of VDC/IE neoadjuvant chemotherapy, neoadjuvant therapy enabled tumor conversion from unresectable to resectable status. Postoperative pathology confirmed extraskeletal EWS/peripheral primitive neuroectodermal tumor (pPNET) following right middle and lower lobectomy, with good postoperative recovery. Following a multidisciplinary team (MDT) consensus, the patient initiated adjuvant chemotherapy utilizing the same VDC/IE regimen. As of the latest follow-up, she has successfully completed six cycles of adjuvant chemotherapy, and no clinical or radiological signs of recurrence have been observed. This case underscores the extreme rarity of PPEWS in children and the complexities of its diagnosis and treatment. Neoadjuvant chemotherapy can facilitate tumor conversion, while surgery plays a pivotal role in localized cases with incomplete chemotherapeutic response. Multidisciplinary management is essential for optimizing outcomes.
Percutaneous Ultrasound-Guided Intratumoral Injection of Lauromacrogol and Pingyangmycin in the Treatment of Advanced pPNET in Children.
To evaluate real-time ultrasound-guided intratumoral lauromacrogol + pingyangmycin for pediatric peripheral primitive neuroectodermal tumors (pPNET) refractory to chemotherapy. Five tumor lesions in three children from our institution were treated under real-time ultrasound guidance. Color Doppler and contrast-enhanced ultrasound assessed tumor hemodynamics and size pre- and post- injection. Pre-injection, all tumors showed rich blood flow (mixed arteriovenous signals). Post-injection contrast ultrasound revealed significantly reduced arterial-phase blood supply. At 4-week follow-up, all five tumors showed statistically significant volume reduction (p < 0.05) and reduced tumor-related pain. No adverse reactions such as bleeding and pain occurred during injection. Ultrasound-guided intratumoral lauromacrogol + pingyangmycin injection effectively reduces tumor blood supply, destroys local vasculature, and shrinks tumor volume in end-stage pediatric pPNET. It is a safe and effective local palliative treatment.
Multimodal Treatment of a Peripheral Primitive Neuroectodermal Tumor Originating From the Thoracic Cavity in a Dog.
Peripheral primitive neuroectodermal tumor (pPNET) is a very rare, highly malignant tumor encountered in young dogs, with only four necropsy cases in the veterinary literature. A 1.5-year-old male intact French Bulldog presented for evaluation of progressive left forelimb lameness and ipsilateral Horner's syndrome. Whole body computed tomography identified a 12 cm mediastinal mass with extension into the vertebral canal and multifocal metastatic lesions. Histological and immunohistochemical results were consistent with a pPNET. Chemotherapy, radiation therapy, immunotherapy, and targeted therapy were administered. Precision-based tumor testing, including DNA sequencing and chemosensitivity assays, were performed to guide systemic treatment recommendations. A partial remission was observed 3.5 months from presentation based on imaging and improved clinical status. After 7 months of treatment, diffuse metastatic disease, including intracranial spread, was observed and the dog was euthanized. This PDQ cancer information summary has current information about the treatment of childhood Ewing sarcoma. It is meant to inform and help patients, families, and caregivers. It does not give formal guidelines or recommendations for making decisions about health care. Editorial Boards write the PDQ cancer information summaries and keep them up to date. These Boards are made up of experts in cancer treatment and other specialties related to cancer. The summaries are reviewed regularly and changes are made when there is new information. The date on each summary ("Date Last Modified") is the date of the most recent change. The information in this patient summary was taken from the health professional version, which is reviewed regularly and updated as needed, by the PDQ Pediatric Treatment Editorial Board.
Primary ovarian peripheral primitive neuroectodermal tumor presented with breast metastasis; Case report.
Ewing sarcoma family tumors (ESFT) pose diagnostic challenges, which largely depend on the primary site of involvement and tumor stage. Despite advancements in treatment, metastatic ESFTs remain associated with poor outcomes. This case describes a 21-year-old woman who, in July 2022, presented with a left breast mass identified through ultrasound and CT scan, along with abdominal distention. A biopsy of the breast mass confirmed metastatic extraskeletal Ewing sarcoma. Further imaging revealed an ovarian mass, with subsequent biopsy confirming ovarian origin as extraskeletal Ewing sarcoma. The breast mass was identified as metastatic based on imaging features, including irregular margins and CT scan confirmation of widespread metastasis. Histopathology and immunohistochemistry confirmed Ewing sarcoma, consistent with the ovarian mass pathology that was the primary site. She underwent 15 cycles of VDC/IE chemotherapy ((vincristine, doxorubicin, and cyclophosphamide) for 2 days and 5 days IE (ifosfamide etoposide)), resulting in tumor cytoreduction. However, in less than 2 years, she developed metastases to the dura, spine, and bone, with optic nerve involvement. Despite treatment with radiotherapy and two cycles of high-dose Ifosfamide chemotherapy, her condition deteriorated, and she passed away in April 2024. This case underscores the complexity of managing metastatic ESFTs. Further research is needed to improve outcomes and establish treatment protocols for this malignancy.
Challenges in Diagnosing Primary Intracranial Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report.
Primary intracranial Ewing Sarcoma/peripheral Primitive Neuroectodermal Tumor (EWS/pPNET) is exceedingly rare and easy to misdiagnose. We present a case involving a 23-year-old male who presented with headaches and vomiting. The preoperative brain imaging revealed an irregular mass in the left parietal lobe, initially misdiagnosed as meningioma. However, the surgical specimen was ultimately diagnosed as primary intracranial EWS/pPNET. The patient underwent a total tumor resection, followed by adjuvant chemotherapy and radiotherapy. No recurrence or distant metastasis was observed 18 months after the surgery. When the imaging features of young patients' lesions are solid, aggressive, and unevenly enhanced masses, physicians should be aware of the possibility of primary intracranial EWS/pPNET, and if possible, Gross Total Resection (GTR) and intensive chemotherapy and radiotherapy are recommended. This PDQ cancer information summary for health professionals provides comprehensive, peer-reviewed, evidence-based information about the treatment of childhood Ewing sarcoma and undifferentiated small round cell sarcomas of bone and soft tissue. It is intended as a resource to inform and assist clinicians in the care of their patients. It does not provide formal guidelines or recommendations for making health care decisions. This summary is reviewed regularly and updated as necessary by the PDQ Pediatric Treatment Editorial Board, which is editorially independent of the National Cancer Institute (NCI). The summary reflects an independent review of the literature and does not represent a policy statement of NCI or the National Institutes of Health (NIH).
Publicações recentes
Neoadjuvant chemotherapy-enabled tumor conversion and surgical resection in pediatric primary pulmonary Ewing sarcoma: a case report.
Percutaneous Ultrasound-Guided Intratumoral Injection of Lauromacrogol and Pingyangmycin in the Treatment of Advanced pPNET in Children.
Multimodal Treatment of a Peripheral Primitive Neuroectodermal Tumor Originating From the Thoracic Cavity in a Dog.
Ewing Sarcoma Treatment (PDQ®): Patient Version.
📚 EuropePMC199 artigos no totalmostrando 111
Neoadjuvant chemotherapy-enabled tumor conversion and surgical resection in pediatric primary pulmonary Ewing sarcoma: a case report.
Frontiers in oncologyPercutaneous Ultrasound-Guided Intratumoral Injection of Lauromacrogol and Pingyangmycin in the Treatment of Advanced pPNET in Children.
Journal of clinical ultrasound : JCUMultimodal Treatment of a Peripheral Primitive Neuroectodermal Tumor Originating From the Thoracic Cavity in a Dog.
Journal of veterinary internal medicinePrimary ovarian peripheral primitive neuroectodermal tumor presented with breast metastasis; Case report.
Rare tumorsChallenges in Diagnosing Primary Intracranial Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report.
Current medical imagingAxillary lesion in a young adult ends up to a peculiar diagnosis: primitive neuro-ectodermal tumor (PNET) of ulnar nerve: a rare case report.
Annals of medicine and surgery (2012)Concurrent delayed recurrence of peripheral primitive neuroectodermal tumors in orbital and sellar/suprasellar regions in an older adult.
European journal of ophthalmologyPrimary Ewing's sarcoma of the intestine: case report and literature review.
Frontiers in oncologyAskin's Tumor in the Chest Wall-a Rare Clinical Entity and Review of Literature.
Indian journal of surgical oncologyEwing sarcoma with intra thoracic and multiple extra thoracic metastases in a young adult male: A case report.
International journal of surgery case reportsPrimary intracranial peripheral primitive neuroectodermal tumor: lessons from an exceptionally rare neoplasm. Illustrative case.
Journal of neurosurgery. Case lessonsExtraskeletal Ewing's sarcoma of supraglottis: A rare case report.
Oral oncologyClinical and histopathological spectrum of cranial small round cell tumors: An experience from a tertiary care center.
Journal of cancer research and therapeuticsPrimary Intracranial Ewing Sarcoma With EWSR1-FLI1 Gene Translocation Mimicking a Meningioma and a Multidisciplinary Therapeutic Approach: A Case Report and Systematic Review of Literatures.
Brain tumor research and treatmentDetection of various fusion genes by one-step RT-PCR and the association with clinicopathological features in 242 cases of soft tissue tumor.
Frontiers in cell and developmental biologyAskin's Tumor a Rare Clinical Entity of Thoracopulmonary Region Cresenting as a Case of Paraparesis: Findings on 18F-FDG PET/CT.
Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, IndiaPeripheral Primitive Neuroectodermal Tumor: A Rare Case in Pediatrics.
CureusAskin Tumor - Presenting as a Case of Paraparesis: A Rare Clinical Entity. Case Report and Findings on 18F-Fluorodeoxyglucose-Positron Emission Tomography/Computed Tomography.
Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, IndiaPeripheral primitive neuroectodermal tumor of the orbit in Graves' ophthalmopathy - A rare presentation.
Saudi journal of ophthalmology : official journal of the Saudi Ophthalmological SocietyIntracranial peripheral primitive neuroectodermal tumor presenting as neurosurgical emergency: A report of two cases.
Journal of neurosciences in rural practicePeripheral primitive neuroectodermal tumor orbit in an elderly woman.
Oman journal of ophthalmologyPrimary intracranial extraosseous Ewing's sarcoma of the skull base in an elderly adult: illustrative case.
Journal of neurosurgery. Case lessonsThe prognostic factors of Ewing sarcoma/peripheral primitive neuroectodermal tumor: A retrospective analysis of 67 patients at a single center.
Medicine[Peripheral primitive neuroectodermal tumor in the oropharynx of a child: a case report].
Zhonghua er bi yan hou tou jing wai ke za zhi = Chinese journal of otorhinolaryngology head and neck surgeryPrimary Ewing's sarcoma (ES)/peripheral primitive neuroectodermal tumor (pPNET) of the tongue in a child: A case report.
Oral oncologyPeripheral primitive neuroectodermal tumor: a case report.
Journal of medical case reportsPrimary intracranial peripheral primitive neuroectodermal tumor in an adult patient with aphasia: A rare case report.
Clinical case reportsPrimary intradural extramedullary extraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumor (PIEES/PNET) of the thoracolumbar spine: A case report and literature review.
Open medicine (Warsaw, Poland)Primary Mediastinal Ewing sarcoma presenting as a massive lung lesion with a mediastinal shift.
Clinical case reportsPrimary Spinal Extradural Extraosseous Primitive Neuroectodermal Tumor/Ewing's Sarcoma: A Critical Analysis and Review.
Asian journal of neurosurgeryPrimitive neuroectodermal tumor of the pericardium: a case report and literature review.
BMC cardiovascular disordersProstate Ewing Sarcoma/PNET: A case of long survival in a highly aggressive malignancy.
UrologyCongenital Cutaneous Peripheral Primitive Neuroectodermal Tumor (pPNET) of Scalp: Youngest Case So Far.
Journal of Indian Association of Pediatric SurgeonsRadiological and pathological diagnosis of an incidental Askin tumor.
Radiology case reportsPrimary Spinal Epidural Extraosseous Ewing's Sarcoma with Brachial Plexus Infiltration.
Asian journal of neurosurgeryPrimary Primitive Neuroectodermal Tumor of the Spine With t(11;22): Report of 3 Cases and Review of Literature.
Journal of pediatric hematology/oncologyPrimary pulmonary Ewing sarcoma/peripheral primitive neuroectodermal tumor.
Proceedings (Baylor University. Medical Center)Primary Intracranial Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor Mimicking Meningioma: A Case Report and Literature Review.
Frontiers in oncologyOutcome of multidisciplinary treatment of peripheral primitive neuroectodermal tumor.
Scientific reportsPrimary vulvar Ewing sarcoma/peripheral primitive neuroectodermal tumor with pelvic lymph nodes metastasis: A case report and review of literature.
The journal of obstetrics and gynaecology researchPrimary intracranial Ewing sarcoma/ peripheral primitive neuroectodermal tumor, an entity of unacquaintance: a series of 8 cases.
Child's nervous system : ChNS : official journal of the International Society for Pediatric NeurosurgeryIntracranial Ewing Sarcoma - A case report.
Surgical neurology internationalA case report of neonatal orbital peripheral primitive neuroectodermal tumor and literature review.
European journal of ophthalmologyPrimary Peripheral Primitive Neuroectodermal Tumor of the Prostate on 18F-DCFPyL PET/CT.
Clinical nuclear medicineEwing's sarcoma/peripheral primitive neuroectodermal tumor with extraskeletal myxoid chondrosarcoma-like areas: a case report.
International journal of clinical and experimental pathologyEwing's Sarcoma of the Sinonasal Tract: A Report of Two Challenging Cases.
Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of IndiaRetroperitoneal extraosseous peripheral primitive neuroectodermal tumor in a Formosan serow: case report and literature review.
Journal of veterinary diagnostic investigation : official publication of the American Association of Veterinary Laboratory Diagnosticians, IncPrimary Intracranial Dural-Based Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor with Extracranial Extension: An Uncommon Case.
Asian journal of neurosurgeryCongenital cutaneous peripheral primitive neuroectodermal tumor/Ewing sarcoma: A rare case in a male neonate.
Pediatric blood & cancerExtraskeletal Ewing's sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation.
Clinical and experimental gastroenterologyBone marrow examination in patients with Ewing sarcoma/peripheral primitive neuroectodermal tumor without metastasis based on 18F-fluorodeoxyglucose positron emission tomography/computed tomography.
Medical oncology (Northwood, London, England)Ewing's sarcoma of the sinonasal tract with orbital extension: a rare case report and literature review.
Journal of surgical case reportsPeripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases.
Iranian journal of pathologyPrimary Intra-abdominal Ewing's Sarcoma in Adults: A Multimodality Imaging Spectrum.
Current problems in diagnostic radiologyPeripheral primitive neuroectodermal tumor associated with paraneoplastic Cushing's syndrome: The rare case.
Annals of medicine and surgery (2012)Ultrasensitive quantification of tumor mRNAs in extracellular vesicles with an integrated microfluidic digital analysis chip.
Lab on a chipA Rare Case of Dumbbell-shaped Primary Intraspinal Peripheral Primitive Neuroectodermal Tumor Involving Thoracic Spinal Epidural Space.
Asian journal of neurosurgeryScrotal Peripheral Primitive Neuroectodermal Tumor.
Current urologyEwing's Sarcoma/Peripheral Primitive Neuroectodermal Tumors in Bronchus.
The American journal of the medical sciencesFrom Ataxia to Diagnosis of Askin Tumor - a Case Report.
Acta medica (Hradec Kralove)Intracranial Peripheral Primitive Neuroectodermal Tumor Arising from the Clivus with Intracranial Metastasis in an Elderly Woman: Case Report and Review of the Literature.
World neurosurgeryPrimary Ewing Family of Tumor Arising in the Ovary: A Case Report.
International journal of gynecological pathology : official journal of the International Society of Gynecological PathologistsPeripheral primitive neuroendocrine tumor of the chest wall-A case report with pathological correlation.
Radiology case reportsEwing Sarcoma/Peripheral Primitive Neuroectodermal Tumor in the Adrenal Gland of a Child.
Iranian journal of kidney diseasesPeripheral primitive neuroectodermal tumor of cauda equina: A report and review of literature.
Neurology IndiaPrimary Intracranial pPNET/Ewing Sarcoma: Diagnosis, Management, and Prognostic Factors Dilemma-A Systematic Review of the Literature.
World neurosurgeryExtraosseous Primary Intracranial Ewing Sarcoma/peripheral Primitive Neuroectodermal Tumor: Series of Seven Cases and Review of Literature.
Asian journal of neurosurgeryPrimary primitive neuroectodermal tumor of the kidney.
Indian journal of pathology & microbiologyEwing sarcoma of the adrenal gland: a case report and review of the literature.
Journal of medical case reportsSpinal Peripheral Primitive Neuroectodermal Tumors: A Radiological Analysis of Ten Cases.
Turkish neurosurgeryAdrenal mass of unusual etiology: Ewing sarcoma in a young man.
Radiology case reports[Paranasal peripheral primitive neuroectodermal tumor: a case report].
Zhonghua er bi yan hou tou jing wai ke za zhi = Chinese journal of otorhinolaryngology head and neck surgeryAntiangiogenic therapy for primitive neuroectodermal tumor with thalidomide: A case report and review of literature.
Medicine[The treatment and prognosis of peripheral primitive neuroectodermal tumor].
Zhonghua zhong liu za zhi [Chinese journal of oncology]Skull base bony lesions: Management nuances; a retrospective analysis from a Tertiary Care Centre.
Asian journal of neurosurgeryPrimary intracranial dural-based Ewing sarcoma/peripheral primitive neuroectodermal tumor mimicking a meningioma: A rare tumor with review of literature.
Asian journal of neurosurgerySystemic Therapy Outcomes in Adult Patients with Ewing Sarcoma Family of Tumors.
Case reports in oncologyPrimary primitive neuroectodermal tumor of the cervix: A report of two cases and review of the literature.
Molecular and clinical oncologyCytogenetically confirmed primary Ewing's sarcoma of the pancreas.
BMJ case reportsEwing's Sarcoma Family Tumors in the Jaws: Case Report, Immunohistochemical Analysis and Literature Review.
In vivo (Athens, Greece)Triple-phase 99mTc-3P-RGD2 imaging of peripheral primitive neuroectodermal tumor in the hip muscle group with bone metastasis.
Molecular and clinical oncologyIsolated cardiac peripheral primitive neuroectodermal tumor: A case report.
Cancer biology & therapyComputed Tomography and Magnetic Resonance Imaging Characteristics of Peripheral Primitive Neuroectodermal Tumor: A Retrospective Analysis of 16 Cases.
Journal of computer assisted tomographyHuge peripheral primitive neuroectodermal tumor of the small bowel mesentery at nonage: A case report and review of the literature.
World journal of clinical casesPeripheral primitive neuroectodermal tumors of the spine: a case report and review of the literature.
BMC research notesMeningeal Ewing Sarcoma/Peripheral PNET: Clinicopathological, Immunohistochemical and FISH study of four cases.
Neuropathology : official journal of the Japanese Society of NeuropathologyPrimary Brachial Plexus Tumors: Clinical Experiences of 143 Cases.
Clinical neurology and neurosurgeryPeripheral Primitive Neuroectodermal Tumor of Breast.
Journal of the College of Physicians and Surgeons--Pakistan : JCPSPSynthetic treatment of intracranial peripheral primitive neuroectodermal tumor with multiple metastasis: a case report.
OncoTargets and therapyCervicomedullary intramedullary peripheral primitive neuroectodermal tumor with intratumoral bleed: Report of one case and review of literature.
Journal of craniovertebral junction & spineA peripheral primitive neuroectodermal tumor in the larynx: A case report and literature review.
Oncology lettersPeripheral Primitive Neuroectodermal Tumor and Neurofibromatosis Type 1 in an Adolescent Male.
Pediatric blood & cancer[Peripheral Primitive Neuroectodermal Tumor of the Small Bowel Mesentery - Report of a Case].
Srpski arhiv za celokupno lekarstvoA unique cause of neck pain: peripheral primitive neuroectodermal tumor.
The spine journal : official journal of the North American Spine SocietyPeripheral Primitive Neuroectodermal Tumor (pPNET) of the Parotid: Report of a Rare Case.
Archives of Iranian medicineEfficacy of trabectedin in advanced soft tissue sarcoma: beyond lipo- and leiomyosarcoma.
Drug design, development and therapySinonasal small round blue cell tumors: An approach to diagnosis.
Seminars in diagnostic pathologyIncidences of Primary Soft Tissue Sarcoma Diagnosed on Extremities and Trunk Wall: A Population-Based Study in Taiwan.
MedicinePrimitive neuroectodermal tumor of the prostate: Case report from China.
Journal of cancer research and therapeuticsRenal primitive neuroectodermal tumor as a second malignancy after chemotherapy and radiation for Non-Hodgkin's Lymphoma--treatment-related or just poor old bad luck?: A case report.
Journal of cancer research and therapeuticsA peripheral primitive neuroectodermal tumor originating from the pancreas: a case report and review of the literature.
Surgical case reportsCyclin D1 and Ewing's sarcoma/PNET: A microarray analysis.
Acta histochemicaRadiological and clinical findings of osseous peripheral primitive neuroectodermal tumors.
Oncology lettersApplication of electron microscopic analysis and fluorescent in situ hybridization technique for the successful diagnosis of extraskeletal Ewing's sarcoma.
The Journal of dermatologyMandibular peripheral primitive neuroectodermal tumor: a rare case report with review of literature.
Journal of maxillofacial and oral surgeryPeripheral primitive neuroectodermal tumor of chest wall in young adult.
Radiologia brasileiraCyclin D1 is a useful marker for soft tissue Ewing's sarcoma/peripheral Primitive Neuroectodermal Tumor in children and adolescents: A comparative immunohistochemical study with rhabdomyosarcoma.
Acta histochemicaPrimary intracranial Ewing's sarcoma with unusual features.
International journal of clinical and experimental pathologyPeripheral primitive neuroectodermal tumor of seminal vesicles: is there a role for relatively aggressive treatment modalities?
Archivio italiano di urologia, andrologia : organo ufficiale [di] Societa italiana di ecografia urologica e nefrologicaPancreatic peripheral primitive neuroectodermal tumor diagnosed by endoscopic ultrasound.
EndoscopyPeripheral primitive neuroectodermal tumor: dynamic CT, MRI and clinicopathological characteristics--analysis of 36 cases and review of the literature.
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Neoadjuvant chemotherapy-enabled tumor conversion and surgical resection in pediatric primary pulmonary Ewing sarcoma: a case report.
- Percutaneous Ultrasound-Guided Intratumoral Injection of Lauromacrogol and Pingyangmycin in the Treatment of Advanced pPNET in Children.
- Multimodal Treatment of a Peripheral Primitive Neuroectodermal Tumor Originating From the Thoracic Cavity in a Dog.
- Primary ovarian peripheral primitive neuroectodermal tumor presented with breast metastasis; Case report.
- Challenges in Diagnosing Primary Intracranial Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report.
- Correction to "Multimodal Treatment of a Peripheral Primitive Neuroectodermal Tumor Originating From the Thoracic Cavity in a Dog".
- Ewing Sarcoma Treatment (PDQ®): Patient Version.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:370348(Orphanet)
- MONDO:0018271(MONDO)
- GARD:17601(GARD (NIH))
- Variantes catalogadas(ClinVar)
- Busca completa no PubMed(PubMed)
- Q56014124(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
