Uma doença respiratória causada por sangramentos repetidos e espalhados nos saquinhos de ar dos pulmões, sem uma causa aparente e que afeta principalmente crianças. A maioria dos pacientes apresenta anemia, tosse e manchas nos pulmões, visíveis em radiografias de tórax.
Introdução
O que você precisa saber de cara
Uma doença respiratória causada por sangramentos repetidos e espalhados nos saquinhos de ar dos pulmões, sem uma causa aparente e que afeta principalmente crianças. A maioria dos pacientes apresenta anemia, tosse e manchas nos pulmões, visíveis em radiografias de tórax.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 12 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 35 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
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Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Hemossiderose pulmonar, idiopática
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Outros ensaios clínicos
3 ensaios clínicos encontrados, 1 ativos.
Publicações mais relevantes
[Clinical, imaging, and pathological features of diffuse alveolar filling diseases].
Diffuse alveolar filling disease (DAFD) is characterized by diffuse lesions in both lungs caused by the abnormal filling of bilateral alveolar spaces (and sometimes the terminal bronchioles) with substances such as water, blood, lipids, inflammatory cells, pathogens, or tumor cells. Clinically, it is characterized mainly by dyspnea and hypoxemia, while imaging examinations reveal diffuse ground-glass opacities or consolidation shadows in both lungs. In the early stage, lung volume generally remains unchanged, but pulmonary interstitial fibrosis may occur in the advanced stage. Typical diseases included in this category are pulmonary alveolar proteinosis (PAP), diffuse alveolar hemorrhage (DAH), idiopathic pulmonary hemosiderosis (IPH), and pneumocystis pneumonia (PCP). While these diseases share certain similarities in clinical symptoms, imaging features, and pathological manifestations, each has its own distinct characteristics. Bronchoalveolar lavage fluid (BALF) detection and lung biopsy are the main confirmatory diagnostic methods. As a newly proposed concept, DAFD and diffuse interstitial lung diseases (DILD) both belong to diffuse parenchymal lung diseases (DPLD). The formal proposal of this new concept is of great significance for the diagnosis and differential diagnosis of DPLD. 弥漫性肺泡填充性疾病(DAFD)是指双侧肺泡腔被水、血液、类脂、炎性渗出物、病原微生物或肿瘤细胞等物质异常填充所导致的双肺弥漫性病变。临床以呼吸困难、低氧血症为主要表现,影像学可见双肺弥漫性磨玻璃影或实变影,晚期可能出现肺间质纤维化。典型疾病包括肺泡蛋白沉着症(PAP)、弥漫性肺泡出血(DAH)、特发性肺含铁血黄素沉着症(IPH)及肺孢子菌肺炎(PCP)等,各类疾病在症状、影像学特征及病理表现上既相似又各具特点。支气管肺泡灌洗液检测和肺活检是其主要的确诊方法。DAFD与弥漫性间质性肺病(DILD)同属弥漫性实质性肺病(DPLD),这个新概念的提出对DPLD的诊断和鉴别诊断具有重要的意义。.
The role of arterial embolization in pediatric Idiopathic Pulmonary Hemosiderosis: a case report and literature review.
Idiopathic Pulmonary Hemosiderosis is a rare life-threatening disorder, characterized by recurrent episodes of Diffuse Alveolar Hemorrhage. Currently, there are still many unresolved questions concerning its actual etiopathogenesis and, consequently, the most appropriate treatment to adopt. Through our case report we aim to highlight the role of angiography in identifying the presence of abnormal pulmonary collaterals as a possible cause of therapeutic failure. Although further studies are needed and even if it remains unclear if they are simultaneous problems or causative of one another, embolization of abnormal pulmonary arteries appears to play an important role in cases of Idiopathic Pulmonary Hemosiderosis unresponsive to conventional therapies and presenting severe side effects due to immunosuppression. After an extensive literature review, we found only two studies supporting our hypothesis; to our knowledge, this is the first case in Western world.
Idiopathic Pulmonary Hemosiderosis Characterized by Recurrent Infections and Anemia.
Idiopathic pulmonary hemosiderosis (IPH) is a rare condition characterized by recurrent alveolar bleeding, hemosiderin deposition, and pulmonary fibrosis, predominantly affecting children. Its diagnosis and management are complex. A case involving a 3-year-old female patient with iron deficiency anemia and recurrent pneumonia was analyzed supported by laboratory and imaging investigations. Clinical symptoms included nausea, fever, and pallor. Initial evaluations indicated moderate anemia (HGB 73 g/L) and signs of infection, with imaging revealing diffuse ground-glass opacities. Following the exclusion of other conditions, a diagnosis of IPH was established, and comprehensive treatment resulted in notable clinical improvement. This case underscores the importance of multidisciplinary collaboration in diagnosing and managing IPH, particularly in pediatric patients, to enhance outcomes and quality of life.
Idiopathic Pulmonary Hemosiderosis in a Child Diagnosed by Transbronchial Cryobiopsy.
Age at disease onset is an independent risk factor for physical growth of children with idiopathic pulmonary hemosiderosis.
Idiopathic pulmonary hemosiderosis (IPH), a pediatric pulmonary disorder requiring prolonged corticosteroid therapy raises concerns about growth impairment. While corticosteroid-induced stunting is well-documented, its specific impact on the height of IPH patients remains unclear. This study aimed to evaluate the impact of corticosteroid exposure on height outcomes and identify key predictors of growth restriction in children with IPH. In this retrospective cohort study, 45 IPH patients [2018-2023] were stratified into normal-stature (n=37) and short-stature (n=8) groups based on anthropometric criteria. Multivariable Cox regression and comparative analyses assessed age at onset, diagnostic delay, corticosteroid duration, nutritional parameters, pulmonary function, and growth hormone (GH) therapy efficacy. Short-stature patients demonstrated an earlier disease onset (P=0.004) and prolonged diagnostic delay (P=0.002). A younger age at onset independently predicted impaired height growth [hazard ratio (HR) =0.435, 95% confidence interval (CI): 0.206-0.920, P=0.02], while corticosteroid duration showed no association (P=0.45). Secondary analyses identified synergistic effects of anemia (P=0.02), malnutrition (P=0.045), and pulmonary fibrosis (P=0.008). GH therapy significantly improved height velocity (P<0.001) and bone metabolism markers (P<0.05). Early IPH onset, rather than corticosteroid exposure, drives growth impairment in children. Timely diagnosis, nutritional optimization, and adjunctive GH therapy may mitigate height deficits, underscoring the significance of multidisciplinary management strategies.
Publicações recentes
Bilateral Lung Transplantation for Lymphangioleiomyomatosis With Secondary Pulmonary Hemosiderosis: A Case Report.
[Clinical, imaging, and pathological features of diffuse alveolar filling diseases].
The role of arterial embolization in pediatric Idiopathic Pulmonary Hemosiderosis: a case report and literature review.
Idiopathic Pulmonary Hemosiderosis in a Child Diagnosed by Transbronchial Cryobiopsy.
Idiopathic Pulmonary Hemosiderosis Characterized by Recurrent Infections and Anemia.
📚 EuropePMC444 artigos no totalmostrando 117
[Clinical, imaging, and pathological features of diffuse alveolar filling diseases].
Zhonghua jie he he hu xi za zhi = Zhonghua jiehe he huxi zazhi = Chinese journal of tuberculosis and respiratory diseasesThe role of arterial embolization in pediatric Idiopathic Pulmonary Hemosiderosis: a case report and literature review.
Respiratory medicine case reportsIdiopathic Pulmonary Hemosiderosis in a Child Diagnosed by Transbronchial Cryobiopsy.
Pediatric pulmonologyIdiopathic Pulmonary Hemosiderosis Characterized by Recurrent Infections and Anemia.
Clinical laboratoryHeiner syndrome and correlation with food allergy: case report.
Frontiers in allergyBack to the Diving Board: A Rare Cause of Hemoptysis in a Healthy Female Athlete.
Case reports in pulmonologyAge at disease onset is an independent risk factor for physical growth of children with idiopathic pulmonary hemosiderosis.
Translational pediatricsIdiopathic pulmonary hemosiderosis: A pediatric case report.
Respiratory medicine case reportsDifferent clinical presentations of idiopathic pulmonary hemosiderosis.
Anales de pediatriaIdiopathic Pulmonary Hemosiderosis Mimicking Transfusion-Related Acute Lung Injury.
Indian journal of pediatricsIdiopathic Pulmonary Hemosiderosis Complicated by Direct Antiglobulin Test-negative Autoimmune Hemolytic Anemia.
Journal of pediatric hematology/oncologyNeuropsychiatric Side Effects of Hydroxychloroquine in a Patient With Idiopathic Pulmonary Hemosiderosis.
Journal of paediatrics and child healthThe gut-lung axis in celiac disease: a narrative review of pulmonary manifestations and pathogenic mechanisms.
Gastroenterology and hepatology from bed to benchClinical features and risk factors for recurrence of idiopathic pulmonary hemosiderosis in children.
BMC pulmonary medicinePulmonary hemorrhagic syndromes.
Pediatric pulmonologyNovel germline STAT3 gain-of-function mutation causes autoimmune diseases and severe growth failure.
The journal of allergy and clinical immunology. GlobalDiffuse alveolar hemorrhage in pediatrics: Etiologies and outcomes.
Pediatric pulmonologyIdiopathic pulmonary hemosiderosis associated with Kabuki syndrome.
Immunological medicineA Rare Presentation of Late-Onset Idiopathic Pulmonary Hemosiderosis: A Case Report.
CureusPulmonary siderosis complicated with severe mycoplasma pneumoniae pneumonia: A case report.
Respiratory medicine case reportsCardiomyopathy in Celiac Disease: A Systematic Review.
Journal of clinical medicinePanacinar emphysema complicating idiopathic pulmonary hemosiderosis: a case report.
Oxford medical case reportsIdiopathic Pulmonary Hemosiderosis. Reply.
The New England journal of medicineIdiopathic Pulmonary Hemosiderosis.
The New England journal of medicineIdiopathic Pulmonary Hemosiderosis: The Great Hemolytic Anemia Mimicker.
CureusLeflunomide Is Safe and Effective for the Induction and Maintenance of Idiopathic Pulmonary Hemosiderosis Remission.
Pediatric allergy, immunology, and pulmonologyAn Adult Case of Idiopathic Pulmonary Hemosiderosis Associated with Pulmonary Fibrosis and Emphysematous Change.
Internal medicine (Tokyo, Japan)Determining the threshold for azathioprine use in recurrent diffuse alveolar hemorrhage in idiopathic pulmonary hemosiderosis.
The American journal of the medical sciencesIdiopathic pulmonary hemosiderosis and stroke secondary to protein C deficiency in a child with Down syndrome: a case report.
Journal of medical case reportsFatal Invasive Aspergillosis in a Child with Idiopathic Pulmonary Hemosiderosis.
Turkish archives of pediatricsLane-Hamilton Syndrome in an Adult With Down Syndrome: A Case Report.
CureusDiffuse alveolar hemorrhage in children with interstitial lung disease: Determine etiologies!
Pediatric pulmonologyRituximab in Idiopathic Pulmonary Hemosiderosis in Children: A Novel and Less Toxic Treatment Option.
Pharmaceuticals (Basel, Switzerland)The role of flexible bronchoscopy in the diagnostic pathway of children with unexplained peripheral eosinophilia.
Pediatrics international : official journal of the Japan Pediatric SocietyUpdates in idiopathic pulmonary hemosiderosis in 2022: A state of the art review.
Pediatric pulmonologyAssessment of type I interferon signatures in undifferentiated inflammatory diseases: A Japanese multicenter experience.
Frontiers in immunologyCeliac disease and idiopathic pulmonary hemosiderosis: a literature review of the Lane-Hamilton syndrome.
Postgraduate medicinePlace of bronchoscopy in the diagnostics and follow-up of patients with idiopathic pulmonary hemosiderosis.
Folia medicaLate presentation of lane-hamilton syndrome in a 33 year old female: A case report.
International journal of applied & basic medical researchThe Spectrum of Autoantibodies in Adult Patients With Idiopathic Pulmonary Hemosiderosis: A Brief Review of the Literature.
CureusAn Infant With Interstitial Lung Disease of Rare Cause.
ChestLiposteroid Therapy for Idiopathic Pulmonary Hemosiderosis: A Scoping Review of the Literature.
Prague medical reportComparative Analysis of Adult Patients With Idiopathic Pulmonary Hemosiderosis and Lane-Hamilton Syndrome: A Systematic Review of the Literature in the Period 1971-2022.
CureusStrike while the iron is hot: diagnosis of pediatric idiopathic pulmonary hemosiderosis.
BloodRecurrence of idiopathic pulmonary hemosiderosis in adults with childhood onset: A case report and literature review.
Respiratory investigationA 49-year-old man with ischemic cardiomyopathy and persistent hemoptysis for eighteen months.
The American journal of the medical sciencesProposed Pathogenesis of Diffuse Alveolar Hemorrhage in Idiopathic Pulmonary Hemosiderosis.
LungRare causes of anemia in children: Two cases of idiopathic pulmonary hemosiderosis.
Respiratory medicine case reportsIdiopathic pulmonary hemosiderosis: A mimic of severe COVID-19 pneumonia.
Pediatrics international : official journal of the Japan Pediatric SocietyAdult patients with idiopathic pulmonary hemosiderosis: a comprehensive review of the literature.
Clinical rheumatologyAssociation between idiopathic pulmonary hemosiderosis and celiac disease in pediatric patients: A scoping review of the literature over the past 50 years.
Pediatric pulmonologyPrevalence of autoantibodies in pediatric patients with idiopathic pulmonary hemosiderosis: a scoping review of the literature in the period 1980-2021.
Clinical rheumatologyThe etiology, clinical profile, and outcome of diffuse alveolar hemorrhage in children: a ten-year single-center experience.
Translational pediatricsPuzzling (IRIDA-Like and Hemolytic) Anemia in a Child With Idiopathic Pulmonary Hemosiderosis.
Journal of pediatric hematology/oncologyChildren with Heiner Syndrome: A Single-Center Experience.
Children (Basel, Switzerland)Short Review of Liposteroid: A Novel Targeted Glucocorticoid Preparation for Treatment of Autoimmune and Inflammatory Diseases.
Prague medical reportIdiopathic Pulmonary Hemosiderosis: An Unexplored Cause of Treatment Refractory Pediatric Iron Deficiency Anemia.
The Indian journal of radiology & imagingDifferentiation of idiopathic pulmonary hemosiderosis from rheumatologic and autoimmune diseases causing diffuse alveolar hemorrhage: establishing a diagnostic approach.
Clinical rheumatologyCoincidence or connection? A patient with concurrent Lane Hamilton Syndrome and idiopathic membranous nephropathy.
Respiratory medicine case reportsLung transplant to manage end-stage lung disease due to idiopathic pulmonary hemosiderosis: A review of the literature.
Respiratory investigationDiffuse alveolar hemorrhage in children with trisomy 21.
Pediatric rheumatology online journalDiffuse alveolar haemorrhage with suspected idiopathic pulmonary hemosiderosis and decrease in lung diffusing capacity and chronic respiratory failure.
BMJ case reportsPulmonary Nocardia infection in a child with idiopathic pulmonary hemosiderosis.
BMC pulmonary medicineIs It Time to Call Idiopathic Pulmonary Hemosiderosis by the Correct Name: Immune-Mediated Pulmonary Hemosiderosis?
The American journal of the medical sciencesRisk factors for recurrent pulmonary exacerbation in idiopathic pulmonary hemosiderosis.
Pediatric pulmonologyIdiopathic pulmonary hemosiderosis: A state of the art review.
Respiratory medicineIdiopathic pulmonary hemosiderosis: a review of the treatments used during the past 30 years and future directions.
Clinical rheumatologyIdiopathic Pulmonary Hemosiderosis Associated with Emphysematous Change in an Adult Who Underwent Lung Transplantation.
Internal medicine (Tokyo, Japan)Diffuse alveolar hemorrhage in infants: Report of five cases.
Respiratory medicine case reportsPossible association of idiopathic pulmonary hemosiderosis with rheumatoid arthritis: A case report.
Experimental and therapeutic medicineDisease recurrence after lung transplantation for idiopathic pulmonary hemosiderosis.
Respiratory medicine case reportsIdiopathic pulmonary hemosiderosis - A rare cause of chronic anemia.
Monaldi archives for chest disease = Archivio Monaldi per le malattie del toraceAggressive corticosteroid treatment in childhood idiopathic pulmonary hemosiderosis with better outcome.
Journal of the Formosan Medical Association = Taiwan yi zhiSuccessful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome.
Case reports in pediatricsCobalamin C deficiency presenting with diffuse alveolar hemorrhage and pulmonary microangiopathy.
Pediatric pulmonologyIdiopathic Pulmonary Hemosiderosis as a Mimic of Pulmonary Vasculitis: A Case Report and Review of the Literature.
Current allergy and asthma reportsThoracotomy Wound Dehiscence After Lung Transplant Is an Effective Surgical Solution: A Case Report.
Transplantation proceedingsEarly diagnosis of idiopathic pulmonary hemosiderosis using gastric lavage.
Pediatrics international : official journal of the Japan Pediatric SocietyChildhood diffuse parenchymal lung diseases: We need a new classification.
The clinical respiratory journal[Diffuse alveolar hemorrhage in children].
Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatricsCryobiopsy in the diagnosis of idiopathic pulmonary hemosiderosis: a case report.
Journal of thoracic diseaseExtracorporeal Membrane Oxygenation for Diffuse Alveolar Hemorrhage Caused by Idiopathic Pulmonary Hemosiderosis: A Case Report and a Review of the Literature.
Journal of pediatric intensive careAutoimmunity and Delayed Diagnosis in Pediatric Idiopathic Pulmonary Hemosiderosis.
Journal of pediatric hematology/oncologyEarly Initiation of Steroid-sparing Drugs in Idiopathic Pulmonary Hemosiderosis.
Indian pediatricsFatal case of Hajdu-Cheney syndrome with idiopathic pulmonary hemosiderosis.
Pediatrics international : official journal of the Japan Pediatric SocietyA different clinical presentation of Heiner syndrome: The case of diffuse alveolar hemorrhage causing massive hemoptysis and hematemesis.
Respiratory medicine case reportsSevere iron-deficiency anemia as initial manifestation of pulmonary hemosiderosis in a child.
Einstein (Sao Paulo, Brazil)Diffuse pulmonary small nodular and patchy infiltrates on chest X-ray with hemoptysis: TB or not TB?-a call for scale up of respiratory medicine services in African TB high burden countries: a case of idiopathic pulmonary hemosiderosis.
The Pan African medical journalClinical characteristics and prognosis of idiopathic pulmonary hemosiderosis in pediatric patients.
The Journal of international medical researchRecurrent idiopathic pulmonary hemosiderosis after long-term remission presented with Sjogren's syndrome: Idiopathic no more?
Respiratory medicine case reportsLiposteroid and methylprednisolone combination therapy for a case of idiopathic lung hemosiderosis.
Respiratory medicine case reportsPulmonary Hemorrhage in Children: Etiology, Clinical Profile and Outcome.
Indian journal of pediatricsRespiratory Distress and Severe Anemia in a Child With Idiopathic Pulmonary Hemosiderosis.
Journal of pediatric hematology/oncology[Diffuse alveolar hemorrhage in 4 girls].
Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatricsIdiopathic pulmonary hemosiderosis: Hemorrhagic flare after 6 years of remission.
Revista portuguesa de pneumologiaMethylprednisolone pulse therapy rescued life-threatening pulmonary hemorrhage due to idiopathic pulmonary hemosiderosis.
The American journal of emergency medicineIdiopathic Pulmonary Hemosiderosis Mimicking Iron Deficiency Anemia: A Delayed Diagnosis?
Hematology reportsIdiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis.
Case reports in pediatricsCorticosteroid in Combination with Leflunomide and Mesenchymal Stem Cells for Treatment of Pediatric Idiopathic Pulmonary Hemosiderosis.
Journal of tropical pediatrics[Idiopathic pulmonary hemosiderosis with dendriform pulmonary ossification].
Biomedica : revista del Instituto Nacional de SaludSevere Alveolar Hemorrhage - What's in it for the Gastroenterologist?
Journal of gastrointestinal and liver diseases : JGLDA Case of Idiopathic Pulmonary Hemosiderosis Presenting With Signs and Symptoms Mimicking Hemolytic Anemia.
Journal of pediatric hematology/oncologyUnusual presentation: Concurrent IgA deficiency and idiopathic pulmonary hemosiderosis.
Pediatric pulmonologyCor triatriatum sinister: a rare underlying cause of pulmonary hemosiderosis.
SpringerPlus[Analysis of the etiology of hemoptysis and its diagnosis and treatment in 106 cases].
Zhonghua er ke za zhi = Chinese journal of pediatricsIdiopathic pulmonary hemosiderosis in adults: review of cases reported in the latest 15 years.
The clinical respiratory journalSevere Respiratory Distress in a Child with Pulmonary Idiopathic Hemosiderosis Initially Presenting with Iron-Deficiency Anemia.
Case reports in pulmonologyAdvances in pediatrics in 2014: current practices and challenges in allergy, gastroenterology, infectious diseases, neonatology, nutrition, oncology and respiratory tract illnesses.
Italian journal of pediatricsIdiopathic pulmonary hemosiderosis complicated by Down syndrome.
Pediatrics international : official journal of the Japan Pediatric SocietyAssociation of Celiac Disease With Idiopathic Pulmonary Hemosiderosis; Lane Hamilton Syndrome.
Iranian journal of pediatricsDecreased VEGF Level Is Associated with Elevated Ferritin Concentration in Bronchoalveolar Lavage Fluid of Children with Interstitial Lung Diseases.
Respiration; international review of thoracic diseasesIdiopathic Pulmonary Hemosiderosis Presenting as Anemia, Failure to Thrive, and Jaundice in a Toddler.
Pediatric emergency careA physician survey reveals differences in management of idiopathic pulmonary hemosiderosis.
Orphanet journal of rare diseasesIdiopathic Pulmonary Hemosiderosis With Allergic Asthma Diagnosis in a Pediatric Patient.
Journal of pediatric hematology/oncologyIdiopathic pulmonary hemosiderosis presenting in an adult: A case report and review of the literature.
Lung India : official organ of Indian Chest SocietyUnexplained childhood anaemia: idiopathic pulmonary hemosiderosis.
Hong Kong medical journal = Xianggang yi xue za zhiA young man with hemoptysis: Rare association of idiopathic pulmonary hemosiderosis, celiac disease and dilated cardiomyopathy.
Lung India : official organ of Indian Chest SocietyAssociações
Organizações que acompanham esta doença — pra ter apoio e orientação
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Comunidades
Grupos ativos de quem convive com esta doença aqui no Raras
Ainda não existe comunidade no Raras para Hemossiderose pulmonar, idiopática
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- [Clinical, imaging, and pathological features of diffuse alveolar filling diseases].Zhonghua jie he he hu xi za zhi = Zhonghua jiehe he huxi zazhi = Chinese journal of tuberculosis and respiratory diseases· 2026· PMID 41820048mais citado
- The role of arterial embolization in pediatric Idiopathic Pulmonary Hemosiderosis: a case report and literature review.
- Idiopathic Pulmonary Hemosiderosis Characterized by Recurrent Infections and Anemia.
- Idiopathic Pulmonary Hemosiderosis in a Child Diagnosed by Transbronchial Cryobiopsy.
- Age at disease onset is an independent risk factor for physical growth of children with idiopathic pulmonary hemosiderosis.
- Bilateral Lung Transplantation for Lymphangioleiomyomatosis With Secondary Pulmonary Hemosiderosis: A Case Report.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:99931(Orphanet)
- OMIM OMIM:178550(OMIM)
- MONDO:0008346(MONDO)
- GARD:6763(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q1052626(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
