Evaluating pozelimab in the treatment of CHAPLE disease.

An Unusual Case with Abdominal Distension and Peripheral Edema.

Emerging Concepts in the Understanding and Treatment of Canine Protein-Losing Enteropathy.

Sustained remission of post-Fontan protein-losing enteropathy achieved by combination therapy with high-dose spironolactone and the somatostatin analogue octreotide: a case report.

Pancreatic lymphangioma and concurrent intestinal lymphangiectasia in a dog.

Primary intestinal lymphangiectasia presenting with intussusception in a child.

Intestinal Lymphangiectasia as a Rare Myeloma-Defining Event.

Insights into KIF11 pathogenesis in microcephaly-lymphedema-chorioretinopathy syndrome from a lymphatic perspective.

Uncommon association of familial short stature with primary intestinal lymphangiectasia.

What causes lymphopenia in primary lymphatic anomalies? Implications for understanding lymphocyte homeostasis.

Clinical presentation, treatment, and outcome of children with primary intestinal lymphangiectasia: A national retrospective study.

Camostat mesylate restores intestinal barrier integrity and attenuated protein loss in experimental protein-losing enteropathy.

Primary intestinal lymphangiectasia in a 5-month-old boy.

Evaluation of Immune System Components in Dogs With Protein-Losing Enteropathy Compared to Healthy Controls.

Clinical characterization of primary intestinal lymphangiectasia in infants and young children: a single-center retrospective analysis in China.

An Unusual Case of Leg Hemihypertrophy, Chronic Leg Lymphedema, and New-Onset Ascites With Pleural Effusion.

Intestinal Lymphangiectasia: A Rare Etiology of Gastrointestinal Bleeding.

An unusual etiology of diarrhea: primary intestinal lymphangiectasia.

Primary intestinal lymphangiectasia: French National Diagnosis and Care Protocol (PNDS; Protocole National de Diagnostic et de Soins).

Elusive Edematous Primary Intestinal Lymphangiectasia in an Adult Patient Presenting With New Onset of Protein-Losing Enteropathy.

Protein-losing enteropathy and multiple vasculature dysplasia in LZTR1-related Noonan syndrome: A case report and review of literature.

Secondary Hyperparathyroidism in Primary Intestinal Lymphangiectasia: A Report of Four Cases.

A Rare Cause of Abdominal Distension in Infancy.

Recurrent pericardial effusion due to Hennekam lymphangiectasia-lymphedema syndrome: a case report and literature review.

Complement dysregulation at lymphatics.

Intestinal lymphangiectasia in a dog: Clinical, ultrasonographic, endoscopic, and strain elastographic aspects.

Duodenal-Acquired Intestinal Lymphangiectasia After Lymph Node Excision and Inferior Vena Cava Injury in an 18-Year-Old Woman.

Scintigraphic Improvement of Primary Intestinal Lymphangiectasia in a Patient Treated With Alpelisib for a PIK3CA-Related Overgrowth Spectrum.

Elderly Onset Primary Intestinal Lymphangiectasia-A Rare Case.

Primary intestinal lymphangiectasia.

Lymphangiogram in primary intestinal lymphangiectasia.

Case 332: Tyrosine Kinase Inhibitor-induced Intestinal Lymphangiectasia.

An evaluation of pozelimab for the treatment of CHAPLE disease.

Importance of scattered white spots detected in the duodenum and their relationship with zonulin.

[Clinical features of 50 patients with primary intestinal lymphangiectasia].

Constrictive Pericarditis and Protein-Losing Enteropathies: Exploring the Heart-Gut Axis.

Endoscopic Diagnosis of Primary Intestinal Lymphangiectasia in an Adult With Refractory Protein-Losing Enteropathy: A Case Report.

MR Lymphangiography: Congenital Lymphatic Flow Disorders.

Primary intestinal lymphangiectasia - A rare cause of growth delay.

Pharmacotherapy for CD55 deficiency with CHAPLE disease: how close are we to a cure?

First case report of intestinal lymphangiectasia with refractory bleeding from the duodenum, successfully treated by intra-abdominal lymphaticovenous anastomosis with venous ligation.

Intestinal lymphangiectasia: Understanding the bigger picture.

In-hospital mortality in dogs with protein-losing enteropathy and associated risk factors.

Primary intestinal lymphangiectasia: A case report.

Waldmann's disease: Primary intestinal lymphangiectasia diagnosed by 99mTc-labeled albumin macroaggregate scintigraphy-A case report in an adult patient.

Hypocalcaemic tetany linked to vitamin D deficiency and hypomagnesemia in primary intestinal lymphangiectasia: a literature review.

A Preliminary Study Assessing a Transfer Learning Approach to Intestinal Image Analysis to Help Determine Treatment Response in Canine Protein-Losing Enteropathy.

Experience of primary intestinal lymphangiectasia in adults: Twelve case series from a tertiary referral hospital.

Secondary Intestinal Lymphangiectasia.

Mulibrey nanism and immunological complications: a comprehensive case report and literature review.

Yellow Nail Syndrome: Analysis of 23 Consecutive Patients and Effect of Combined Fluconazole-Vitamin-E Treatment.

Recurrent cellulitis and bacteremia in a patient with Noonan syndrome: A case report.

Use of octreotide for the treatment of protein-losing enteropathy in dogs: Retrospective study of 18 cases.

Newfound features associated with Hennekam Syndrome (Intestinal Lymphangiectasia-Lymphedema-Intellectual-Disability Syndrome) complicated with comorbid Waldmann's Disease resulting in Celiac Disease.

Profound and selective lymphopaenia in primary lymphatic anomaly patients demonstrates the significance of lymphatic-lymphocyte interactions.

Prevalence and risk factors of lymphatic dysfunction in cirrhosis patients with refractory ascites: An often unconsidered mechanism.

Primary Intestinal Lymphangiectasia Successfully Controlled with a Denver Peritoneovenous Shunt for Refractory Ascites.

A late diagnosis of primary intestinal lymphangiectasia in a Syrian girl.

Small intestinal mucosal abnormalities using video capsule endoscopy in intestinal lymphangiectasia.

Solitary Intestinal Lymphangiectasia Causing Transient Intussusception.

Misty mesentery, ascites, and bowel wall thickening in a child: Diagnostic clue for intestinal lymphangiectasia.

Cryptococcal meningitis and cerebral vasculitis in a patient with primary intestinal lymphangiectasia: a case report.

Milky Way: Management of Primary Intestinal Lymphangiectasia.

Small Bowel Lymphangiectasia Leading to Massive Gastrointestinal Bleeding: A Case Report.

An undernutrition screening score for dogs with protein-losing enteropathy: A prospective multicenter study.

Polypoid Lymphangiectasia in the Sigmoid Colon: A Case Report of a Rare Entity.

[Genetics, diagnostics and clinical presentation of primary lymphoedema].

Colonic Lymphangiomatosis.

In-silico assessment of high-risk non-synonymous SNPs in ADAMTS3 gene associated with Hennekam syndrome and their impact on protein stability and function.

Trichobezoar: A Rare Cause of Protein-losing Enteropathy.

Choroidal effusion and serous retinal detachment in protein-losing enteropathy from intestinal lymphangiectasia.

Possible biallelic inheritance in TIE1 in a family with congenital lymphedema, intestinal lymphangiectasia and cutis aplasia.

Adult-Onset Primary Intestinal Lymphangiectasia With Liver Enzymes Elevation.

Evaluation of Clinical Findings in Children with Chylothorax: A Descriptive Study.

Analysis of fecal microbial profiles in dogs with intestinal lymphangiectasia.

A case of systemic lupus erythematosus presenting with intestinal lymphangiectasia-associated protein-losing enteropathy accompanying hyperinflammation.

Correlation between capsule endoscopy classification and CT lymphangiography of primary intestinal lymphangiectasia.

Pathophysiology, Diagnosis, and Management of Canine Intestinal Lymphangiectasia: A Comparative Review.

Application of capsule endoscopy in patients with chronic and recurrent abdominal pain: Abbreviated running title: capsule endoscopy in abdominal pain.

Clinical diversity and molecular mechanism of VPS35L-associated Ritscher-Schinzel syndrome.

Severe vaccine-acquired rotavirus infection in an infant with primary intestinal lymphangiectasia.

Endoscopic classification and pathological features of primary intestinal lymphangiectasia.

Primary intestinal lymphangiectasia presenting as limb convulsions: A case report.

Diagnostic dilemma in diagnosing rare cause of protein losing enteropathy: Waldmann's disease.

Protein-losing Enteropathy as a Complication and/or Differential Diagnosis of Common Variable Immunodeficiency.

Case Report: Protein-Losing Enteropathy in Association With Tuberculosis-Related Constrictive Pericarditis.

Tyrosine Kinase Inhibitor-related Intestinal Lymphangiectasia.

Hypomagnesemia in intestinal lymphangiectasia: a case report and review of the literature.

Evaluation of the degree and distribution of lymphangiectasia in full-thickness canine small intestinal specimens diagnosed with lymphoplasmacytic enteritis and granulomatous lymphangitis.

Primary intestinal lymphangiectasia: a rare disease as a cause of protein-losing enteropathy.

A rare case of intestinal lymphangiectasia induced by pazopanib.

Redefining WILD syndrome: a primary lymphatic dysplasia with congenital multisegmental lymphoedema, cutaneous lymphovascular malformation, CD4 lymphopaenia and warts.

A case of primary intestinal lymphangiectasia with non-Hodgkin lymphoma.

Histopathology of intestinal villi in neonatal and paediatric age: main features with clinical correlation - Part I.

Association between intestinal lymphangiectasia and expression of inducible nitric oxide synthase in dogs with lymphoplasmacytic enteritis.

Protein-losing enteropathy caused by disseminated Mycobacterium avium complex infection in a patient receiving antiretroviral therapy: an autopsy case report.

Clinicopathological and Fecal Proteome Evaluations in 16 Dogs Presenting Chronic Diarrhea Associated with Lymphangiectasia.

Primary Intestinal Lymphangiectasia in a Middle-Aged Female.

Primary intestinal lymphangiectasia in children: Twelve years of experience in the diagnosis and management.

The Update of Treatment for Primary Intestinal Lymphangiectasia.

Drugs in Focus: Octreotide Use in Children With Gastrointestinal Disorders.

Dynamic Contrast Magnetic Resonance Lymphangiography Localizes Lymphatic Leak to the Duodenum in Protein-Losing Enteropathy.

Complicated primary intestinal lymphangiectasia (Waldmann's disease) in a child successfully treated with octreotide: A case report from a low-resource setting.

An unusual cause of heparin resistance - A case report.

Intestinal lymphangiectasia in an adult: case report.

Home parenteral nutrition a life-saving therapy in a primary intestinal lymphangiectasia patient affecting the entire GI tract - 3 year follow-up case report.

Primary intestinal lymphangiectasia presenting as limb hemihyperplasia: a case report and literature review.

Therapeutic Lymphatic Embolization in Pediatric Primary Intestinal Lymphangiectasia.

Refractory primary intestinal lymphangiectasia effectively managed with subcutaneous octreotide.

Lymphatic dysfunction in advanced cirrhosis: Contextual perspective and clinical implications.

[Intestinal lymphangiectasia in a patient with Sanfilippo B syndrome].

The diagnostic value of capsule endoscopy in children with intestinal lymphangiectasia.

Long-term endoscopic findings in pediatric primary intestinal lymphangiectasia.

Intestinal Lymphangiectasia Associated With Refractory Ascites in a Cirrhosis Patient.

Primary intestinal lymphangiectasia in an adult patient: A case report and review of literature.

Individual approach for treatment of primary intestinal lymphangiectasia in children: single-center experience and review of the literature.

A case of "misplaced" Tritrichomonas foetus infection in a dog in Northern Italy.

Enhanced Collagen Deposition in the Duodenum of Patients with Hyaline Fibromatosis Syndrome and Protein Losing Enteropathy.

Dietary and Nutritional Approaches to the Management of Chronic Enteropathy in Dogs and Cats.

Primary Intestinal Lymphangiectasia: Diagnostic Accuracy of 99mTc-Labeled Human Serum Albumin Nanocolloid SPECT/CT Before Biopsy.

Overlap of lymphatic dysplasia in Fontan-associated protein-losing enteropathy and Mucosa-Associated Lymphoid Tissue (MALT lymphoma): implications for management of protein-losing enteropathy.

Primary intestinal lymphangiectasia diagnosed by video capsule endoscopy in a patient with immunodeficiency presenting with Morganella morganii bacteraemia.

A case of Heck's disease with primary intestinal lymphangiectasia treated with imiquimod.

Severe chronic bowel obstruction associated with brown bowel syndrome.

Intestinal lymphangiectasia in a 3-month-old girl: A case report of Hennekam syndrome caused by CCBE1 mutation.

Tuberous sclerosis complex presenting as primary intestinal lymphangiectasia: A case report.

Magnetic Resonance Lymphangiography.

Primary intestinal lymphangiectasia in children: A review.

Gastrointestinal Cryptococcosis Associated with Intestinal Lymphangiectasia.

Chronic diarrhea with white colon: primary intestinal lymphangiectasia.

Updates on bone health in children with gastrointestinal diseases.

First Report of Treatment with Pancreas-Sparing Duodenectomy in a Child with Primary Intestinal Lymphangiectasia.

A girl with protein-losing enteropathy during a ketogenic diet: a case report.

Clinical characteristics of dogs with food-responsive protein-losing enteropathy.

Vaginal discharge caused by lymphatic malformation identified by lymphoscintigraphy combined with T2-weighted magnetic resonance imaging.

Carbohydrate Intolerance and Disaccharidase Measurement - a Mini-Review.

Primary Intestinal Lymphangiectasia Causing Intussusception and Small Bowel Obstruction.

Obscure GI bleeding in a young man.

Abdominal Pain, Fevers, and Intestinal Lymphangiectasia.

Biallelic mutation of FBXL7 suggests a novel form of Hennekam syndrome.

Primary intestinal lymphangiectasia in a 23-month- old girl.

Hennekam syndrome: an uncommon cause of chylous ascites and intestinal lymphangiectasia in the tropics.

Protein-losing enteropathy and primary intestinal lymphangiectasia.

Intestinal lymphangiectasia-A novel finding in Van Maldergem syndrome challenging the role of lymphedema for the distinction from Hennekam syndrome.

[Primary intestinal lymphangiectasia: first case report in Peru].

Ayurveda Herbal Medicine-induced Liver Cirrhosis.

Clinical Profile, Response to Therapy, and Outcome of Children with Primary Intestinal Lymphangiectasia.

Phenotype and Genotype of a Cohort of Chinese Children with Early-Onset Protein-Losing Enteropathy.

Pediatric localized intestinal lymphangiectasia treated with resection.

Comparative pathophysiology and management of protein-losing enteropathy.

Primary lymphangiectasia of the gastrointestinal tract.

CHAPLE syndrome uncovers the primary role of complement in a familial form of Waldmann's disease.

[Primary intestinal lymphangiectasia: Could propranolol be an effective alternative treatment?].

Novel Magnified Single-Balloon Enteroscopy Enables Observation of Jejunal White Spots Associated with Lymphangiectasia.

Milky Mesentery: Acute Abdomen with Chylous Ascites.

Eculizumab Is Safe and Effective as a Long-term Treatment for Protein-losing Enteropathy Due to CD55 Deficiency.

Primary Intestinal Lymphangiectasia (Waldmann's Disease).

Primary intestinal lymphangiectasia and a review of the current literature.

Intestinal lymphangiectasia: a rare cause of intussusception in an adolescent.

CT Lymphangiography (CTL) in Primary Intestinal Lymphangiectasia (PIL): A Comparative Study with Intraoperative Enteroscopy (IOE).

The application value of capsule endoscopy in diagnosing small intestinal carcinoma.

Case report of primary intestinal lymphangiectasia diagnosed in an octogenarian by ileal intubation and by push enteroscopy after missed diagnosis by standard colonoscopy and EGD.

Nutritional therapy and effect assessment of infants with primary intestinal lymphangiectasia: Case reports.

[Clinical analysis of intestinal lymphangiectasia in 47 children].

[Primary intestinal lymphangiectasia associated with follicular lymphoma: one case report].

Primary Intestinal Lymphangiectasia (Waldmann's Disease) Presenting with Chylous Effusions in a 15-Year-Old.

[Diagnostic and therapeutic approach to chronic inflammatory enteropathies in dogs].

[Primary intestinal lymphangiectasia (Waldmann's disease)].

Exacerbation of primary intestinal lymphangiectasia during late pregnancy and recovery after delivery: A case report and literature review.

Deterioration of duodenal lymphangiectasia after radiotherapy for gastric MALT lymphoma.

Primary intestinal lymphangiectasia in an elderly female patient: A case report on a rare cause of secondary immunodeficiency.

Cutaneous lymphangiectasia in a patient with primary intestinal lymphangiectasia.

Causes Of Chronic Non-Infectious Diarrhoea In Infants Less Than 6 Months Of Age: Rarely Recognized Entities.

In vivo characterization of abnormalities in small-bowel diseases using probe-based confocal laser endomicroscopy.

CD55 Deficiency, Early-Onset Protein-Losing Enteropathy, and Thrombosis.

Primary Intestinal Lymphangiectasia as a First Manifestation of Tuberous Sclerosis Complex.

Waldmann's Disease (Primary Intestinal Lymphangiectasia) with Atrial Septal Defect.

Abdominal Lymphangiomatosis With Intestinal Lymphangiectasia Diagnosed by Magnetic Resonance Lymphangiography: A Case Report.

A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation.

Protein-losing Enteropathy Caused by Intestinal or Colonic Lymphangiectasia Complicated by Sporadic Lymphangioleiomyomatosis: A Report of Two Cases.

Waldmann's disease: a rare cause of protein losing enteropathy in an adult patient.

Lymphatic deletion of calcitonin receptor-like receptor exacerbates intestinal inflammation.

Primary intestinal lymphangiectasia: Multiple detector computed tomography findings after direct lymphangiography.

Eculizumab in secondary atypical haemolytic uraemic syndrome.

Video Capsule Endoscopy to Diagnose Primary Intestinal Lymphangiectasia in a 14-Month-Old Child.

TNFΔARE Mice Display Abnormal Lymphatics and Develop Tertiary Lymphoid Organs in the Mesentery.

Deep Vein Thrombosis as Initial Manifestation of Whipple Disease.

[Malabsorption is a leading clinical sign of small bowel disease].

Intestinal Lymphangiectasia: Insights on Management and Literature Review.

Protein-losing enteropathy with intestinal lymphangiectasia in skeletal dysplasia with Lys650Met mutation.

Successful therapy for protein-losing enteropathy caused by chronic neuronopathic Gaucher disease.

Primary Intestinal Lymphangiectasia Manifested as Unusual Edemas and Effusions: A Case Report.

Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.

Everolimus for Primary Intestinal Lymphangiectasia With Protein-Losing Enteropathy.

Disorders associated with malabsorption of iron: A critical review.

Intestinal lymphangiectasia in children. A favorable response to dietary modifications.

Dietary or enteral medium-chain triglyceride usage in a Chinese general hospital.

Severe Refractory Anemia in Primary Intestinal Lymphangiectasia. A Case Report.

The lymphatic phenotype in Noonan and Cardiofaciocutaneous syndrome.

Primary intestinal lymphangiectasia with generalized warts.