Raras
Buscar doenças, sintomas, genes...
Síndrome de Balint
ORPHA:363746CID-10 · H51.8CID-11 · 9C82.4DOENÇA RARA

A síndrome de Balint é uma doença neurológica rara caracterizada pela tríade de ataxia óptica, apraxia ocular e simultanagnosia devido a lesões do lobo parietal posterior. Os pacientes relatam dificuldades oftalmológicas na ausência de anomalias oftalomológicas subjacentes e apresentam graves deficiências visuais e espaciais para localizar e alcançar objetos, iniciar movimentos oculares voluntários e perceber mais de um objeto por vez.

Mantido por Agente Raras·Colaborar como especialista →

Introdução

O que você precisa saber de cara

📋

A síndrome de Balint é uma doença neurológica rara caracterizada pela tríade de ataxia óptica, apraxia ocular e simultanagnosia devido a lesões do lobo parietal posterior. Os pacientes relatam dificuldades oftalmológicas na ausência de anomalias oftalomológicas subjacentes e apresentam graves deficiências visuais e espaciais para localizar e alcançar objetos, iniciar movimentos oculares voluntários e perceber mais de um objeto por vez.

Publicações científicas
87 artigos
Último publicado: 2026 Apr

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Início
All ages
🏥
SUS: Sem cobertura SUSScore: 0%
CID-10: H51.8
Você se identifica com essa condição?
O Raras está aqui pra te apoiar — com ou sem diagnóstico

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Entender a doença

Do básico ao detalhe, leia no seu ritmo

Preparando trilha educativa...

Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Características mais comuns

Apraxia oculomotora
1sintomas
Sem dados (1)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 1 características clínicas mais associadas, ordenadas por frequência.

Apraxia oculomotoraOculomotor apraxia

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico87PubMed
Últimos 10 anos37publicações
Pico20217 papers
Linha do tempo
2026Hoje · 2026📈 2021Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Síndrome de Balint

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

Nenhum ensaio clínico registrado para esta condição.

🧪 Está conduzindo uma pesquisa?
Divulgue para pacientes e familiares que acompanham esta doença.
Divulgar pesquisa →

Publicações mais relevantes

Timeline de publicações
38 papers (10 anos)
#1

Balint syndrome as the initial presentation of neuromyelitis optica spectrum disorder.

Revue neurologique2026 Mar 17
#2

Between the Borders: Balint Syndrome as a Rare Manifestation of Posterior Circulation Stroke.

Cureus2025 Nov

Balint syndrome is a rare disorder caused by bilateral parieto-occipital damage, most often occurring within the posterior watershed territory between the middle and posterior cerebral arteries. It is characterized by a triad of simultanagnosia, optic ataxia, and oculomotor apraxia, and is often misdiagnosed as delirium, dementia, or cortical blindness, particularly in elderly patients. We report a case of an 82-year-old woman who presented with confusion and visuospatial disorientation following a collapse. Her visual acuity was preserved, but she demonstrated simultanagnosia and oculomotor apraxia. Computed tomography of the brain revealed bilateral occipital watershed infarcts, consistent with Balint syndrome secondary to posterior border-zone infarction. She was managed with secondary stroke prevention and commenced on neurorehabilitation focusing on visuospatial and visuomotor retraining. This case highlights the importance of recognizing Balint syndrome as a rare manifestation of posterior circulation stroke. Awareness of its classic triad facilitates early diagnosis, appropriate neuroimaging correlation, and tailored rehabilitation to optimize patient outcomes.

#3

Bálint Syndrome From Posterior Cerebral Artery Infarctions Case Report.

Clinical neuropharmacology2025

Bálint syndrome is a debilitating, rare neurological condition characterized by a triad of visuospatial distortions: simultanagnosia, optic ataxia, and oculomotor apraxia. We highlight the pathways involved with infarction of the posterior cerebral artery (PCA), which may be an important underlying factor leading to the development of clinical presentations found in Bálint syndrome. We present a case of a middle-aged patient who presents with Bálint syndrome following a PCA infarction. A 49-year-old male bus driver with a recent PCA infarction presented with all 3 components of Bálint syndrome. His clinical course was notable for simultanagnosia, optic ataxia, oculomotor apraxia, and a right greater than left lower visual field deficit. Neuroimaging revealed infarctions in the P1 and bilateral P2 segments of the posterior cerebral arteries, affecting the parieto-occipital regions known to underlie visuospatial processing. Laboratory workup helped exclude opportunistic and systemic causes, supporting a stroke-related etiology. Posterior cerebral artery infarctions may be responsible for the clinical presentation of Bálint syndrome; however, further investigation into vascular and neuronal networks underlying the clinical signs and symptoms of Bálint syndrome is needed.

#4

Balint Syndrome in a Patient With Isolated Corpus Callosum Stroke: A Case Study With Narrative Review.

Cureus2025 Jun

We report a case of an isolated bilateral corpus callosum stroke (body and splenium) who exhibited Balint syndrome (optic ataxia, simultanagnosia, optic apraxia), along with a partial Gerstmann syndrome (left/right disorientation, acalculia, finger agnosia), with extinction to double simultaneous stimulation and astereognosis without direct involvements of the parietal lobes. We review the vascular anatomy of the corpus callosum, mechanisms and risk factors for stroke in this area, and the components of Balint syndrome and localization, with descriptions of recent data on neural networks involved in higher-level cortical function. Attention to the visual-spatial symptoms of Balint syndrome is important to consider when evaluating and treating patients with ischemic disease of the corpus callosum.

#5

Bálint syndrome in dementia with lewy bodies: A new phenotypic variant with progression implications?

Neurology perspectives2024

Publicações recentes

Ver todas no PubMed

📚 EuropePMC50 artigos no totalmostrando 35

2026

Balint syndrome as the initial presentation of neuromyelitis optica spectrum disorder.

Revue neurologique
2025

Between the Borders: Balint Syndrome as a Rare Manifestation of Posterior Circulation Stroke.

Cureus
2025

Bálint Syndrome From Posterior Cerebral Artery Infarctions Case Report.

Clinical neuropharmacology
2025

Balint Syndrome in a Patient With Isolated Corpus Callosum Stroke: A Case Study With Narrative Review.

Cureus
2024

Bálint syndrome in dementia with lewy bodies: A new phenotypic variant with progression implications?

Neurology perspectives
2024

A novel case of Bálint syndrome with hallucinatory palinopsia following hypoglycemic coma: opening new doors to the origin of palinopsia.

Neurology perspectives
2023

Bálint syndrome in a patient with drug-resistant epilepsy having underlying X-linked lissencephaly with subcortical band heterotopia/"double cortex" syndrome.

Neurology perspectives
2023

Bálint syndrome as the presenting manifestation of adrenoleukodystrophy.

Neurology perspectives
2023

Snakebite envenomation-induced posterior reversible encephalopathy syndrome presenting with Bálint syndrome.

Neurologia
2022

Clinical Screening for Posterior Cortical Atrophy.

Cognitive and behavioral neurology : official journal of the Society for Behavioral and Cognitive Neurology
2021

A Case of Balint Syndrome Due to Left Basal Ganglia Hemorrhagic Stroke: Exploring the Pathogenesis Through Parietal Lobe Circuits.

The primary care companion for CNS disorders
2021

Who is really blind in the time of coronavirus: the patient or the doctor? A rare case of Balint's syndrome.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2021

Egocentric and allocentric spatial representations in a patient with Bálint-like syndrome: A single-case study.

Cortex; a journal devoted to the study of the nervous system and behavior
2020

A rare case report of Lilliputian and Brobdingnagian hallucinations in a case of pemphigus vulgaris.

Indian journal of psychiatry
2021

18F-FDG PET/CT in the Diagnosis and Follow-up of Balint Syndrome.

Clinical nuclear medicine
2021

Teaching Video NeuroImages: Posterior Cortical Atrophy Presenting With Balint Syndrome.

Neurology
2021

Numeric input operation on electronic devices among individuals with visuospatial working memory impairment.

Neuropsychological rehabilitation
2020

Simultanagnosia as a cause of visual disturbance following Posterior Reversible Encephalopathy Syndrome (PRES): A case report.

Indian journal of ophthalmology
2019

[Progressive supranuclear palsy-Richardson syndrome with visual attention disturbance (Holmes and Horrax) and ataxie optique (Garcin): a case report].

Rinsho shinkeigaku = Clinical neurology
2019

Hemianopia and Features of Bálint Syndrome following Occipital Lobe Hemorrhage: Identification and Patient Understanding Have Aided Functional Improvement Years after Onset.

Case reports in ophthalmological medicine
2019

[A Patient with Progressive Multifocal Leukoencephalopathy Who Developed Bálint Syndrome Improved by Combination Therapy Using Mefloquine and Mirtazapine].

Brain and nerve = Shinkei kenkyu no shinpo
2019

Balint syndrome in anti-NMDA receptor encephalitis.

Neurology(R) neuroimmunology &amp; neuroinflammation
2018

Can hypnosis displace the threshold for visual consciousness?

Neuroscience of consciousness
2018

Balint syndrome (chronic visual-spatial disorder) presenting without known cause.

Radiology case reports
2018

Bálint syndrome caused by bilateral medial occipital infarcts.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2018

Bilateral parietal dysfunctions and disconnections in simultanagnosia and Bálint syndrome.

Handbook of clinical neurology
2018

Optic ataxia: beyond the dorsal stream cliché.

Handbook of clinical neurology
2018

Ocular Dysfunctions Presenting in Tacrolimus-Induced Posterior Reversible Encephalopathy Syndrome: A Case Presentation.

PM &amp; R : the journal of injury, function, and rehabilitation
2017

Memory for Spatial Locations in a Patient with Near Space Neglect and Optic Ataxia: Involvement of the Occipitotemporal Stream.

Frontiers in neurology
2017

Simultaneous object perception deficits are related to reduced visual processing speed in amnestic mild cognitive impairment.

Neurobiology of aging
2016

Bilateral injury of the superior longitudinal fasciculus in a patient with Balint syndrome.

Neurology
2015

Imaging of Retrochiasmal and Higher Cortical Visual Disorders.

Neuroimaging clinics of North America
2015

Effectiveness of Use of Button-Operated Electronic Devices Among Persons With Bálint Syndrome.

The American journal of occupational therapy : official publication of the American Occupational Therapy Association
2015

Visuospatial working memory is severely impaired in Bálint syndrome patients.

Cortex; a journal devoted to the study of the nervous system and behavior
2015

Perceptual-motor dysfunction.

Continuum (Minneapolis, Minn.)
Ver todos os 50 no EuropePMC

Associações

Organizações que acompanham esta doença — pra ter apoio e orientação

Ainda não temos associações cadastradas para Síndrome de Balint.

É de uma associação que acompanha esta doença? Fale com a gente →

Comunidades

Grupos ativos de quem convive com esta doença aqui no Raras

Ainda não existe comunidade no Raras para Síndrome de Balint

Pacientes, familiares e cuidadores se organizam em comunidades pra compartilhar experiências, fazer perguntas e se apoiar. Você pode ser o primeiro.

Tire suas dúvidas

Perguntas, dicas e experiências compartilhadas aqui na página

Participe da discussão

Faça login para postar dúvidas, compartilhar experiências e interagir com especialistas.

Fazer login

Doenças relacionadas

Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico

Ordenadas pelo número de sintomas em comum.

Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Balint syndrome as the initial presentation of neuromyelitis optica spectrum disorder.
    Revue neurologique· 2026· PMID 41850923mais citado
  2. Between the Borders: Balint Syndrome as a Rare Manifestation of Posterior Circulation Stroke.
    Cureus· 2025· PMID 41446452mais citado
  3. B&#xe1;lint Syndrome From Posterior Cerebral Artery Infarctions Case Report.
    Clinical neuropharmacology· 2025· PMID 40663424mais citado
  4. Balint Syndrome in a Patient With Isolated Corpus Callosum Stroke: A Case Study With Narrative Review.
    Cureus· 2025· PMID 40621301mais citado
  5. B&#xe1;lint syndrome in dementia with lewy bodies: A new phenotypic variant with progression implications?
    Neurology perspectives· 2024· PMID 39309256mais citado

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:363746(Orphanet)
  2. MONDO:0018211(MONDO)
  3. GARD:21558(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Artigo Wikipedia(Wikipedia)
  6. Q174651(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Síndrome de Balint
Compêndio · Raras BR

Síndrome de Balint

ORPHA:363746 · MONDO:0018211
Prevalência
Unknown
Herança
Not applicable
CID-10
H51.8 · Outros transtornos especificados do movimento binocular
CID-11
Início
All ages
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C0270706
EuropePMC
Wikidata
Wikipedia
Papers 10a
DiscussaoAtiva

Nenhuma novidade ainda. O agente esta monitorando.

0membros
0novidades