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Encefalite do tronco cerebral Bickerstaff
ORPHA:79138CID-10 · G61.0CID-11 · 8C01.0DOENÇA RARA

A Encefalite de Tronco Cerebral de Bickerstaff (BBE) é uma doença neurológica rara que surge após uma infecção. Ela se caracteriza pela combinação de dificuldade para mover os olhos, falta de coordenação dos movimentos, ausência de reflexos nas pernas, um reflexo anormal na planta do pé (onde o dedão se estica para cima ao invés de se curvar para baixo) e alterações na consciência (como sonolência, torpor profundo ou coma).

Mantido por Agente Raras·Colaborar como especialista →

Introdução

O que você precisa saber de cara

📋

A Encefalite de Tronco Cerebral de Bickerstaff (BBE) é uma doença neurológica rara que surge após uma infecção. Ela se caracteriza pela combinação de dificuldade para mover os olhos, falta de coordenação dos movimentos, ausência de reflexos nas pernas, um reflexo anormal na planta do pé (onde o dedão se estica para cima ao invés de se curvar para baixo) e alterações na consciência (como sonolência, torpor profundo ou coma).

Publicações científicas
175 artigos
Último publicado: 2026 Mar

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Início
All ages
🏥
SUS: Cobertura mínimaScore: 15%
CID-10: G61.0
🇧🇷Dados SUS / DATASUS
PROCEDIMENTOS SIGTAP (2)
0202010694
Sequenciamento completo do exoma (WES)genetic_test
0301070040
Atendimento em reabilitação — doenças rarasrehabilitation
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

🫁
Pulmão
5 sintomas
🧠
Neurológico
4 sintomas
👁️
Olhos
3 sintomas
💪
Músculos
2 sintomas
🛡️
Imunológico
2 sintomas
😀
Face
2 sintomas

+ 29 sintomas em outras categorias

Características mais comuns

90%prev.
Velocidade de condução nervosa motora diminuída
Muito frequente (99-80%)
90%prev.
Infecção grave
Muito frequente (99-80%)
90%prev.
Desmielinização do SNC
Muito frequente (99-80%)
90%prev.
Ataxia
Muito frequente (99-80%)
90%prev.
Confusão
Muito frequente (99-80%)
90%prev.
EMG: resposta decremental do potencial de ação muscular composto à estimulação nervosa repetitiva
Muito frequente (99-80%)
48sintomas
Muito frequente (8)
Frequente (15)
Ocasional (25)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 48 características clínicas mais associadas, ordenadas por frequência.

Velocidade de condução nervosa motora diminuídaDecreased motor nerve conduction velocity
Muito frequente (99-80%)90%
Infecção graveSevere infection
Muito frequente (99-80%)90%
Desmielinização do SNCCNS demyelination
Muito frequente (99-80%)90%
Ataxia
Muito frequente (99-80%)90%
ConfusãoConfusion
Muito frequente (99-80%)90%

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico175PubMed
Últimos 10 anos120publicações
Pico202521 papers
Linha do tempo
2026Hoje · 2026📈 2025Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

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Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

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Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Encefalite do tronco cerebral Bickerstaff

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Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

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Publicações mais relevantes

Timeline de publicações
125 papers (10 anos)
#1

Bickerstaff brainstem encephalitis: a 13-case series and literature review.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology2026 Feb 26
#2

Anti-GQ1b Antibody Syndrome: A Clinician-Oriented Perspective on Diagnostics, Therapy, and Atypical Phenotypes-With an Illustrative 16-Case Institutional Series.

Journal of clinical medicine2026 Jan 19

Anti-GQ1b antibody syndrome (AGABS) unifies triad-defined Miller Fisher syndrome (MFS), Bickerstaff brainstem encephalitis (BBE), and the ophthalmoplegic variant of Guillain-Barré syndrome (GBS-O) under a post-infectious immune mechanism centered on IgG to disialosyl gangliosides. The spectrum also encompasses triad-minus phenotypes-acute ophthalmoparesis without ataxia, acute vestibular syndrome, optic involvement, and acute sensory-ataxic neuropathy. A molecular-mimicry model with complement-mediated nodal/paranodal dysfunction explains severe early deficits despite bland limb nerve conduction studies (NCSs), the cranial/proprioceptive predilection, and generally favorable treatment responsiveness to immunotherapy. In practice, a serology-first strategy, complemented by targeted electrophysiology-blink and H-reflex testing, and, where feasible, paired SEP-ABR showing a literature-supported dissociation (normal ABR with impaired median-nerve cortical SEPs), which, in our series, was documented in one illustrative BBE case-and by structured neuro-otologic examination, mitigates the "normal-NCS trap" and enables timely treatment. Intravenous immunoglobulin (IVIg) is first-line; plasma exchange (PLEX) is an alternative in severe or IVIg-ineligible cases; and intravenous methylprednisolone (IVMP) may be added selectively for central/optic-weighted phenotypes without routine oral taper. We consolidate actionable diagnostic and therapeutic steps and examine them in an institutional series of 16 consecutive seropositive patients (2015-2025): all were anti-GQ1b-positive with frequent GT1a co-reactivity; most reported an antecedent infection-typically upper respiratory, less often gastrointestinal-within the two weeks before onset; limb NCSs were often nondiagnostic whereas reflex/evoked-potential studies were informative; two required intubation in addition to IVIg; outcomes were generally favorable with early immunotherapy. The practical message: order anti-GQ1b at first contact, pair targeted electrophysiology with neuro-otology, and treat early to exploit reversible nodal/paranodal dysfunction.

#3

Bickerstaff Brainstem Encephalitis with a Decorticate-like Posture, Involuntary Movements, Impaired Visual Acuity, and Prolonged Motor Disability.

Internal medicine (Tokyo, Japan)2026 Jan 15

The acute immune-mediated disorder, Bickerstaff brainstem encephalitis (BBE), is characterized by consciousness disturbance, external ophthalmoplegia, and ataxia. BBE is usually readily diagnosed and patients recover well, but rare features may sometimes obscure the diagnosis, and some patients develop prolonged weakness. We herein describe a Japanese patient with BBE who presented with uncharacteristic features of a decorticate-like posture, involuntary movements, and impaired visual acuity, entered a coma requiring intubation, and later required orthosis-assisted ambulation for 10 months. Despite these uncharacteristic features, the typical triad and other BBE characteristic features can be valuable for making an early diagnosis. BBE with a coma or intubation may therefore occasionally lead to prolonged weakness.

#4

Anti-GQ1b antibody syndrome: clinical overlap of Bickerstaff brainstem encephalitis and Miller Fisher syndrome-a diagnostic conundrum.

BMJ case reports2025 Oct 15

This case presents an early adolescent girl who initially presented with clinical features overlapping Bickerstaff brainstem encephalitis and Miller Fisher syndrome, including progressive lower limb weakness, cranial neuropathies, hyperreflexia, positive Babinski sign and hypersomnolence following a gastrointestinal illness. MRI revealed brainstem involvement, and cerebrospinal fluid analysis showed albumin cytologic dissociation. Further investigations revealed a positive serum anti-GQ1b antibody titre of 1:160, leading to a diagnosis of anti-GQ1b antibody syndrome. She was treated with immunotherapy (intravenous immunoglobulin), which resolved her symptoms. These overlapping conditions share anti-GQ1b positivity but differ in clinical and radiological findings, emphasising the importance of recognising this evolving autoimmune spectrum for timely diagnosis and management.

#5

Overlapping Miller Fisher Syndrome, Bickerstaff Brainstem Encephalitis, and Guillain-Barré Syndrome without glycolipid antibodies-a case report and literature review.

Clinical neurology and neurosurgery2025 Nov

We present a rare case of a 56-year-old female presenting with overlapping features of Miller Fisher syndrome (MFS), Bickerstaff's brainstem encephalitis (BBE) and Guillain-Barré syndrome (GBS), despite seronegativity for anti-GQ1b, GM1, GD1b, GT1a, and GT1b IgG antibodies. The patient developed sequential neurological deficits (ophthalmoplegia, ataxia, tetraparesis, and altered consciousness) following an upper respiratory infection. Electrophysiological studies confirmed acute motor-sensory axonal neuropathy, while cerebrospinal fluid analysis showed albuminocytological dissociation. Dual intravenous immunoglobulin (IVIG) courses and methylprednisolone therapy led to partial recovery, with independent ambulation achieved by day 76. This case underscores the complexity of overlapping anti-GQ1b antibody syndromes and highlights the need for alternative diagnostic biomarkers in seronegative patients.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC94 artigos no totalmostrando 115

2026

Bickerstaff brainstem encephalitis: a 13-case series and literature review.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2026

Anti-GQ1b Antibody Syndrome: A Clinician-Oriented Perspective on Diagnostics, Therapy, and Atypical Phenotypes-With an Illustrative 16-Case Institutional Series.

Journal of clinical medicine
2026

Bickerstaff Brainstem Encephalitis with a Decorticate-like Posture, Involuntary Movements, Impaired Visual Acuity, and Prolonged Motor Disability.

Internal medicine (Tokyo, Japan)
2025

Overlap of Bickerstaff Encephalitis and Pharyngeal-Cervical-Brachial Variant of Guillain-Barré Syndrome Following COVID-19 Infection.

Cureus
2025

Guillain-Barré Syndrome and Variants.

Neurologic clinics
2025

Anti-GQ1b antibody syndrome: clinical overlap of Bickerstaff brainstem encephalitis and Miller Fisher syndrome-a diagnostic conundrum.

BMJ case reports
2025

Overlapping Miller Fisher Syndrome, Bickerstaff Brainstem Encephalitis, and Guillain-Barré Syndrome without glycolipid antibodies-a case report and literature review.

Clinical neurology and neurosurgery
2025

Neurological manifestations of chronic graft versus host disease.

Internal medicine journal
2025

Acute Bickerstaff Brainstem Encephalitis in a Middle-Aged Male: Diagnostic Challenges and Therapeutic Responses.

Cureus
2025

Bickerstaff encephalitis: a comprehensive narrative review of pathophysiology, clinical features, and global health considerations.

Annals of medicine and surgery (2012)
2025

A retrospective observational study of clinical and electrophysiological types of Guillain-Barre syndrome from Delhi.

Journal of family medicine and primary care
2025

Bickerstaff brainstem encephalitis developed quickly after COVID-19 infection.

Acute medicine &amp; surgery
2025

Case Report: Therapeutic effect of efgartigimod in refractory anti-GQ1b antibody syndrome coexisting with myasthenia gravis.

Frontiers in immunology
2025

Utility of the combination of median nerve SEPs and auditory brainstem responses for diagnosing Bickerstaff brainstem encephalitis.

Clinical neurophysiology : official journal of the International Federation of Clinical Neurophysiology
2025

Atypical Overlap Presentation in Guillain-Barré Syndrome: Lessons From a Case Report.

Cureus
2025

Influenza A-triggered Bickerstaff brainstem encephalitis successfully treated with therapeutic plasma exchange: A case report.

Hematology, transfusion and cell therapy
2025

Frequency of Guillain-Barré Syndrome During the COVID-19 Pandemic: A Multicenter Study.

Muscle &amp; nerve
2025

Rehabilitation of a Patient With Bickerstaff Brainstem Encephalitis Presenting With Ataxia.

Cureus
2025

A Rare Case of Bickerstaff Encephalitis in Childhood: A Case Report.

Neurology international
2024

Bickerstaff brainstem encephalitis-Miller-Fisher syndrome (BBE-MFS) overlap with negative anti-GQ1b serology.

BMJ case reports
2025

First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice.

Radiology case reports
2025

Positive Antiganglioside Antibodies in a Patient with Primary Diffuse Large B-cell Lymphoma of the Central Nervous System.

Internal medicine (Tokyo, Japan)
2024

The First Report of Bickerstaff Brainstem Encephalitis Induced by Atezolizumab for Metastatic Breast Cancer.

Acta medica Okayama
2024

Clinical presentation and symptomatology of Guillain-Barré syndrome: A literature review.

Medicine
2024

The spectrum of anti-GQ1B antibody syndrome: beyond Miller Fisher syndrome and Bickerstaff brainstem encephalitis.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2024

Bickerstaff Brainstem Encephalitis Presenting With Negative Anti-GM1 and Anti-GQ1B Antibodies.

Cureus
2024

Bickerstaff Brainstem Encephalitis With Exceptionally Fast Recovery.

Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society
2024

Expanding Clinical Spectrum of Anti-GQ1b Antibody Syndrome: A Review.

JAMA neurology
2024

Utility of Brainstem Auditory Evoked Response as a Diagnostic Tool and Rituximab as a Treatment for Severe Bickerstaff Brainstem Encephalitis: A Case Report.

Cureus
2024

Case report: Shingles-associated probable Bickerstaff brainstem encephalitis with IgM anti-sulfatide positivity.

Frontiers in immunology
2024

Anti-sulfatide antibody-related Guillain-Barré syndrome presenting with overlapping syndromes or severe pyramidal tract damage: a case report and literature review.

Frontiers in neurology
2024

Guillain Barre syndrome mimicking brain death.

The journal of the Royal College of Physicians of Edinburgh
2024

Bickerstaff encephalitis in childhood: a review of 74 cases in the literature from 1951 to today.

Frontiers in neurology
2024

[Bickerstaff brainstem encephalitis preceding central nervous system relapse of diffuse large B-cell lymphoma].

[Rinsho ketsueki] The Japanese journal of clinical hematology
2023

Miller-Fisher Syndrome Unveiled in the Presence of Cholangiocarcinoma.

Cureus
2023

Guillain-Barré Syndrome Presenting as Symmetrical Proximal Muscle Weakness: An Atypical Presentation.

Cureus
2023

Delayed onset Bickerstaff brainstem encephalitis overlapping Miller-Fisher Syndrome during SARS-CoV-2 infection.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2023

Bickerstaff's brainstem encephalitis: a rare case of neurologic complication in Ulcerative Colitis.

BMC neurology
2023

Bickerstaff brainstem encephalitis: A case report.

Radiology case reports
2023

JAPANESE ENCEPHALITIS VIRUS TRIGGERED OVERLAPPING MILLER FISHER SYNDROME WITH BICKERSTAFF ENCEPHALITIS IN A YOUNG FILIPINO CRUISE LINE WORKER.

European journal of case reports in internal medicine
2024

Enhancement of Subarachnoid Oculomotor Nerves in Bickerstaff Brainstem Encephalitis.

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques
2023

Nationwide survey of childhood Guillain-Barré syndrome, Fisher syndrome, and Bickerstaff brainstem encephalitis in Japan.

Brain &amp; development
2022

Bickerstaff encephalitis: An uncommon sequalae of a bacterial infection.

The journal of the Royal College of Physicians of Edinburgh
2022

Mild Encephalitis/Encephalopathy with a Reversible Splenial Lesion Coincidents with Bickerstaff Brainstem Encephalitis.

Neurology India
2022

Weakness in both lower limbs for 1 week and blepharoptosis for 3 days in a boy aged 1 year and 7 months.

Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics
2022

A Case Report of Herpes Zoster-Associated Bickerstaff Brainstem Encephalitis.

Infection and drug resistance
2022

Case report: A pediatric case of Bickerstaff brainstem encephalitis after COVID-19 vaccination and Mycoplasma pneumoniae infection: Looking for the culprit.

Frontiers in immunology
2022

Guillain-Barré syndrome spectrum as manifestation of HIV-related immune reconstitution inflammatory syndrome: case report and literature review.

The Brazilian journal of infectious diseases : an official publication of the Brazilian Society of Infectious Diseases
2022

Atypical anti-NMDA receptor encephalitis associated with varicella zoster virus infection.

Journal of neurovirology
2022

Modified Zipper Method, a Promising Treatment Option in Severe Pediatric Immune-Mediated Neurologic Disorders.

Journal of child neurology
2022

Inpatient Management of Encephalopathy.

Cureus
2022

Paroxysmal Dysarthria Ataxia-Tremor-Blepharospasm Syndrome in Bickerstaff Brainstem Encephalitis; A Variant of Paroxysmal Dysarthria Ataxia Syndrome.

Neurology India
2022

Bickerstaff brainstem encephalitis treated using selective plasma exchange owing to anaphylaxis attributed to fresh frozen plasma: A case report.

Therapeutic apheresis and dialysis : official peer-reviewed journal of the International Society for Apheresis, the Japanese Society for Apheresis, the Japanese Society for Dialysis Therapy
2022

Bickerstaff brainstem encephalitis: clinical, neurophysiological, laboratory and postmortem findings of a case presenting as encephalomyelitis.

BMJ case reports
2021

Case Report: Takotsubo Cardiomyopathy in Bickerstaff Brainstem Encephalitis Triggered by COVID-19.

Frontiers in neurology
2022

[Pathophysiological and diagnostic aspects of Guillain-Barré syndrome].

La Revue de medecine interne
2021

Bickerstaff Brainstem Encephalitis with Isolated Acute Bilateral Ophthalmoplegia: An Unusual Presentation.

Annals of Indian Academy of Neurology
2021

Helicobacter pylori Infection and Extragastric Diseases-A Focus on the Central Nervous System.

Cells
2021

Imaging Presentation of Bickerstaff Brainstem Encephalitis.

The Neurohospitalist
2021

Seasonality in the incidence of anti-GQ1b antibody syndrome-A territory-wide study.

Brain and behavior
2021

[Interdisciplinary rehabilitation of a patient with associated Bickerstaff brainstem encephalitis and Guillain-Barré syndrome].

Revue medicale de Liege
2021

Autoimmune Brainstem Encephalitis: An Illustrative Case and a Review of the Literature.

Journal of clinical medicine
2021

Abnormal Movements in Bickerstaff Brainstem Encephalitis Mimicking Anti-N-Methyl-d-Aspartate Receptor Encephalitis.

JAMA neurology
2021

Bickerstaff brainstem encephalitis with Guillain-Barré syndrome overlap following chlamydia infection.

BMJ case reports
2021

Recurrent Miller-Fisher syndrome overlapping Guillain-Barrè syndrome and Bickerstaff brainstem encephalitis: A case report.

Clinical neurology and neurosurgery
2021

Clinical Characterization of Anti-GQ1b Antibody Syndrome in Childhood.

Frontiers in pediatrics
2021

Cholesterol-added antigens can enhance antiglycolipid antibody activity: Application to antibody testing.

Journal of neuroimmunology
2021

Paroxysmal Dysarthria Ataxia-Tremor-Blepharospasm Syndrome in Bickerstaff Brainstem Encephalitis: A Variant of Paroxysmal Dysarthria Ataxia Syndrome.

Neurology India
2021

Determining the Utility of the Guillain-Barré Syndrome Classification Criteria.

Journal of clinical neurology (Seoul, Korea)
2020

Paediatric Bickerstaff brainstem encephalitis: A rare case report.

JPMA. The Journal of the Pakistan Medical Association
2020

Bickerstaff brainstem encephalitis with or without anti-GQ1b antibody.

Neurology(R) neuroimmunology &amp; neuroinflammation
2021

Refractory Psychomotor Agitation Responding to Dexmedetomidine Infusion: A Rare Presentation of Bickerstaff Brainstem Encephalitis (BBE).

Neurocritical care
2020

Clinical Characteristic Analysis of Seven Children With Bickerstaff Brainstem Encephalitis in China.

Frontiers in neurology
2020

Case of Bickerstaff encephalitis with positive glutamic acid decarboxylase antibodies.

BMJ case reports
2020

[Anti-GQ1b syndrome. A child with Miller-Fisher-Bickerstaff syndrome].

Archivos argentinos de pediatria
2020

Relapsing Bickerstaff Brainstem Encephalitis After Autologous Stem Cell Transplant.

Journal of clinical neuromuscular disease
2020

[A man in his sixties with gait ataxia, dysarthria and mild cognitive impairment].

Tidsskrift for den Norske laegeforening : tidsskrift for praktisk medicin, ny raekke
2020

A Probable Case of Recurrent Bickerstaff Brainstem Encephalitis With Fulminant Course in a Pediatric Patient.

The neurologist
2020

Neuroimaging of Multiple Sclerosis Mimics.

Neurologic clinics
2019

Acute psychosis secondary to atypical Bickerstaff brainstem encephalitis.

Asian journal of psychiatry
2019

Acute vestibular syndrome associated with anti-GQ1b antibody.

Neurology
2019

Guillain-Barré syndrome and related diseases after influenza virus infection.

Neurology(R) neuroimmunology &amp; neuroinflammation
2019

[Clinical features of 19 children with Bickerstaff brainstem encephalitis].

Zhonghua er ke za zhi = Chinese journal of pediatrics
2019

Antecedent infections in Fisher syndrome: sources of variation in clinical characteristics.

Journal of neurology
2019

Clinical spectrum of the anti-GQ1b antibody syndrome: a case series of eight patients.

Acta neurologica Belgica
2019

Long-term Sequelae of Pediatric Bickerstaff Brainstem Encephalitis Includes Autonomic and Sleep Dysregulation.

Journal of child neurology
2018

Area postrema syndrome as frequent feature of Bickerstaff brainstem encephalitis.

Annals of clinical and translational neurology
2019

Bickerstaff Brainstem Encephalitis and overlapping Guillain-Barré syndrome in children: Report of two cases and review of the literature.

European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society
2019

An overlapping case of Bickerstaff brainstem encephalitis and acute motor axonal neuropathy variant of Guillain-Barré syndrome associated with systemic lupus erythematosus.

Polish archives of internal medicine
2018

Varied antibody reactivities and clinical relevance in anti-GQ1b antibody-related diseases.

Neurology(R) neuroimmunology &amp; neuroinflammation
2018

Overlap of Bickerstaff brainstem encephalitis/Guillain-Barré syndrome simulating brain death.

Neurology India
2018

Miller Fisher syndrome, Bickerstaff brainstem encephalitis and Guillain-Barré syndrome overlap with persistent non-demyelinating conduction blocks: a case report.

BMC neurology
2018

A Case Report of Overlapping Miller Fisher Syndrome, Guillain-Barré Syndrome, and the Bickerstaff Brainstem Encephalitis.

The neurologist
2018

Headache and Ophthalmoparesis: Case Report of an "Atypical" Incomplete Miller-Fisher Syndrome.

Headache
2018

Anti-ganglioside complex antibody profiles in a recurrent complicated case of GQ1b-seronegative miller fisher syndrome and Bickerstaff brainstem encephalitis: a case report.

BMC neurology
2018

Miller-Fisher syndrome complicated by Bickerstaff brainstem encephalitis: A case report.

Medicine
2018

Bickerstaff brainstem encephalitis in a patient with ankylosing spondylitis on tumour necrosis factor-alpha inhibitor.

Clinical and experimental rheumatology
2018

Pediatric Bickerstaff brainstem encephalitis: a systematic review of literature and case series.

Journal of neurology
2017

Cerebrospinal fluid findings in Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathies.

Handbook of clinical neurology
2020

Early electrophysiological findings in Fisher-Bickerstaff syndrome.

Neurologia
2017

[A case of Bickerstaff brainstem encephalitis with transient reflex myoclonus].

Rinsho shinkeigaku = Clinical neurology
2017

Guillain-Barré Syndrome, variants & forms fruste: Reclassification with new criteria.

Clinical neurology and neurosurgery
2016

Altered gene expression of glycosyltransferases and sialyltransferases and total amount of glycosphingolipids following herpes simplex virus infection.

Carbohydrate research
2016

Poster 345 Rehabilitation of Bickerstaff Brainstem Encephalitis: A Case Report.

PM &amp; R : the journal of injury, function, and rehabilitation
2016

Clinical classification of 103 Japanese patients with Guillain-Barré syndrome.

Journal of the neurological sciences
2016

An atypical Bickerstaff's brainstem encephalitis with involvement of spinal cord.

The neuroradiology journal
2016

[Bickerstaff brainstem encephalitis after upper respiratory infection].

Ugeskrift for laeger
2016

Recurrent Diplopia in a Pediatric Patient with Bickerstaff Brainstem Encephalitis.

Case reports in neurological medicine
2016

Recurrent Guillain-Barré syndrome, Miller Fisher syndrome and Bickerstaff brainstem encephalitis.

Journal of the neurological sciences
2016

How often and when Fisher syndrome is overlapped by Guillain-Barré syndrome or Bickerstaff brainstem encephalitis?

European journal of neurology
2016

Listeria meningoencephalitis and anti-GQ1b antibody syndrome.

Infection
2016

Teaching NeuroImages: Extensive vasogenic edema in Bickerstaff brainstem encephalitis.

Neurology
2015

[Fisher Syndrome and Bickerstaff Brainstem Encephalitis].

Brain and nerve = Shinkei kenkyu no shinpo
2015

[Bickerstaff brainstem encephalitis].

Nihon rinsho. Japanese journal of clinical medicine
2015

Progressive subacute Miller-Fisher syndrome successfully treated with plasmapheresis.

Neurologia i neurochirurgia polska

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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Bickerstaff brainstem encephalitis: a 13-case series and literature review.
    Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology· 2026· PMID 41746399mais citado
  2. Anti-GQ1b Antibody Syndrome: A Clinician-Oriented Perspective on Diagnostics, Therapy, and Atypical Phenotypes-With an Illustrative 16-Case Institutional Series.
    Journal of clinical medicine· 2026· PMID 41598737mais citado
  3. Bickerstaff Brainstem Encephalitis with a Decorticate-like Posture, Involuntary Movements, Impaired Visual Acuity, and Prolonged Motor Disability.
    Internal medicine (Tokyo, Japan)· 2026· PMID 41535039mais citado
  4. Anti-GQ1b antibody syndrome: clinical overlap of Bickerstaff brainstem encephalitis and Miller Fisher syndrome-a diagnostic conundrum.
    BMJ case reports· 2025· PMID 41101789mais citado
  5. Overlapping Miller Fisher Syndrome, Bickerstaff Brainstem Encephalitis, and Guillain-Barr&#xe9; Syndrome without glycolipid antibodies-a case report and literature review.
    Clinical neurology and neurosurgery· 2025· PMID 40886512mais citado
  6. 후뇌염의 영상 소견 스펙트럼: 임상 화보.
    J Korean Soc Radiol· 2026· PMID 41971108recente
  7. Autoimmune maladies of the brainstem.
    Handb Clin Neurol· 2026· PMID 41896006recente
  8. Author's reply: Bickerstaff Brainstem Encephalitis with Decorticate-like Posture, Involuntary Movements, Impaired Visual Acuity, and Prolonged Motor Disability.
    Intern Med· 2026· PMID 41882904recente
  9. Clinical Vigilance in Bickerstaff Brainstem Encephalitis: From Psychiatric Manifestations to Long-term Recovery.
    Intern Med· 2026· PMID 41882903recente
  10. Reversible Right Cerebellar FLAIR Hyperintensity in Bickerstaff Brainstem Encephalitis.
    Intern Med· 2026· PMID 41882901recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:79138(Orphanet)
  2. MONDO:0019208(MONDO)
  3. GARD:18944(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q3508622(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Encefalite do tronco cerebral Bickerstaff
Compêndio · Raras BR

Encefalite do tronco cerebral Bickerstaff

ORPHA:79138 · MONDO:0019208
Prevalência
Unknown
Herança
Not applicable
CID-10
G61.0 · Síndrome de Guillain-Barré
CID-11
Início
All ages
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C1960543
EuropePMC
Wikidata
Papers 10a
DiscussaoAtiva

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