O tumor fibroso solitário (TFS) é um tipo raro de tumor, formado por células alongadas (chamadas células fusiformes), que pode aparecer em diversas partes do corpo. Ele pode ser benigno (não-canceroso) ou maligno (canceroso). Geralmente, surge com mais frequência na pleura (membrana que recobre o pulmão) e no peritônio (membrana que reveste o abdômen), e mais raramente em outras partes como cabeça e pescoço, fígado e músculos. O TFS pode não apresentar sintomas ou pode se manifestar como uma massa que cresce, causando efeitos de compressão nos órgãos vizinhos, dependendo do local onde está. Mais raramente, pode causar sintomas incomuns que afetam outras partes do corpo (chamados de manifestações paraneoplásicas), como problemas nas articulações e ossos (osteoartropatia) ou baixo açúcar no sangue (hipoglicemia).
Introdução
O que você precisa saber de cara
O tumor fibroso solitário (TFS) é um tipo raro de tumor, formado por células alongadas (chamadas células fusiformes), que pode aparecer em diversas partes do corpo. Ele pode ser benigno (não-canceroso) ou maligno (canceroso). Geralmente, surge com mais frequência na pleura (membrana que recobre o pulmão) e no peritônio (membrana que reveste o abdômen), e mais raramente em outras partes como cabeça e pescoço, fígado e músculos. O TFS pode não apresentar sintomas ou pode se manifestar como uma massa que cresce, causando efeitos de compressão nos órgãos vizinhos, dependendo do local onde está. Mais raramente, pode causar sintomas incomuns que afetam outras partes do corpo (chamados de manifestações paraneoplásicas), como problemas nas articulações e ossos (osteoartropatia) ou baixo açúcar no sangue (hipoglicemia).
Tem tratamento?
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 21 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 31 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Genes associados
2 genes identificados com associação a esta condição. Padrão de herança: Not applicable.
Acts as a transcriptional repressor for zinc finger transcription factors EGR1 and EGR2. Isoform 2 lacks repression ability (By similarity)
Nucleus
Carries out a dual function: signal transduction and activation of transcription. Involved in IL4/interleukin-4- and IL3/interleukin-3-mediated signaling
CytoplasmNucleus
Hyper-IgE syndrome 6, autosomal dominant, with recurrent infections
An immunologic disorder characterized by severe allergic disease with onset in infancy. Common features are treatment-resistant atopic dermatitis, food allergies, asthma, eosinophilic gastrointestinal disease, and severe episodes of anaphylaxis. Half of the patients present with recurrent skin, respiratory, and viral infections. Clinical laboratory testing is notable for eosinophilia and markedly elevated serum IgE levels.
Medicamentos e terapias
Mecanismo: DNA topoisomerase II alpha inhibitor
Mecanismo: DNA topoisomerase II alpha inhibitor
Mecanismo: Vascular endothelial growth factor receptor inhibitor
Mecanismo: Tubulin inhibitor
Mecanismo: Fibroblast growth factor receptor 3 inhibitor
Variantes genéticas (ClinVar)
26 variantes patogênicas registradas no ClinVar.
Vias biológicas (Reactome)
5 vias biológicas associadas aos genes desta condição.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Tumor fibroso solitário
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Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.
Pesquisa ativa
Ensaios clínicos abertos e novidades científicas recentes
Ensaios em destaque
🟢 Recrutando agora
3 pesquisas recrutando participantes. Converse com seu médico sobre a possibilidade de participar.
Outros ensaios clínicos
101 ensaios clínicos encontrados, 3 ativos.
Publicações mais relevantes
Mostrando amostra de 200 publicações de um total de 1.827
Effectiveness of classification and scoring systems in solitary fibrous tumor prognosis prediction.
Because thoracic solitary fibrous tumors (SFTs) are rare, there is limited information on their clinical features, treatment, and follow-up. The literature mainly comprises individual case reports. Our study aimed to analyse SFT data to identify prognosis-related factors and to compare the performance of two describing approaches and three risk stratification models. We conducted a retrospective review of medical data from 37 patients, including 32 patients with SFT aged 18 years and older who underwent surgical treatment and five patients diagnosed by biopsy at Kocaeli University Hospital between January 2004 and December 2024. Parameters affecting recurrence and survival were investigated, and the effectiveness of existing classification and scoring systems was compared. Factors potentially associated with recurrence included four or more mitoses (10 HPF) (p=0.023), necrosis (p=0.007), at least 10% Ki-67 positivity (p=0.012), malignancy (p=0.046), and tumor size (p=0.022). Relapses were observed only in the malignant group according to the England classification (p=0.046), only in stage-3 according to the de Perrot classification (p=0.161), only in those with scores of three or higher according to the Tapias classification (p=0.036), only in those with scores of two or higher according to the Diebold classification (p=0.021), and all in high-stage groups (p=0.001) according to the Demicco classification. All recurrences occurred at significant or high scores. The Tapias, Diebold, and Demicco scoring systems are highly effective in predicting recurrence and prognosis. However, the modified Demicco system is more advantageous and offers a higher level of assessment.
Beyond the Globe: Molecular Diagnostics of Optic Nerve, Orbital, and Adnexal Neoplasms.
Recent advances in molecular pathology have transformed the diagnostic landscape and management of human cancer. Increasingly, integration of genomic and epigenomic data with conventional histopathology has improved tumor classification, refined prognostic assessment, and revealed previously unsuspected therapeutic targets. High-throughput techniques such as next-generation sequencing, gene fusion panels, and methylation arrays have expanded applicability to formalin-fixed tissue and enabled simultaneous evaluation of multiple cancer-defining alterations/genetic drivers. In optic nerve gliomas, MAPK pathway activation through BRAF or FGFR1 alterations, or NF1 inactivation, is a basic biological feature with diagnostic implications, while MEK inhibitors may be of clinical benefit in selected patients. Optic nerve sheath/orbital meningiomas demonstrate divergent molecular landscapes depending on location, with NF2-driven and non-NF2-driven pathways informing recurrence risk and behavior. In the orbit, characteristic genetic drivers facilitate diagnosis of mesenchymal tumors such as solitary fibrous tumor (NAB2::STAT6) and alveolar rhabdomyosarcoma (PAX3/7::FOXO1), while molecular profiling assists in distinguishing challenging peripheral nerve and melanocytic lesions. Similarly, lacrimal gland neoplasms parallel salivary gland counterparts, with recurrent fusions such as PLAG1, HMGA2, and MYB::NFIB of great diagnostic utility. These advances underscore the growing role of molecular diagnostics in improving accuracy, guiding prognostication, and refining the classification of rare ocular tumors. As high-throughput techniques continue to mature, integration with evolving spatial and single-cell-based approaches promises to expand our understanding and further personalize diagnostic and therapeutic strategies.
Incidentally detected multifocal calcifying fibrous tumour of the pleura: a diagnostic enigma.
Calcifying fibrous tumour of the pleura (CFTP) is a rare, benign soft tissue neoplasm with uncertain aetiology. To our knowledge, only 36 cases (including this case) have been reported in English literature. A man in his early 30s presented with an incidental pleural lesion identified following investigation for a persistent cough. Imaging revealed left pleural thickening with calcification, raising concern for a possible malignant pleural process. CT-guided biopsy demonstrated fibrosis without malignancy, and a video-assisted thoracoscopic surgery excision was performed. Histopathology confirmed multifocal CFTP. This case highlights the diagnostic challenges posed by pleural-based calcified lesions and reinforces the importance of surgical excision for both diagnosis and cure. The rarity of CFTPs, their benign course and their potential to mimic malignancy are discussed alongside a review of the current literature.
Intracranial solitary fibrous tumor with myxoid features: An unusual presentation.
A case of orbital solitary fibrous tumor with fast-growing budding morphology.
Orbital solitary fibrous tumors (SFTs) are rare and are typically benign and slow‑growing. This report details a unique case of a rapidly progressing benign orbital SFT in a 75-year-old man with recurrent prostate cancer. Magnetic Resonance Imaging (MRI) initially revealed an extraconal mass, which, within five months, evolved significantly. Surgical excision revealed a primary encapsulated mass and a smaller, intimately attached, "budding" satellite nodule. Histopathology confirmed benign SFT characteristics with low mitotic activity and strong nuclear STAT6 and CD34 immunoreactivity. This case is notable for its rapid growth and presentation in an older patient with cancer, expanding the known morphological spectrum and growth kinetics of orbital SFTs. While the observation raises a hypothesis regarding potential systemic or hormonal influences, no receptor, molecular, or serum studies were performed to support a causal relationship. Overall, this case underscores the importance of thorough intraoperative exploration, continuous surveillance, and prompts further investigation into systemic or hormonal influences on SFT growth.
Publicações recentes
Primary thoracic synovial sarcoma in a 45-year-old male: A case report and literature review.
🥉 Relato de casoPerioperative Decision-Making for a Solitary Fibrous Tumor of the Pleura: Lessons from Two Cases and Current Evidence.
🥉 Relato de caso[Moderate to high-risk primary malignant solitary fibrous tumor of the kidney: a clinicopathological and molecular analysis of five cases].
🥉 Relato de casoNeurosarcoidosis mimicking multiple meningiomas: illustrative case.
🥉 Relato de casoLong-term control of grade 3 intracranial solitary fibrous tumor achieved with pazopanib and stereotactic radiotherapy: illustrative case.
🥉 Relato de caso📚 EuropePMC2.256 artigos no totalmostrando 198
A case of orbital solitary fibrous tumor with fast-growing budding morphology.
Orbit (Amsterdam, Netherlands)Intraosseous Solitary Fibrous Tumor of the Maxilla: A Report of an Unusual Case.
CureusIntraoperative vascular ligation uncovers the role of tumor vasculature in Doege-Potter syndrome: a case report.
Frontiers in oncologyA hepatic solitary fibrous tumor with giant cells and a review of the literature.
Discover oncologyPediatric intracranial high-grade solitary fibrous tumor/hemangiopericytoma with drop metastasis to cervicodorsal spine: a rare case report.
International journal of surgery case reportsCase report: diagnosis and surgical management of a rare malignant isolated fibrous tumor of the pelvis.
Journal of surgical case reportsEffectiveness of classification and scoring systems in solitary fibrous tumor prognosis prediction.
Pakistan journal of medical sciencesHaemangiopericytoma and solitary fibrous tumour of the parotid gland: a scoping review.
Acta otorhinolaryngologica Italica : organo ufficiale della Societa italiana di otorinolaringologia e chirurgia cervico-faccialeComplete Resection of a Giant Hypervascular Pelvic Floor Solitary Fibrous Tumor Using Intraoperative Balloon Occlusion and Staged Open Abdomen Management: A Case Report.
Surgical case reportsClinical Features of Solitary Fibrous Tumor: Insights From a Single Center Experience.
Journal of surgical oncologyIntracranial solitary fibrous tumor with myxoid features: An unusual presentation.
Journal of neuropathology and experimental neurologyIntracerebral Hemorrhage Secondary to Solitary Fibrous Tumor: A Case Report.
CureusBeyond the Globe: Molecular Diagnostics of Optic Nerve, Orbital, and Adnexal Neoplasms.
Translational vision science & technology[Perioperative Crew Resource Management: an Example of Interdisciplinary Collaboration].
Anasthesiologie, Intensivmedizin, Notfallmedizin, Schmerztherapie : AINSMyxoid Solitary Fibrous Tumor of the Vulva: A Diagnostic Pitfall.
International journal of gynecological pathology : official journal of the International Society of Gynecological PathologistsClinicopathological characteristics and outcomes of 42 cases of ocular adnexal sarcoma.
International ophthalmologyClinicopathological, Radiological, and Prognostic Profile of Solitary Fibrous Tumor of Central Nervous System: A Single Institutional Experience.
Indian journal of surgical oncologyHepatic solitary fibrous tumor.
Journal of gastrointestinal surgery : official journal of the Society for Surgery of the Alimentary TractSolitary fibrous tumor of the sublingual gland: a case report.
Frontiers in oral healthLower Lip Nodule in an Elderly Woman: Challenge.
The American Journal of dermatopathologyLower Lip Nodule in an Elderly Woman: Answer.
The American Journal of dermatopathologyPrimary radiotherapy for intraorbital solitary fibrous tumor: a case report with 5-year follow-up.
Orbit (Amsterdam, Netherlands)Solitary Fibrous Tumor With a 12-Year Recurrence Interval in a Female Patient: A Case Report.
CureusSolitary Fibrous Tumors of the Head and Neck: A Report of Two Cases and Review of the Literature.
CureusThe role of surgery plus radiation versus surgery alone in the management for complicated orbital solitary fibrous tumor: a new insight on a rare disease.
BMC cancerResolution of Refractory Nonislet Cell Tumor Hypoglycemia Following Resection of an Abdominal Solitary Fibrous Tumor.
AACE endocrinology and diabetesA Rare Case of a Solitary Fibrous Tumor of the Prostate: A Case Report.
CureusSolitary Fibrous Tumor of the Oropharyngeal Lateral Wall: A Case Report and Review of Diagnostic and Therapeutic Challenges.
CureusSubcutaneous Solitary Fibrous Tumor in the Chin of a Young Adult: A Diagnostic Challenge.
The American journal of case reportsSingle-Fraction Stereotactic Radiosurgery for Residual, Recurrent, or Metastatic Intracranial Solitary Fibrous Tumors: An IRRF Study Toward Management Guidance.
Neuro-oncologyFDG-PET/CT SUVmax Predicts Recurrence Risk of Resected Pleuropulmonary Solitary Fibrous Tumors.
JTO clinical and research reportsSilent but suspicious: the clinical significance of slowly expanding PET-negative lung nodules.
Journal of cardiothoracic surgerySolitary fibrous tumor of the chest wall with Doege-Potter syndrome: a case report.
Frontiers in oncologyDistant metastasis of intracranial solitary fibrous tumor preceding resection: illustrative case.
Journal of neurosurgery. Case lessonsProceedings of the 2026 North American Society of Head and Neck Pathology Companion Meeting, San Antonio, TX, March 22, 2026: It's a Trap!: Diagnostic Pitfalls in Sinonasal Pathology.
Head and neck pathologyValidation of a seven-gene predictive SIGNature for the efficacy of Immuno-Oncology PD-1 inhibitors in patients with Sarcoma (SIGNIOS).
Clinical cancer research : an official journal of the American Association for Cancer ResearchPathologic Assessment of Retroperitoneal Sarcomas: A Position Paper By the Transatlantic Australasian Retroperitoneal Sarcoma Working Group.
The American journal of surgical pathologySolitary fibrous tumor: an updated review.
Journal of pathology and translational medicineCD 34 negative orbital solitary fibrous tumor: report of a rare case with prognostic implications.
Orbit (Amsterdam, Netherlands)Incidentally detected multifocal calcifying fibrous tumour of the pleura: a diagnostic enigma.
BMJ case reportsRare malignant cervical solitary fibrous tumor.
International journal of gynecological cancer : official journal of the International Gynecological Cancer SocietyContrast-Enhanced Harmonic Endoscopic Ultrasonography for Diagnosing Gastric Subepithelial Tumors.
Diagnostics (Basel, Switzerland)Prognostic clinical and pathological factors in intrathoracic solitary fibrous tumors: A retrospective single-center study.
Turk gogus kalp damar cerrahisi dergisiSolitary Fibrous Tumor of Uterine Cervix: A Rare Entity Mimicking Clinically as Carcinoma Cervix.
International journal of applied & basic medical researchIntraocular Solitary Fibrous Tumor.
Ophthalmology. RetinaSolitary Fibrous Tumor With Doege-Potter Syndrome Successfully Treated With Preoperative Transcatheter Arterial Embolization and Complete Excision; A Case Report.
IJU case reportsFirst In Vivo Monitoring of Helium-Ion Radiation Therapy With Secondary Ions.
International journal of radiation oncology, biology, physicsPeriprosthetic Solitary Fibrous Tumor of the Proximal Femur: A Case Report.
JBJS case connectorLocalization of Persistent Air Leaks Using Technetium-99m Technegas SPECT/CT.
Clinical nuclear medicineRobotic subxiphoid surgical approach for mediastinal lesions: One-year experience.
World journal of clinical casesRefining Risk Stratification and Surveillance Strategies in Pleuropulmonary Solitary Fibrous Tumors-An International, Retrospective, Multicenter Analysis.
CancersMalignant metastatising solitary fibrous tumor of the ovary with additional dedifferentiation and osteoid deposition: an unusual presentation, with a brief description of a diagnostic alghoritm.
PathologicaSolitary Fibrous Tumor of the Nasal Vestibule: A Case Report.
Cureus11 C-Methionine PET for Detecting Solitary Fibrous Tumor Metastases: 2 Cases With Negative FDG-PET.
Clinical nuclear medicineAn Unusual Cause of Hypoglycemia: Doege-Potter Syndrome-A Case Report and Review of Literature.
Indian journal of surgical oncologyMalignant solitary fibrous tumor of the temporal bone with NAB2 ex6::STAT6 ex16 fusion: a case report with literature review.
World journal of surgical oncologyA Rare Metastatic Fibrous Tumor: Review of Literature With a Case Report.
JTO clinical and research reportsPrimary Pulmonary Osteosarcoma Presenting as a 1.7-cm Subpleural Nodule in a 61-Year-Old Man: A Case Report.
The American journal of case reportsThe first case of GOLGA5-RET fusion-positive malignant spindle cell sarcoma of the head and neck responsive to selpercatinib.
International cancer conference journalLarge Thoracic Solitary Fibrous Tumor: A Case Report.
Case reports in oncologyRadiation therapy alleviates Doege-Potter syndrome accompanied with severe aortic valve insufficiency: a case report and literature review.
Frontiers in oncologyBeyond COL1A1::PDGFB: Rare fusions and their clinical implications in dermatofibrosarcoma protuberans.
World journal of clinical cases[Renal solitary fibrous tumors: a clinicopathological analysis of five cases].
Zhonghua bing li xue za zhi = Chinese journal of pathologySolitary Fibrous Tumors of the Chest: Case Series from a Portuguese Center.
Acta medica portuguesaUncommon Spindle Cell Tumors of the Pleura.
Advances in anatomic pathologyA Prostatic Extra-Gastrointestinal Stromal Tumor Treated by Surgery: A Case Report with 7-Year Follow-Up and Review of Literature.
Archivos espanoles de urologiaIncidental Early Pancreatitis Detected on 18F-FDG and 68Ga-FAPI-46 PET/CT in a Patient With Metastatic Soft Tissue Sarcoma Undergoing 177Lu-FAPI-2286 Therapy.
Clinical nuclear medicineA Rare Case of a Huge Solitary Fibrous Tumor in the Kidney.
Medical archives (Sarajevo, Bosnia and Herzegovina)Cytologic and Histologic Findings of Extrapleural Solitary Fibrous Tumor: Report of Two Cases.
Diagnostic cytopathology90Y-FAPI-46 Theranostic for Solitary Fibrous Tumor Shows Promising Early Results.
Radiology. Imaging cancerInitial experience with ihtOBTURA®: A novel EVOH-based embolic agent in the preoperative embolization of hypervascular head, neck, and spinal tumors.
Interventional neuroradiology : journal of peritherapeutic neuroradiology, surgical procedures and related neurosciencesProstatic Solitary Fibrous Tumor With Pulmonary Metastases: A Case Report.
Cureus[Effectiveness evaluation of three-dimensional printed customized hemi-pelvic prosthesis for pelvic reconstruction after resection of massive pelvic tumor].
Zhongguo xiu fu chong jian wai ke za zhi = Zhongguo xiufu chongjian waike zazhi = Chinese journal of reparative and reconstructive surgeryThe Solitary Fibrous Tumor, the Chameleon of the Head and Neck Region-Clinical, Epidemiological, and Histopathological Aspects.
Diagnostics (Basel, Switzerland)Solitary Fibrous Tumour Presenting as Delayed Neck Swelling Following Carotid Endarterectomy.
CureusDoege-Potter syndrome in a patient with solitary fibrous tumor of the retroperitoneum: a case report and literature review.
Discover oncologySolitary Fibrous Tumor of the Mesentery of the Small Intestine: A Rare Case Report.
Journal of the anus, rectum and colonSolitary Fibrous Tumor of the Renal Hilar in a 52-Year-Old Woman: A Case Report.
Clinical case reportsNon-Islet Cell Tumor Hypoglycemia Masquerading as Diabetes Remission in a Patient With Type 2 Diabetes Mellitus.
JCEM case reportsIdentification of BET inhibitors (BETi) against solitary fibrous tumor (SFT) through high-throughput screening (HTS).
Neoplasia (New York, N.Y.)Spectrum and Clinical Impact of Secondary Genetic Alterations in Translocation-Associated Sarcomas.
JCO precision oncologyMalignant solitary fibrous tumor of the kidney with extracapsular extension beyond the renal capsule: An extremely rare Uro-oncological surgical case and diagnostic challenge.
Urology case reportsImaging Characteristics of Hemangiopericytoma: A Case Report.
CureusSolitary Fibrous Tumor of the Forehead.
Indian dermatology online journalA rare case: solitary fibrous tumor with widespread metastasis on [68Ga]Ga-DOTATATE PET/CT.
European journal of nuclear medicine and molecular imagingLaparoscopic resection of a giant pelvic solitary fibrous tumor: a case report.
Frontiers in oncologySolitary Fibrous Tumor of the Pleura Presenting as a Giant Thoracic Mass: A Case Report.
Clinical case reportsRecurrent dermatofibrosarcoma protuberans involving the lacrimal sac: A case report.
World journal of clinical casesInterdisciplinary management of a solitary fibrous tumor of the pleura complicated by Doege-Potter syndrome.
JTCVS techniquesSolitary fibrous tumor of the pancreas in a patient with tumor duplicity: a case report.
Ceskoslovenska patologieRobot-assisted laparoscopic prostate-sparing resection of an extremely rare periprostatic solitary fibrous tumor: a case report and literature review.
World journal of surgical oncologySolitary fibrous tumor of the prostate: a case report and the systematic review of 74 published cases.
Frontiers in oncologyRecurrence of Solitary Fibrous Tumour of the Pleura: A 20-Years Bi-centric Study with Risk Score Comparison.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgerySolitary fibrous tumor of the prostate: Case report and literature review.
Urology case reportsThoracic intradural extramedullary solitary fibrous tumor: A case report and review of the literature.
Surgical neurology international[Analysis of short-term efficacy and safety of transnasal endoscopic approach and the combined transconjunctival-endoscopic approach in resection of benign orbital apex lesions].
Zhonghua er bi yan hou tou jing wai ke za zhi = Chinese journal of otorhinolaryngology head and neck surgeryPediatric Spinal Solitary Fibrous Tumor: A Systematic Review of a Rare Condition.
Children (Basel, Switzerland)Recurrent Solitary Fibrous Tumors in the Orbit.
International ophthalmology clinicsThoracoscopic Resection of a Giant Solitary Fibrous Tumor in the Chest Cavity After Preoperative Arterial Embolization: A Case Report.
CureusPectoralis Major Myocutaneous Flap Reconstruction in Locally Advanced Head and Neck Malignant Solitary Fibrous Tumors: Functional and Oncologic Outcomes.
The Journal of craniofacial surgery3D-guided cadaveric fibula reconstruction for pediatric infratemporal solitary fibrous tumor.
Case reports in plastic surgery & hand surgerySpinal Extradural Solitary Fibrous Tumor Arising at the Level of T12 Vertebra: A Rare and Challenging Diagnosis.
CureusSolitary fibrous tumor of kidney and renal hilus: a multi-institutional clinicopathologic analysis of 43 cases.
Virchows Archiv : an international journal of pathologyImpact of adjuvant therapy on survival in treatment of CNS hemangiopericytomas.
Cancer treatment and research communicationsWHO Grade II or III Solitary Fibrous Tumors (Hemangiopericytomas) of the Spine: Two Case Reports with a Comprehensive Review of the Literature.
Journal of clinical medicineUnusual Case of Multiple and Delayed Recurrence of a Solitary Fibrous Tumor of the Pleura After Complete Resection.
Archivos de bronconeumologiaRadiation Therapy for Solitary Fibrous Tumor of the Orbit.
Ophthalmic plastic and reconstructive surgeryOperative Technique in a Resection of Solitary Fibrous Tumor within the Sigmoid Sinus: Technical Note and Case Presentation.
Journal of neurological surgery. Part A, Central European neurosurgerySolitary Fibrous Tumor of the Stomach: Diagnostic Pitfalls and Clinical Implications.
Surgical case reportsIntraventricular metastasis with malignant progression of an intraspinal solitary fibrous tumor: a case report and review of the literature.
Journal of medical case reportsLong-term follow-up outcomes in intracranial solitary fibrous tumor compared with meningioma: a propensity score matching study.
Journal of neurosurgeryMeningeal Solitary Fibrous Tumor: A Cytological Report With Emphasis on the Usefulness of Immunocytochemical Analysis for STAT6.
Diagnostic cytopathologyEndobronchial solitary fibrous tumor: A case report with comprehensive literature review.
International journal of surgery case reportsAlveolar solitary fibrous tumor: an uncommon morphological form.
Diagnostic pathologySolitary Fibrous Tumor in the Orbit: A Rare Occurrence.
CureusSolitary fibrous tumor of the spine.
Surgical neurology internationalSolitary fibrous tumor with bone metastasis: case report.
Journal of surgical case reportsHybrid Management of Giant Solitary Intracranial Fibrous Tumors: A Report of Two Cases.
CureusA Case of Solitary Fibrous Tumor of the Greater Omentum Incidentally Detected during Preoperative Evaluation for Thyroid Cancer.
Surgical case reportsInfrapubic Solitary Fibrous Tumor in a Young Male: What Is the Optimal Treatment?
UrologyThe association between WHO grading and the long-term outcomes and radiotherapy efficacy of intracranial solitary fibrous tumors.
Acta neuropathologica communicationsSolitary Fibrous Tumor of the Tarsus.
Ophthalmic plastic and reconstructive surgeryA Case of Solitary Fibrous Tumor in the Pelvis Completely Resected Using the Hugo RAS System.
Journal of the anus, rectum and colonThe Diagnosis and Treatment of Solitary Fibrous Tumor of the Parotid Gland.
Ear, nose, & throat journalRecurrent Pediatric Extrapleural Solitary Fibrous Tumor of the Jaw.
Head and neck pathologySolitary Fibrous Tumor of the Oral Cavity: A Rare Entity with Immunohistochemical Profiling.
Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of IndiaHighly Aggressive Intraparenchymal Solitary Fibrous Tumor of the Lung with Distant Metastasis: A Case Report and Review of CT and PET/CT Findings.
Reports (MDPI)Solitary fibrous tumor of the nasal septum: a case report and literature review.
Journal of surgical case reports90Y-FAPI-46 Theranostics Leads to Near-Complete Metabolic Response in 3 Patients with Solitary Fibrous Tumors.
Journal of nuclear medicine : official publication, Society of Nuclear MedicineParaneoplastic Hypoglycaemia in a Patient With Solitary Fibrous Tumor of Pleura.
Respirology case reportsSolitary Fibrous Tumor of the Right Elbow: A Case Report.
CureusManagement of choroidal solitary fibrous tumor with extraocular extension and subsequent postoperative rhegmatogenous retinal detachment.
American journal of ophthalmology case reportsA rare case of a giant pulmonary solitary fibrous tumor: Diagnostic and therapeutic challenges in the absence of malignancy.
Respiratory medicine case reportsThe Significance of Cytoplasmic STAT6 Positivity and High p53/p16 Expression as a Novel Predictor of Histological/Clinical Malignancy in NAB2::STAT6 Fusion-Positive Orbital Solitary Fibrous Tumors.
Pathology internationalClinicopathological and genetic analysis of orbital solitary fibrous tumors.
BMC ophthalmologyFourth Ventricular Solitary Fibrous Tumor: An Atypical Location for a Rare Tumor.
Neurology IndiaA rare case of Doege-Potter syndrome: Anesthesia considerations for the surgical removal of a benign solitary lung fibrous tumor.
Saudi journal of anaesthesiaProstate-sparing conservative management of a solitary fibrous tumor of the prostate: A case report.
Urology case reportsFluorescein-Guided Removal of Thoracic Spinal Solitary Fibrous Tumor: 2-Dimensional Operative Video.
Operative neurosurgery (Hagerstown, Md.)Paraganglioma of the spermatic cord: A rare tumor with unique imaging findings and diagnostic challenges.
GHM open18F-FDG PET/CT SUVmax in pleuropulmonary solitary fibrous tumors: can it be incorporated into risk classification systems for predicting recurrence?
BMC pulmonary medicineHybrid video-assisted thoracoscopic resection of a massive mediastinal solitary fibrous tumor: overcoming challenges: a case report.
Journal of medical case reportsA systematic review and meta-analysis on the efficacy of postoperative radiotherapy after gross total resection of intracranial solitary fibrous tumors.
Scientific reportsA clinical investigation of extracranial metastases in 17 cases of intracranial solitary fibrous tumors.
World journal of surgical oncologyA Rare Case of Cervical Solitary Fibrous Tumor in a Pediatric Patient: Case Report and Literature Review.
NeuroSciCase Report: Doege-Potter syndrome: a giant solitary fibrous pleural tumor causing severe hypoglycemia.
Frontiers in oncology[Solitary fibrous tumor of the kidney].
Arkhiv patologii[Solitary fibrous tumor of common bile duct: case report and literature review].
Arkhiv patologiiIdentification of intracranial solitary fibrous tumor and atypical meningioma by multi-parameter MRI-based radiomics model.
Discover oncologyA schwannoma look-alike: solitary fibrous tumor of the cauda equina. Illustrative case.
Journal of neurosurgery. Case lessonsExploring intraoperative hemorrhage and early recurrence in pelvic malignant solitary fibrotic tumors: a case report and literature review.
Frontiers in oncologySolitary fibrous tumor of the pleura: biphasic contrast-enhanced CT findings with emphasis on differential diagnosis.
Frontiers in medicineMassive Solitary Fibrous Tumor of the Hypopharynx.
CureusA Rare Solitary Fibrous Tumor Localized in the Upper Lip: A Case Report.
CureusDirect puncture embolization of intracranial solitary fibrous tumor with SQUID.
NeurocirugiaSolitary Fibrous Tumor of the Seminal Vesicle With Entrapped Benign Glands Mimicking a Mixed Epithelial and Stromal Tumor: A Case Report With Literature Review.
International journal of surgical pathologyNeuroendoscopic Anterior Prelacrimal Recess Approach for Resection of Tumors in the Infratemporal Fossa.
The Journal of craniofacial surgeryMetastatic Breast Cancer to a Dedifferentiated Solitary Fibrous Tumor Arising from a PTEN Hamartoma of Soft Tissue.
International journal of surgical pathologySolitary fibrous tumors from A to Z: a pictorial review with radiologic-pathologic correlation.
Insights into imagingCase Report: Retroperitoneal dedifferentiated solitary fibrous tumor with unexpected Pax-2 expression, mimicking high grade clear cell renal cell carcinoma.
Frontiers in oncologyDedifferentiated Solitary Fibrous Tumor: A Clinicopathologic, Immunohistochemical, and Molecular Characterization of 25 Cases.
The American journal of surgical pathologySolitary fibrous tumors of the infratemporal fossa: case series.
Journal of surgical case reportsDifferential diagnosis of intracranial solitary fibrous tumor and high-grade meningioma based on CT and MRI features.
The neuroradiology journalSolitary fibrous tumor in the pterygopalatine fossa: a rare case report and literature review.
European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck SurgeryA Case of Intracranial Solitary Fibrous Tumor Followed by Distant Metastasis without Local Recurrence.
NMC case report journalConjunctival Solitary Fibrous Tumor Masquerading as Conjunctival Hemangioma: A Case Report.
Journal of pediatric ophthalmology and strabismusMeningeal malignant solitary fibrous tumor with multiple recurrence, extracranial extension, cervical lymph node metastases: case report and review of the literature.
Discover oncologyMalignant solitary fibrous tumor of the seminal vesicle: a case report and review of the literature.
BMC urologyMalignant solitary fibrous tumor in the anterior abdominal wall: a rare case report with diagnostic and therapeutic insights.
Journal of surgical case reportsAdverse Outcome of a Solitary Fibrous Tumor Originating in the Bladder.
IJU case reportsApplication of 18F-FDGPET/CT in primary isolated pulmonary solitary fibrous tumor.
Frontiers in medicineA Rare Case of Myxoid Solitary Fibrous Tumor of the Upper Lip: The Key Role of STAT6 in Diagnosis.
CureusLow-grade intracranial solitary fibrous tumor with early metastasis to lumbar spine and recurrence twice: case report.
Discover oncology[Doege-Potter syndrome and intra-abdominal giant solitary fibrous tumor: Case report].
Revista medica del Instituto Mexicano del Seguro SocialLaparoscopic Minimally Invasive Approach for Pelvic Solitary Fibrous Tumor.
Annals of surgical oncologyRare Benign Liver Tumors: Current Insights and Imaging Challenges.
Seminars in ultrasound, CT, and MRSpindle lesions in the thyroid: a cytological and histological review.
Virchows Archiv : an international journal of pathologySolitary fibrous tumor-meningioma collision tumor with 18 years of follow-up.
Journal of neuropathology and experimental neurologyA Woman With Persistent Abdominal Pain in the Setting of a Solitary Fibrous Adrenal Tumor.
AACE clinical case reportsMachine Learning Analysis of Single-Voxel Proton MR Spectroscopy for Differentiating Solitary Fibrous Tumors and Meningiomas.
NMR in biomedicineSeizures caused by a solitary fibrous tumour of the pleura: an unusual presentation of Doege-Potter syndrome.
BMJ case reports[Hypoglycemia in a patient with pleural solitary fibrous tumor and response to pasireotide].
Revista de la Facultad de Ciencias Medicas (Cordoba, Argentina)Unveiling the Enigma: Gigantic primary de novo poorly-differentiated ductal adenocarcinoma of the lacrimal gland with aggressive features. A case report and literature review.
Archivos de la Sociedad Espanola de OftalmologiaIntermediate metastatic risk lipomatous solitary fibrous tumor of the thigh (previously known as hemangiopericytoma): A rare case report with a literature review.
MedicineApparent Diffusion Coefficient (ADC) and Magnetic Resonance Imaging (MRI) Nomogram for Differentiating a Solitary Fibrous Tumor (World Health Organization Grade II) From an Angiomatous Meningioma.
CureusQuantification of the immunohistochemical staining of fibroblast activation protein in intrathoracic solitary fibrous tumors using QuPath.
Surgery todayA novel rotation and scale-invariant deep learning framework leveraging conical transformers for precise differentiation between meningioma and solitary fibrous tumor.
Journal of pathology informaticsEndoscopic Transnasal Transclival Removal of a Giant Hemangiopericytoma Involving the Clivus and C1-C2 Vertebrae: A Clinical Case and Literature Review.
CureusIncidental High-Grade Sellar Solitary Fibrous Tumor Mimicking Non-Functioning Pituitary Adenoma: A Case Report and Literature Review.
The American journal of case reportsVulvar Cellular Angiofibroma With Cytologic Atypia and Sarcomatous Transformation: A Clinicopathologic Analysis.
International journal of gynecological pathology : official journal of the International Society of Gynecological PathologistsSolitary Fibrous Tumor of the Pleura: A Clinical Case of a Giant Malignant Tumor With Post-surgical Recurrence.
CureusComparison of [68Ga]Ga-Fibroblast Activation Protein Inhibitor-04 and [18F]FDG PET Imaging for Solitary Fibrous Tumor and Preliminary Application of FAP-Targeted Radiopharmaceutical Therapy.
Journal of nuclear medicine : official publication, Society of Nuclear MedicineSolitary fibrous tumor of temporal and infratemporal region: A case report and review of rare entity.
Journal of oral biology and craniofacial researchA case of solitary fibrous tumor of the breast.
Medical ultrasonographySolitary fibrous tumors: radiologic features with clinical and histopathologic correlation.
Frontiers in oncologyCase report: A study on disease diagnosis and treatment outcome of a case of bilateral malignant solitary fibrous tumor of the kidneys.
Frontiers in oncologySolitary fibrous tumor in the thyroid gland as an incidental finding.
Endocrinologia, diabetes y nutricionHypo-Fractionated versus Standard Fractionation Radiotherapy in Frail and Elderly Patients with Central Nervous System Solitary Fibrous Tumors.
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Effectiveness of classification and scoring systems in solitary fibrous tumor prognosis prediction.
- Beyond the Globe: Molecular Diagnostics of Optic Nerve, Orbital, and Adnexal Neoplasms.
- Incidentally detected multifocal calcifying fibrous tumour of the pleura: a diagnostic enigma.
- Intracranial solitary fibrous tumor with myxoid features: An unusual presentation.
- A case of orbital solitary fibrous tumor with fast-growing budding morphology.
- Primary thoracic synovial sarcoma in a 45-year-old male: A case report and literature review.
- Perioperative Decision-Making for a Solitary Fibrous Tumor of the Pleura: Lessons from Two Cases and Current Evidence.
- [Moderate to high-risk primary malignant solitary fibrous tumor of the kidney: a clinicopathological and molecular analysis of five cases].
- Neurosarcoidosis mimicking multiple meningiomas: illustrative case.
- Long-term control of grade 3 intracranial solitary fibrous tumor achieved with pazopanib and stereotactic radiotherapy: illustrative case.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:2126(Orphanet)
- MONDO:0016238(MONDO)
- GARD:15014(GARD (NIH))
- Variantes catalogadas(ClinVar)
- Busca completa no PubMed(PubMed)
- Artigo Wikipedia(Wikipedia)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
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