Raras
Buscar doenças, sintomas, genes...
Ascite quilosa
ORPHA:1160CID-10 · I89.8CID-11 · DC51.0OMIM 208300DOENÇA RARA

Ascite quilosa é uma forma rara de ascite causada por acúmulo de linfa na cavidade peritoneal, geralmente devido a malignidade intra-abdominal, cirrose hepática ou complicações de cirurgia abdominal, e apresenta distensão abdominal indolor, mas progressiva, dispneia e ganho de peso.

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Introdução

O que você precisa saber de cara

📋

Ascite quilosa é uma forma rara de ascite causada por acúmulo de linfa na cavidade peritoneal, geralmente devido a malignidade intra-abdominal, cirrose hepática ou complicações de cirurgia abdominal, e apresenta distensão abdominal indolor, mas progressiva, dispneia e ganho de peso.

Publicações científicas
1.645 artigos
Último publicado: 2026

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Início
All ages
🏥
SUS: Sem cobertura SUSScore: 0%
CID-10: I89.8
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

🫃
Digestivo
2 sintomas
🧬
Pele e cabelo
1 sintomas
🩸
Sangue
1 sintomas
👁️
Olhos
1 sintomas

+ 4 sintomas em outras categorias

Características mais comuns

90%prev.
Linfedema
Muito frequente (99-80%)
90%prev.
Ascite
Muito frequente (99-80%)
55%prev.
Nódulo subcutâneo
Frequente (79-30%)
17%prev.
Morfologia anormal do intestino
Ocasional (29-5%)
17%prev.
Neoplasia
Ocasional (29-5%)
17%prev.
Glaucoma
Ocasional (29-5%)
9sintomas
Muito frequente (2)
Frequente (1)
Ocasional (4)
Sem dados (2)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 9 características clínicas mais associadas, ordenadas por frequência.

LinfedemaLymphedema
Muito frequente (99-80%)90%
AsciteAscites
Muito frequente (99-80%)90%
Nódulo subcutâneoSubcutaneous nodule
Frequente (79-30%)55%
Morfologia anormal do intestinoAbnormal intestine morphology
Ocasional (29-5%)17%
NeoplasiaNeoplasm
Ocasional (29-5%)17%

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico1.645PubMed
Últimos 10 anos200publicações
Pico202584 papers
Linha do tempo
2026Hoje · 2026🧪 2000Primeiro ensaio clínico📈 2025Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

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Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
2Fase 22
Medicamentos catalogadosEnsaios clínicos· 0 medicamentos · 2 ensaios
Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Ascite quilosa

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Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

4 ensaios clínicos encontrados.

Distribuição por fase
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
687 papers (10 anos)

Mostrando amostra de 200 publicações de um total de 687

#1

Case Report: Pediatric chylous ascites beyond congenital malformations-infectious causes and nutritional management with a literature review.

Frontiers in pediatrics2026

Chylous ascites (CA) is a condition characterized by the accumulation of lymphatic fluid in the peritoneal cavity. Although congenital malformations are the most common cause in newborns, infectious agents represent a clinically significant, potentially reversible etiology that benefits from specific therapy. Various pathogens, including bacteria, viruses, fungi, and parasites, can alter the lymphatic system and lead to the leakage of chyle into the peritoneal cavity, resulting in nutritional, immunological, and metabolic deficiencies. We describe the case of a 5-month-old infant presenting with acute abdomen (vomiting, irritability, and abdominal distension) associated with elevated lipase levels. He underwent emergency laparotomy, which revealed chylous ascites in the absence of structural abnormalities. Initial empiric management, centered on the diagnosis of CA, included fasting and total parenteral nutrition (TPN), followed by a gradual dietary transition from a lipid-free milk formula to a formula enriched in medium-chain triglycerides (MCTs) and reduced in long-chain triglycerides, which was well tolerated. Cytomegalovirus (CMV) infection was identified as the underlying cause and confirmed by PCR on blood, urine, ascitic fluid, and gastric biopsies. The etiological diagnosis allowed for specific antiviral therapy, which, combined with nutritional support, led to complete resolution of the case. We also review published cases of infectious CA in children, analyzing the clinical presentation, diagnostic approaches, and therapeutic strategies. Particular attention is paid to nutritional management. Interventions including the use of TPN, fat-free formulas, or MCT-enriched formulas are also important in infectious etiologies for temporarily controlling the chyle loss mechanism while awaiting complete lymphatic restitution. This review emphasizes the importance of recognizing infectious etiologies in chylous ascites and emphasizes the critical role of personalized nutritional support in optimizing recovery.

#2

Crisis-Driven Autonomization of Pediatric Liver Procurement and Implantation During COVID-19: A Transition From International Support to Local Execution.

Pediatric transplantation2026 Mar

Children's Hospital 2 in Ho Chi Minh City is the only public pediatric center performing pediatric liver transplantation (PLT) in Southern Vietnam. Before the COVID-19 pandemic, our PLT program was implemented and operated in collaboration with Belgian surgical teams who supported both graft procurement and implantation. The program enabled capacity-building and protocol development. Travel restrictions necessitated a transition to a hybrid local model. Building on the Pre-COVID groundwork, the team successfully performed 12 living-donor PLTs between 10/2021 and 9/2022. Standardized protocols- developed through earlier international collaboration- were consistently applied. Procurement surgery was carried out by an experienced adult hepatobiliary surgeon from a local hospital, while the implantation was conducted by the pediatric surgical team. Donors had a mean age of 32 ± 6.1 years. Procurement surgery lasted 422 ± 78.1 min. Mean blood loss was 237.5 ± 122.7 mL, and two donors required transfusion. All donor complications were Clavien-Dindo grade I. Recipients had a median age of 28 months and a weight of 10.4 kg. Biliary atresia accounted for 91.7% of indications. Grafts included seven left lateral segments and five full-left lobes. Recipient surgeries lasted 650 ± 91.5 min; mean transfusion volume was 231.2 ± 164.3 mL; cold ischemia time was 83.2 ± 24.9 min. Complications included chylous ascites (n = 2), portal vein stenosis (n = 1), and acute rejection (n = 2). One patient died from a hospital-acquired infection. This crisis-driven transition to local autonomization demonstrated that prior supportive preparation and implementation enabled safe and effective PLT during a global health emergency.

#3

Severe Lymphorrhea Mimicking Hypovolemic Shock Following Retroperitoneal Lymphadenectomy for Endometrial Cancer: A Case Report.

The journal of obstetrics and gynaecology research2026 Mar

We present a rare case of severe lymphatic leakage resembling hypovolemic shock following retroperitoneal lymphadenectomy for endometrial cancer. A 62-year-old female developed massive lymphorrhea and chylous ascites following total abdominal hysterectomy, bilateral salpingo-oophorectomy, and pelvic and para-aortic lymphadenectomy. Immediately postoperatively, massive lymphatic leakage caused hypotension and oliguria necessitating vasopressor support. Conservative management, including fasting and octreotide, was unsuccessful. Lymphangiography with Lipiodol and subsequent embolization using N-butyl cyanoacrylate were performed but did not achieve hemodynamic stabilization. Re-laparotomy was undertaken, and indocyanine green injection into the bilateral inguinal lymph nodes, along with oral milk ingestion, enabled precise intraoperative identification of leakage sites. These were successfully ligated with adjunctive fibrin glue and oxidized cellulose. Hemodynamics rapidly improved following repair. Although most lymphatic leakages resolve conservatively, severe cases can cause life-threatening circulatory failure. This case highlights the importance of a multidisciplinary approach, including interventional radiology and surgical repair, to achieve successful outcomes.

#4

ACR Appropriateness Criteria® Management of Chylothorax.

Journal of the American College of Radiology : JACR2026 Mar 06

Chylothorax, the accumulation of lymphatic fluid within the pleural cavity, results from disruption or obstruction of the thoracic duct or its tributaries, or from transdiaphragmatic chylous ascites. When severe, this condition may impair respiratory function and induce metabolic complications because of chronic loss of protein and lipids. Management strategies ranging from dietary modifications, medical therapy, surgical ligation, pleurodesis, and lymphatic embolization, generally follow a tiered approach. Special considerations apply to chylothorax associated with central venous obstruction or concurrent chylous ascites, sometimes requiring unique management strategies. The various approaches to the management of chylothorax and their appropriateness in a variety of clinical circumstances are discussed. The American College of Radiology Appropriateness Criteria are evidence-based guidelines for specific clinical conditions that are reviewed annually by a multidisciplinary expert panel. The guideline development and revision process support the systematic analysis of the medical literature from peer reviewed journals. Established methodology principles such as Grading of Recommendations Assessment, Development, and Evaluation or GRADE are adapted to evaluate the evidence. The RAND/UCLA Appropriateness Method User Manual provides the methodology to determine the appropriateness of imaging and treatment procedures for specific clinical scenarios. In those instances where peer reviewed literature is lacking or equivocal, experts may be the primary evidentiary source available to formulate a recommendation.

#5

Chylous Lymphocyst Following Retroperitoneal Lymphadenectomy: A Case Report and Review of Treatment.

International journal of women's health2026

Chylous lymphocyst or lymphocele following pelvic and para-aortic lymphadenectomy is rare. Clinically, patients usually present with abdominal distension or abdominal pain. The milky appearance of the cystic fluid reflects its high triglyceride content. Although specific guidelines for managing chylous lymphocyst are limited, the approaches used for chylous ascites can generally be applied. More than 70% of patients respond to conservative treatment, which includes a modified diet consisting of high protein, fat restriction, and medium-chain triglyceride supplementation. We present the case of a 45-year-old woman who developed a symptomatic 15-cm pelvic lymphocyst one month after surgical staging for a mucinous borderline ovarian tumor. Following the placement of a percutaneous catheter drainage (PCD), the initial output was 300-400 mL/day of clear serous fluid. Notably, a delayed chylous conversion occurred on the 20th day of drainage, the fluid turned milky and biochemical analysis confirmed a triglyceride level of 493 mg/dL. Initiation of a modified high-protein, fat-restricted diet resulted in a rapid decrease in drainage volume to 30 mL/day within 24 hours, alongside a return to clear yellowish appearance. This study aims to report the clinical manifestations and to summarize current therapeutic options for patients with chylous leakage.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC1.122 artigos no totalmostrando 200

2026

Case Report: Pediatric chylous ascites beyond congenital malformations-infectious causes and nutritional management with a literature review.

Frontiers in pediatrics
2026

Crisis-Driven Autonomization of Pediatric Liver Procurement and Implantation During COVID-19: A Transition From International Support to Local Execution.

Pediatric transplantation
2026

Severe Lymphorrhea Mimicking Hypovolemic Shock Following Retroperitoneal Lymphadenectomy for Endometrial Cancer: A Case Report.

The journal of obstetrics and gynaecology research
2026

ACR Appropriateness Criteria® Management of Chylothorax.

Journal of the American College of Radiology : JACR
2026

Chylous Lymphocyst Following Retroperitoneal Lymphadenectomy: A Case Report and Review of Treatment.

International journal of women's health
2026

A Cerebral Ethiodized Embolism after Lymphangiography: A Case Report and Literature Review.

Internal medicine (Tokyo, Japan)
2026

Three Years of Idiopathic Chylous Ascites: Splenic Marginal Zone Lymphoma Behind the Mask.

Cureus
2026

Massive Recurrent Chylous Ascites Following Laparoscopic Inguinal Hernia Mesh Repair.

Cureus
2026

Persistent Lymphatic Ascites After Liver Transplantation: Identification of the Underlying Mechanism of Ascites Permits Successful Percutaneous Treatment.

Cardiovascular and interventional radiology
2026

Chylous Ascites From Cirrhosis-Related Portal Hypertension Treated With Medium-Chain Triglycerides, Octreotide, and Paracentesis.

ACG case reports journal
2026

Marginal zone lymphoma presenting with chylous ascites: A rare clinical manifestation and successful treatment with orelabrutinib-rituximab.

SAGE open medical case reports
2026

Chylous Ascites Manifesting as Vulvovaginal Chyle Leakage: A Rare Gynecologic Presentation.

Journal of minimally invasive gynecology
2025

Low-Dose Radiation Therapy (LDRT) for Lymphatic Obliteration in Persistent Chylous Ascites: A Case Report.

Cureus
2025

Complex Lymphatic Anomaly Presenting with Chylothorax, Chylous Ascites, and Generalized Subcutaneous Edema in a Young Cat: Comparative Insights Based on the Human ISSVA Classification.

Veterinary sciences
2026

Cooperative ETS transcription factors are required for lymphatic endothelial cell integrity and resilience.

The Journal of clinical investigation
2025

Dual Chyle Leak: A Case of Chylothorax With Chylous Ascites.

Cureus
2025

Internal hernia in a patient with chylous ascites: a case report.

Frontiers in medicine
2025

Successful Use of Midodrine in a Normotensive, Non-cirrhotic Patient With Chylous Ascites Due to Chronic Porto-Mesenteric Thrombosis: A Multidisciplinary Challenge.

Cureus
2025

Dietary interventions vs octreotide for post liver transplantation chylous ascites: A scoping review.

World journal of transplantation
2025

Chylous Ascites, a Rare Adverse Reaction to Selpercatinib.

Cureus
2025

[Chylou Peritonitis Secondary to a Lymphocele of the Thoracic Duct due to Blunt Trauma].

Acta gastroenterologica Latinoamericana
2025

A 74-Year-Old Man with Massive Ascites: A Case Report of Yellow Nail Syndrome.

Reports (MDPI)
2026

Lipid-rich abdominal fluid mimicking chyloabdomen in a horse.

Journal of veterinary diagnostic investigation : official publication of the American Association of Veterinary Laboratory Diagnosticians, Inc
2025

Chronic hepatitis E complicated by chylous ascites in an HIV-infected patient with previous disseminated MAC infection: a case report.

ASM case reports
2025

Peritoneovenous Shunting to Manage Chylous Ascites Following Liver Resection for Cholangiocarcinoma: A Case Report.

Surgical case reports
2025

Emergency Surgical Management of Chemotherapy-Induced Tumor Rupture in a Patient with MYCN-Amplified Neuroblastoma: A Case Report.

Surgical case reports
2025

Chylothorax and chylous ascites in AIDS-associated Kaposi sarcoma: a case report and literature review.

BMC infectious diseases
2025

Life-Threatening Noninfectious Complications of Peritoneal Dialysis in an Infant with End-Stage Kidney Disease.

Pediatric reports
2026

Modified radical nephrectomy in the treatment of pediatric unilateral Wilms' tumor: Emphasizing a template-based regional lymphadenectomy.

Journal of pediatric urology
2025

Combined antegrade and retrograde approach for embolization of abdominal chyle leak.

Urology case reports
2025

Evaluating the Impact of Retroperitoneal Lymphadenectomy in Terms of Morbidity and Survival in Advanced Epithelial Ovarian Cancer.

Cureus
2025

Awake pancreaticoduodenectomy without intubation: exploring short-term clinicopathological outcomes of epidural vs. general anesthesia.

Frontiers in surgery
2025

Site-1 protease-mediated cholesterol metabolism is essential for lymphatic development in mice.

JCI insight
2025

Chylothorax in a patient with advanced ovarian cancer: a case report and literature review.

Frontiers in oncology
2025

TIPS to Treat Chylous Ascites due to Cirrhosis.

Clinical case reports
2025

MR Lymphangiography in Pediatrics: Indications, Technique, Findings, and Management.

Seminars in interventional radiology
2025

Chylous ascites following bilateral nephrectomy.

Journal of nephrology
2025

Development of a nomogram for predicting postoperative Hirschsprung-associated enterocolitis.

Frontiers in pediatrics
2025

Imaging of central lymphatics in children with Both Trisomy 21 and congenital heart disease.

Clinical imaging
2025

Percutaneous Lymphatic Embolization for Chylothorax Secondary to Gorham-Stout Disease.

Korean journal of radiology
2025

Management of chylous pleural and peritoneal effusions in a cirrhotic patient: A case report and review of literature.

The Journal of international medical research
2025

Lymphatic Obstruction Related to Small Bowel Obstruction With Chylous Ascites in Prior Roux En Y Gastric Bypass Patient Case Report.

Case reports in surgery
2025

The first case report of chylous ascites in a twin pregnancy following in vitro fertilization: a case report of chylous ascites in twin pregnancy.

Annals of medicine and surgery (2012)
2025

Successful treatment of chylous leakage with delayed presentation after endometrial cancer surgery using dietary therapy, octreotide, and computed tomography-guided lymphangiography: A case report and literature review.

The journal of obstetrics and gynaecology research
2025

Mesenteric Lymphangiography as a New Diagnostic and Therapeutic Tool for Refractory Chylous Lymphatic Leakages and Protein-Losing Enteropathy.

Journal of vascular and interventional radiology : JVIR
2025

Chylous ascites as a postoperative complication of a robot-assisted D3 extended right hemicolectomy: a case report.

Journal of surgical case reports
2025

Chylous ascites and persistent hiccups as complications after laparoscopic radical nephrectomy.

BMJ case reports
2025

Management of Refractory Chylous Ascites.

Urology case reports
2025

Magnetic Resonance Lymphangiography in Children: What the Radiologist Needs to Know.

Radiologic clinics of North America
2025

Management of chylous ascites following pancreaticoduodenectomy surgery using radiotherapy: A case report and review of literature.

International journal of surgery case reports
2025

Remember Chylous Ascites After Open Aneurysm Repair.

EJVES vascular forum
2025

Chylous Leakage After Retroperitoneal Minimally Invasive Surgery: A Multi-institutional Analysis of Risk Factors, Treatment Course, and Surgical Intervention.

Urology
2025

Diagnostic Challenges in Lymphangioleiomyomatosis: From Ovarian Mass to Systemic Diagnosis.

Acta medica Lituanica
2025

Nuclear Medicine Lymphoscintigraphy: Applications and Technical Overview.

Radiographics : a review publication of the Radiological Society of North America, Inc
2025

Refractory Infantyl Chylous Ascites Treatment by Everolimus.

Medeniyet medical journal
2025

Nephrotic syndrome with concurrent effusion from a different cause: A case series.

Journal of family medicine and primary care
2025

Role of Lipiodol® lymphangiography in the diagnosis and management of post-operative chylous ascites.

Frontiers in radiology
2025

Percutaneous lymphatic duct embolisation in postnephrectomy chylous ascites.

BMJ case reports
2025

Diagnostic Evaluation and Management of Idiopathic Chylous Ascites: A Report of a Surgical Case.

Cureus
2025

A systematic review of lymphovenous anastomosis to treat nontraumatic chylous anasarca.

Surgery
2025

Severe Rectal Stenosis as the First Clinical Appearance of a Metastasis Originating from the Bladder: A Case Report and Literature Review.

Life (Basel, Switzerland)
2025

Interventional Radiology in Management of Postoperative Chylous Ascites.

Interventional radiology (Higashimatsuyama-shi (Japan)
2025

Rare complication of chylous ascites following surgery and radiotherapy in endometrial carcinoma managed by diet modification: Case report.

Indian journal of cancer
2025

Successful Treatment of a Refractory Lymphatic Fistula after Laparoscopic Para-Aortic Lymphadenectomy Using Dual Real-Time Lymphangiography with Indocyanine Green and a High-Fat Diet.

Surgical case reports
2025

Pressurized Contrast Injection in a Lymphocele Can Reveal an Embolizable Lymphopseudoaneurysm in Postsurgical Chylous Ascites.

Lymphology
2025

Chylous ascites discovered intraoperatively during laparoscopic cholecystectomy for gallstone pancreatitis.

Journal of surgical case reports
2025

[Postoperative chyle leakage after abdominal surgery-Diagnostic and therapeutic strategies].

Chirurgie (Heidelberg, Germany)
2025

Lymphoid Peritoneal Fluid as a Variant of Chylous-Like Effluent in Peritoneal Dialysis: Proposal for a New Diagnostic Term.

Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologia
2025

Portal Venous Decompression for Treatment of Portal Hypertension-Related Refractory Chylous Ascites or Chylothorax.

Journal of vascular and interventional radiology : JVIR
2026

Efficacy of Microsurgical Venous Couplers in Lymphovenous Anastomosis of the Thoracic Duct: An Examination of Outcomes and Patency at Follow-Up.

Journal of reconstructive microsurgery
2024

Heterotopic Pancreas Masquerading as Omental Nodule on FAPI PET/CT.

Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, India
2025

Laparoscopic curative resection following perioperative chemotherapy with 5-fluorouracil, leucovorin, oxaliplatin, and docetaxel and its influence on Claudin18.2 expression in advanced gastric or gastroesophageal junction adenocarcinoma: a two-case report.

Discover oncology
2025

Lymphatic flow dynamics under exercise load assessed with thoracic duct ultrasonography.

Scientific reports
2025

Efficacy of Sirolimus in Treating Refractory Lymphatic Malformation in Noonan Syndrome: A Case Study.

JCEM case reports
2025

[Lymphatic vessel imaging-Indications and clinical applications].

Radiologie (Heidelberg, Germany)
2025

Lymphatic Malformations with Activating KRAS Mutations Impair Lymphatic Valve Development Through Matrix Metalloproteinases.

bioRxiv : the preprint server for biology
2025

Small Bowel Volvulus With Chylous Ascites Following Total Gastrectomy.

Cureus
2026

Management of Ascites: AJR Expert Panel Narrative Review.

AJR. American journal of roentgenology
2025

Long-term conservative treatment of chylous ascites in gynecological malignant surgery: a case report and literature review.

International cancer conference journal
2025

Sclerosing Mesenteritis Presenting as Hilar Cholangiocarcinoma Causing Recurrent Chylous Ascites and Gastric Outlet Obstruction.

ACG case reports journal
2025

Chylous ascites as an initial presentation of lupus nephritis.

BMJ case reports
2025

Chyle leak following root of mesentery dissection in pancreaticoduodenectomy with inferior infracolic superior mesenteric artery first approach.

World journal of clinical cases
2025

Comparison of laparoscopic versus robot-assisted sugery for rectal cancer after neo-adjuvant therapy: a large volume single center experience.

BMC surgery
2025

Impact of sympathetic denervation via paraaortic lymphadenectomy on blood pressure in endometrial cancer patients.

Turkish journal of obstetrics and gynecology
2025

Comparison of the Effectiveness of Inguinal Lymphangiography and Transjugular Intrahepatic Portosystemic Shunt Creation in Cirrhosis-Related Chylous Ascites.

Journal of vascular and interventional radiology : JVIR
2025

Focusing on chylous ascites: a noteworthy complication after laparoscopic/robotic para-aortic lymphadenectomy in left-sided colorectal cancer in a high-volume single center.

Techniques in coloproctology
2025

Efficiency of intranodal lymphangiography in the treatment of postoperative lymphatic leakage.

Ulusal travma ve acil cerrahi dergisi = Turkish journal of trauma &amp; emergency surgery : TJTES
2025

Advancing Pediatric Surgery with Indocyanine Green: Nonhepatobiliary Applications and Outcomes.

Journal of Indian Association of Pediatric Surgeons
2025

Looks are deceiving: An uncommon cause of milky white peritoneal dialysis effluent.

Peritoneal dialysis international : journal of the International Society for Peritoneal Dialysis
2025

Chylous Leakage after Endometrial Carcinoma Surgery: A Case Report.

Annali italiani di chirurgia
2025

Petersen's hernia with chylous ascites following laparoscopic total gastrectomy and Roux-en-Y anastomosis: A case report and review of literature.

World journal of gastrointestinal surgery
2025

Management of chylous ascites after liver cirrhosis: A case report.

World journal of hepatology
2025

Effectiveness and Safety of Peritoneovenous (Denver) Shunt Placement for Treatment of Chylous Ascites Following Unsuccessful Lymphatic Embolization.

Journal of vascular and interventional radiology : JVIR
2024

An Unusual Case of Chylous Ascites.

Cureus
2025

Conservative management of large-volume chylous ascites following a robotic-assisted left radical nephrectomy.

BMJ case reports
2024

Fetal Ascites: Its Prenatal Management and Postnatal Outcome.

Journal of obstetrics and gynaecology of India
2025

Accidentally Encountered Chylous Ascites: Recurrence of Peritoneal Tuberculosis.

Journal of minimally invasive gynecology
2025

Is cloudy peritoneal dialysate associated with adverse drug reactions to benidipine?

Peritoneal dialysis international : journal of the International Society for Peritoneal Dialysis
2025

Postoperative chylous ascites successfully managed by selective lymphatic embolization: Case report and literature review.

Radiology case reports
2024

Multidisciplinary management of chylous ascites following resection of a retroperitoneal, functional Paraganglioma.

Urology case reports
2024

Refractory Chylous Ascites Leading to Chylothorax Following Extended Right Hepatectomy for Intrahepatic Cholangiocarcinoma.

Cureus
2024

Chylous Ascites in Laparoscopic versus Open Surgeries: A Meta-Analysis and Review of Literature.

Current problems in surgery
2025

Chyloperitoneum in a toddler on peritoneal dialysis.

Pediatric nephrology (Berlin, Germany)
2024

[Clinical features of 50 patients with primary intestinal lymphangiectasia].

Zhonghua wai ke za zhi [Chinese journal of surgery]
2024

Contrast-enhanced CT Lymphangiography for Various Central Lymphatic Disorders.

Radiographics : a review publication of the Radiological Society of North America, Inc
2024

Severe Hypertrophic Cardiomyopathy Caused by a Protein Kinase Adenosine Monophosphate-Activated Non-catalytic Subunit Gamma 2 (PRKAG2) Mutation With Refractory Chylous Effusions in a Neonate: A Case Report and Literature Review.

Cureus
2025

Isolated Chylous Ascites After Arterial Switch Surgery in a Newborn: Peritoneal Dialysis and Right Ventricular Pressure as Potential Contributing Factors.

Journal of cardiothoracic and vascular anesthesia
2024

Application of ultrasound-guided intranodal lymphangiography in the diagnosis and treatment of chylous ascites after abdominal surgery.

Polish journal of radiology
2024

A rare type of ascites in liver cirrhosis: Chylous ascites.

Asian journal of surgery
2024

Refractory bilateral chylothorax and chylous ascites in a patient with systemic lupus erythematosus treated by pleuro-peritoneal and peritoneal-venous shunts along with cell-free and concentrated ascites re-infusion therapy.

Respiratory investigation
2024

Propranolol As a Treatment Option for Chylous Effusions and Chylous Ascites in Fetuses and Neonates: A Systematic Review.

The journal of pediatric pharmacology and therapeutics : JPPT : the official journal of PPAG
2024

Single-Center Experience With Dynamic Contrast-Enhanced Magnetic Resonance Lymphangiography for Diagnosing Lymphatic Disorders and Guiding Percutaneous Embolization.

Journal of Korean medical science
2024

Chylous ascites secondary to pancreatic pseudocyst: A case report.

Revista de gastroenterologia de Mexico (English)
2024

Unexpected Chylous Ascites During Umbilical Hernia Repair in a Patient with Necrotizing Pancreatitis: A Case Report.

The American journal of case reports
2025

Effective Intractable Chylous Ascites Treatment by Lymphangiography with Lipiodol in a Patient with Follicular Lymphoma.

Internal medicine (Tokyo, Japan)
2024

Acute Abdomen in Pregnancy due to Idiopathic Chylous Ascites.

Case reports in obstetrics and gynecology
2024

Chylothorax in a Young Woman With Crohn Disease.

Chest
2024

A case of refractory chylothorax due to an unenclosed esophageal hiatus after subtotal esophagectomy treated with lipiodol lymphangiography.

Surgical case reports
2024

Massive chylous pleural effusion and protein‑losing enteropathy caused by mesenteric panniculitis: A case report.

Biomedical reports
2024

Navigating the Labyrinth: Chylothorax and Chylous Ascites Unveiled After Abdominal Surgery for an Exceptionally Rare Tumor.

Cureus
2024

Contemporary short-term peri-operative outcomes of open primary retroperitoneal lymph node dissection.

BJU international
2024

Understanding acute chyloperitoneum in appendicitis: case report and literature review.

Journal of surgical case reports
2025

MR Lymphangiography: Congenital Lymphatic Flow Disorders.

Investigative radiology
2024

Lymphatic Imaging and Intervention in Congenital Heart Disease.

Journal of the Society for Cardiovascular Angiography &amp; Interventions
2024

Enterogenic bacterial peritonitis and delayed chylous ascites associated with overheated peritoneal dialysis fluid infusion.

Clinical kidney journal
2025

Cancer of Unknown Primary Presenting with Chylothorax.

Internal medicine (Tokyo, Japan)
2024

Sildenafil as a Potential Therapeutic Option for Refractory Congenital Chylous Ascites in a Premature Neonate: A Case Report and Literature Review.

Klinische Padiatrie
2024

Management of Chyle Leak in Pediatric Surgical Oncology: A Systematic Review.

Journal of pediatric hematology/oncology
2024

Colon signet-ring cell carcinoma with chylous ascites caused by immunosuppressants following liver transplantation: A case report.

World journal of gastrointestinal surgery
2024

Bilateral Renal Vein Thrombosis and Chylous Ascites in Phospholipase A2 Receptor-Associated Membranous Nephropathy: A Case Report.

Cureus
2024

Examination of the Usefulness of Standby Therapy for Refractory Chylous Ascites After Multiple Lymphangiography Interventions.

Cureus
2024

Diagnosis and Treatment of a 64-Year-Old Man with Chyle Leak Following Laparoscopic Cholecystectomy: A Case Report.

The American journal of case reports
2024

A Case of Polyserositis, Chylous Ascites and Hepatitis Induced by Immune Checkpoint Inhibitors.

European journal of case reports in internal medicine
2024

Postoperative Chylous Ascites in Gynecological Malignancies: Two Case Reports and a Literature Review.

Obstetrics and gynecology international
2024

Left Chylothorax Without Ascites in a Liver Transplant Patient.

Cureus
2024

Acute primary chylous peritonitis mimicking acute abdomen: a case report and literature review.

The Pan African medical journal
2024

Neonatal perspective on central lymphatic disorders.

Seminars in pediatric surgery
2024

Chylous ascites after associating liver partition and portal vein ligation for stage hepatectomy (ALPPS): overview and case report.

Journal of surgical case reports
2024

Surgical management of chronic lymphatic pleural effusions and chronic lymphatic ascites.

Seminars in pediatric surgery
2024

Acute Chyloperitoneum with Small Bowel Volvulus: Case Series and Systematic Review of the Literature.

Journal of clinical medicine
2024

Intranodal Lymphangiography and Embolization for Management of Iatrogenic Chylous Ascites after Oncological Surgery.

Journal of vascular and interventional radiology : JVIR
2024

Clinical Practice Guide: Management of Chylous Ascites After Retroperitoneal Lymph Node Dissection.

European urology focus
2024

Sclerosing Mesenteritis: A Concise Clinical Review for Clinicians.

Mayo Clinic proceedings
2024

Successful management of chylous ascite after removal of residual mass in non-seminomatous germ cell tumours following chemotherapy: A single-center experience and review of the literature.

International journal of surgery case reports
2024

Indocyanine green lymphography in the congenital chylothorax and chylous ascites.

Journal of neonatal-perinatal medicine
2024

Central conducting lymphatic anomaly: from bench to bedside.

The Journal of clinical investigation
2024

Management of Idiopathic Infantile Chylous Ascites.

Cureus
2024

Lymphatic Chyle Duct Injury and Identification During Laparoscopic Sleeve Gastrectomy Preventing Postoperative Chylous Ascites.

Obesity surgery
2024

Successful Treatment of Refractory Chylous Ascites With Octreotide in a Patient With Decompensated Cirrhosis.

ACG case reports journal
2024

Interventional treatment of refractory non-traumatic chylous effusions in patients with lymphoproliferative disorders.

Clinical and experimental medicine
2024

Chylous Ascites Associated with Advanced Pancreatic Cancer That Improved with Appropriate Treatment: A Case Report.

Current oncology (Toronto, Ont.)
2024

Incidence and Risk Factors for Chyle Leaks After Neuroblastic Tumor Resection: A Systematic Review of Published Studies.

Journal of pediatric surgery
2024

A sutureless overlapped anastomosis technique using linear staplers with reinforced bioabsorbable material in robotic right colectomy with intracorporeal anastomosis.

Colorectal disease : the official journal of the Association of Coloproctology of Great Britain and Ireland
2024

Chylothorax Chronicles: Tubercular Lymphadenopathy and Hemophagocytic Lymphohistiocytosis.

Cureus
2024

Rare Combination of Chyloperitoneum Secondary to Primary Small-Bowel Volvulus.

Cureus
2024

Refractory chylous ascites revealing follicular lymphoma: A case report.

International journal of surgery case reports
2024

Aetiology and diagnostic utility of serum ascites albumin gradient in children with ascites.

Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver
2024

Chylous drainage through percutaneous cholecystostomy: an extremely rare complication.

Journal of surgical case reports
2024

Interrelation of cancers of unknown primary, chylous ascites, and cavernous mesenteric lymphangioma in a 57-year-old female patient: a case report.

Journal of surgical case reports
2024

Hybrid Lymphovenous Anastomosis Surgery Guided by Intraoperative Mesenteric Intranodal Lymphangiography for Refractory Nontraumatic Chylous Ascites: A Case Report.

Archives of plastic surgery
2024

An Elemental Diet Reduces Chylous Ascites of Patients Undergoing Pancreatoduodenectomy in the Setting of Early Enteral Feeding.

Pancreas
2024

A case of chylous ascites caused by reflux from the cisterna chyli to the disrupted common iliac lymphatic vessel: fluoroscopic records during intranodal lymphangiography.

BJR case reports
2024

Robotic-assisted retroperitoneal lymph node dissection for stage II testicular cancer.

Asian journal of urology
2024

Small bowel volvulus with chylous ascites: a case report.

Journal of surgical case reports
2024

Repair of lymphoperitoneal fistulae for chylous ascites following robotic-assisted partial nephrectomy: Anatomic foundation for left-sided predominance following renal surgery.

Urology case reports
2024

[Laparoscopic Surgery for Delayed Chylous Ascites in Unresectable Gastric Cancer Patient-A Case Report].

Gan to kagaku ryoho. Cancer &amp; chemotherapy
2024

Massive Chylous Ascites in a 9-Year-Old Girl with Malrotation-A Case Report.

European journal of pediatric surgery reports
2024

Complications of Peritoneal Dialysis Part II: Nonmechanical Complications.

Clinical journal of the American Society of Nephrology : CJASN
2024

Lipiodol embolization for chylous leak complication post robotic-assisted para-aortic lymph node resection.

Radiology case reports
2023

Novel Interventional Radiology for the Treatment of Various Lymphatic Leakages: Lymphatic Intervention and Embolization.

Vascular specialist international
2023

Newfound features associated with Hennekam Syndrome (Intestinal Lymphangiectasia-Lymphedema-Intellectual-Disability Syndrome) complicated with comorbid Waldmann's Disease resulting in Celiac Disease.

Clinical case reports
2023

Utility of 99mTc-Sulfur Colloid Lymphoscintigraphy and SPECT/CT in Chylothorax and Chylous Ascites.

Nuclear medicine and molecular imaging
2024

Refractory Peritonitis Related to Peritoneal Dialysis Caused by Enterococcus gallinarum.

Internal medicine (Tokyo, Japan)
2023

Prevalence and risk factors of lymphatic dysfunction in cirrhosis patients with refractory ascites: An often unconsidered mechanism.

World journal of hepatology
2024

Surgical Management of Central Lymphatic Conduction Disorders: A Review.

Journal of pediatric surgery
2023

Hyperthyroidism With Non-chylous Ascites: A Case Report.

Cureus
2024

Nutrition support considerations in pediatric small bowel transplantation.

Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition
2023

Gallbladder perforation following trauma in an 18-month-old child with a common bile duct cyst.

Radiology case reports
2023

Post-interventional infectious complications in percutaneous transabdominal lymphatic interventions: an observational study.

Scientific reports
2023

A late diagnosis of primary intestinal lymphangiectasia in a Syrian girl.

Clinical case reports
2023

Successful surgical treatment of congenital chylous ascites co-existed with congenital hypothyroidism: A rare case report.

International journal of surgery case reports
2023

Long-Term Clinical Outcome of Abdomino-Thoracic Lymphatic Interventions of Traumatic and Non-Traumatic Lymphatic Leakage in Adults.

Biomedicines
2023

Unusual manifestation of gastric adenocarcinoma presenting with lymphedema, chylothorax, and chylous ascites.

Clinical journal of gastroenterology
2024

Chylous ascites: A warning sign of life-threatening encapsulated peritoneal sclerosis in patient recently transferred to haemodialysis.

Peritoneal dialysis international : journal of the International Society for Peritoneal Dialysis
2023

Utility of MR lymphangiography in chylous ascites: A report of two cases.

SA journal of radiology
2023

Selpercatinib and Pralsetinib Induced Chylous Ascites in RET-Rearranged Lung Adenocarcinoma: A Case Series.

Clinical lung cancer
2023

Chylous ascites following retroperitoneal lymphadenectomy in a patient with recurrent dysgerminoma of ovary: A case report.

Gynecologic oncology reports
2023

Chylous Ascites Associated with Small Bowel Volvulus: Case Report on a Laparoscopic Diagnosis.

Middle East journal of digestive diseases
2023

Literature Review and 2 Cases of Isolated Chylothorax After Pediatric Living-Donor Liver Transplant.

Experimental and clinical transplantation : official journal of the Middle East Society for Organ Transplantation
2023

Chylous ascites complicating perinatal severe hypophosphatasia in an infant on high-setting ventilation and enzyme replacement therapy.

Pediatrics international : official journal of the Japan Pediatric Society
2023

Massive Right Chylothorax Secondary to a Severe Systemic Lupus Erythematosus Flare With Secondary Evans Syndrome: A Case Report and Literature Review.

Clinical medicine insights. Case reports
2023

Chylothorax: A Late Complication of Disseminated Mycobacterium avium Complex (MAC) Infection.

Cureus
2023

Successful Treatment of Cirrhotic Chylous Ascites using Orlistat and Dietary Modifications: A Case Study and Literature Review.

The American journal of case reports
2023

Chyloperitoneum After Penetrating Abdominal Trauma: A Report of a Rare Case.

Cureus
2023

Massive Elevation of CA-125 in Chylous Ascites.

Turkish archives of pediatrics
2023

Acute pancreatitis with chylous ascites mimicking acute appendicitis: A rare case report.

International journal of surgery case reports
2023

Chylous ascites as a rare complication of abdominal trauma in a 7-year-old girl: A case report.

Clinical case reports
2023

[Chylous ascites in NSCLC: It is not always malignant].

Pneumologie (Stuttgart, Germany)
2023

A case of mycotic infrarenal abdominal aortic aneurysm after bacillus Calmette-Guérin immunotherapy for bladder cancer and a review of the literature.

Journal of vascular surgery cases and innovative techniques
2023

Chylothorax associated with primary membranous nephropathy: a case report.

Annals of palliative medicine
Ver todos os 1.122 no EuropePMC

Associações

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Comunidades

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Case Report: Pediatric chylous ascites beyond congenital malformations-infectious causes and nutritional management with a literature review.
    Frontiers in pediatrics· 2026· PMID 41867932mais citado
  2. Crisis-Driven Autonomization of Pediatric Liver Procurement and Implantation During COVID-19: A Transition From International Support to Local Execution.
    Pediatric transplantation· 2026· PMID 41856788mais citado
  3. Severe Lymphorrhea Mimicking Hypovolemic Shock Following Retroperitoneal Lymphadenectomy for Endometrial Cancer: A Case Report.
    The journal of obstetrics and gynaecology research· 2026· PMID 41793077mais citado
  4. ACR Appropriateness Criteria&#xae; Management of Chylothorax.
    Journal of the American College of Radiology : JACR· 2026· PMID 41790078mais citado
  5. Chylous Lymphocyst Following Retroperitoneal Lymphadenectomy: A Case Report and Review of Treatment.
    International journal of women's health· 2026· PMID 41743620mais citado
  6. A Rare Case of Small Bowel Volvulus with Chylous Ascites Presumed to Be Caused by Multiple Congenital Adhesions in a Virgin Abdomen: A Case Report and Literature Review.
    Surg Case Rep· 2026· PMID 41982300recente
  7. Primary Intestinal Lymphangiectasia Presenting as Recurrent Chylous Ascites: A Rare Case.
    J Investig Med High Impact Case Rep· 2026· PMID 41943452recente
  8. Congenital Chylous Ascites in a Neonate with Isolated Aqueductal Stenosis: A Case Report and Literature Review.
    Reports (MDPI)· 2026· PMID 41893447recente
  9. Lymphatic Malformations With Activating KRAS Mutations Impair Lymphatic Valve Development Through Matrix Metalloproteinases.
    Arterioscler Thromb Vasc Biol· 2026· PMID 41884898recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:1160(Orphanet)
  2. OMIM OMIM:208300(OMIM)
  3. MONDO:0008829(MONDO)
  4. GARD:1359(GARD (NIH))
  5. Busca completa no PubMed(PubMed)
  6. Q15727012(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Ascite quilosa
Compêndio · Raras BR

Ascite quilosa

ORPHA:1160 · MONDO:0008829
Prevalência
Unknown
CID-10
I89.8 · Outros transtornos não-infecciosos, especificados, dos vasos linfáticos e dos gânglios linfáticos
CID-11
Início
All ages
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C0008732
EuropePMC
Wikidata
Papers 10a
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